Mitrofanoff continent vesicostomy as a treatment option for epidermolysis bullosa complicated by posterior urethral stenosis

A small proportion of patients with EB develop genitourinary disorders, which can nevertheless have a major impact on their morbidity. We present the case of a 7-year-old boy with junctional EB who presented with dysuria and lower back pain caused by bladder lithiasis complicating posterior urethral...

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Main Authors: A. Kissel, N. Boudaoud, N. Bellon, M. Pons, M.L. Poli-Merol
Format: Article
Language:English
Published: Elsevier 2022-01-01
Series:Journal of Pediatric Surgery Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2213576621003377
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author A. Kissel
N. Boudaoud
N. Bellon
M. Pons
M.L. Poli-Merol
author_facet A. Kissel
N. Boudaoud
N. Bellon
M. Pons
M.L. Poli-Merol
author_sort A. Kissel
collection DOAJ
description A small proportion of patients with EB develop genitourinary disorders, which can nevertheless have a major impact on their morbidity. We present the case of a 7-year-old boy with junctional EB who presented with dysuria and lower back pain caused by bladder lithiasis complicating posterior urethral stenosis, surgical management, and postoperative outcomes.
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spelling doaj.art-173ee6bd25334facaf6e04272951129b2022-12-21T18:44:25ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662022-01-0176102116Mitrofanoff continent vesicostomy as a treatment option for epidermolysis bullosa complicated by posterior urethral stenosisA. Kissel0N. Boudaoud1N. Bellon2M. Pons3M.L. Poli-Merol4Corresponding author.; American Memorial Hospital, Reims, FranceAmerican Memorial Hospital, Reims, FranceAmerican Memorial Hospital, Reims, FranceAmerican Memorial Hospital, Reims, FranceAmerican Memorial Hospital, Reims, FranceA small proportion of patients with EB develop genitourinary disorders, which can nevertheless have a major impact on their morbidity. We present the case of a 7-year-old boy with junctional EB who presented with dysuria and lower back pain caused by bladder lithiasis complicating posterior urethral stenosis, surgical management, and postoperative outcomes.http://www.sciencedirect.com/science/article/pii/S2213576621003377Epidermolysis bullosaUrethral stenosisVesicostomyMitrofanoff
spellingShingle A. Kissel
N. Boudaoud
N. Bellon
M. Pons
M.L. Poli-Merol
Mitrofanoff continent vesicostomy as a treatment option for epidermolysis bullosa complicated by posterior urethral stenosis
Journal of Pediatric Surgery Case Reports
Epidermolysis bullosa
Urethral stenosis
Vesicostomy
Mitrofanoff
title Mitrofanoff continent vesicostomy as a treatment option for epidermolysis bullosa complicated by posterior urethral stenosis
title_full Mitrofanoff continent vesicostomy as a treatment option for epidermolysis bullosa complicated by posterior urethral stenosis
title_fullStr Mitrofanoff continent vesicostomy as a treatment option for epidermolysis bullosa complicated by posterior urethral stenosis
title_full_unstemmed Mitrofanoff continent vesicostomy as a treatment option for epidermolysis bullosa complicated by posterior urethral stenosis
title_short Mitrofanoff continent vesicostomy as a treatment option for epidermolysis bullosa complicated by posterior urethral stenosis
title_sort mitrofanoff continent vesicostomy as a treatment option for epidermolysis bullosa complicated by posterior urethral stenosis
topic Epidermolysis bullosa
Urethral stenosis
Vesicostomy
Mitrofanoff
url http://www.sciencedirect.com/science/article/pii/S2213576621003377
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AT nboudaoud mitrofanoffcontinentvesicostomyasatreatmentoptionforepidermolysisbullosacomplicatedbyposteriorurethralstenosis
AT nbellon mitrofanoffcontinentvesicostomyasatreatmentoptionforepidermolysisbullosacomplicatedbyposteriorurethralstenosis
AT mpons mitrofanoffcontinentvesicostomyasatreatmentoptionforepidermolysisbullosacomplicatedbyposteriorurethralstenosis
AT mlpolimerol mitrofanoffcontinentvesicostomyasatreatmentoptionforepidermolysisbullosacomplicatedbyposteriorurethralstenosis