Malignant peripheral nerve sheath tumor in a child
Among the diverse causes of posterior mediastinal masses, malignant peripheral nerve sheath tumors is a very rare neurogenic tumor. Imaging features tend to be variable. A 20-month-old toddler presented with a 3-month history of persistent diffuse thoracic and abdominal pain. A chest magnetic resona...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Elsevier
2021-01-01
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| Series: | Radiology Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S1930043320305471 |
| _version_ | 1819052719396093952 |
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| author | Brian Daniel Noreña-Rengifo, MD Lina Marcela Cadavid-Alvarez, RR Patricia Eugenia Gil-Serrano, RR Gabriel Jaime Varela-Aguirre, PR |
| author_facet | Brian Daniel Noreña-Rengifo, MD Lina Marcela Cadavid-Alvarez, RR Patricia Eugenia Gil-Serrano, RR Gabriel Jaime Varela-Aguirre, PR |
| author_sort | Brian Daniel Noreña-Rengifo, MD |
| collection | DOAJ |
| description | Among the diverse causes of posterior mediastinal masses, malignant peripheral nerve sheath tumors is a very rare neurogenic tumor. Imaging features tend to be variable. A 20-month-old toddler presented with a 3-month history of persistent diffuse thoracic and abdominal pain. A chest magnetic resonance imaging was taken and shown a posterior mediastinal lesion. Histopathology and immunohistochemical analysis confirmed the diagnosis of a malignant peripheral nerve sheath tumor with myxoid areas.Malignant peripheral nerve sheath tumors are an uncommon entity in the children with a poor prognosis. Magnetic resonance imaging is the preferred technique in children to limit the use of ionizing radiation and because has a higher contrast resolution; however, all suspicious tumors should be biopsied to make an appropriate diagnosis. Treatment is radical surgery with excision of the entire mass; however, there is a high incidence of local recurrence. |
| first_indexed | 2024-12-21T12:24:18Z |
| format | Article |
| id | doaj.art-17b91ccd51b2404bb04a376ea9a9250d |
| institution | Directory Open Access Journal |
| issn | 1930-0433 |
| language | English |
| last_indexed | 2024-12-21T12:24:18Z |
| publishDate | 2021-01-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj.art-17b91ccd51b2404bb04a376ea9a9250d2022-12-21T19:04:14ZengElsevierRadiology Case Reports1930-04332021-01-01161145151Malignant peripheral nerve sheath tumor in a childBrian Daniel Noreña-Rengifo, MD0Lina Marcela Cadavid-Alvarez, RR1Patricia Eugenia Gil-Serrano, RR2Gabriel Jaime Varela-Aguirre, PR3Department of Radiology, Universidad de Antioquia, Medellín, Colombia; Corresponding author.Department of Radiology, Hospital Pablo Tobón Uribe, Medellín, Colombia; Department of Radiology, IMEDI, Rionegro, ColombiaDepartment of Radiology, Sura Ayudas Diagnósticas, Cali, ColombiaDepartment of Radiology, Hospital Pablo Tobón Uribe, Medellín, ColombiaAmong the diverse causes of posterior mediastinal masses, malignant peripheral nerve sheath tumors is a very rare neurogenic tumor. Imaging features tend to be variable. A 20-month-old toddler presented with a 3-month history of persistent diffuse thoracic and abdominal pain. A chest magnetic resonance imaging was taken and shown a posterior mediastinal lesion. Histopathology and immunohistochemical analysis confirmed the diagnosis of a malignant peripheral nerve sheath tumor with myxoid areas.Malignant peripheral nerve sheath tumors are an uncommon entity in the children with a poor prognosis. Magnetic resonance imaging is the preferred technique in children to limit the use of ionizing radiation and because has a higher contrast resolution; however, all suspicious tumors should be biopsied to make an appropriate diagnosis. Treatment is radical surgery with excision of the entire mass; however, there is a high incidence of local recurrence.http://www.sciencedirect.com/science/article/pii/S1930043320305471Malignant peripheral nerve sheath tumorNerve sheath neoplasmsPeripheral nerveChildNeurofibromaSchwannoma |
| spellingShingle | Brian Daniel Noreña-Rengifo, MD Lina Marcela Cadavid-Alvarez, RR Patricia Eugenia Gil-Serrano, RR Gabriel Jaime Varela-Aguirre, PR Malignant peripheral nerve sheath tumor in a child Radiology Case Reports Malignant peripheral nerve sheath tumor Nerve sheath neoplasms Peripheral nerve Child Neurofibroma Schwannoma |
| title | Malignant peripheral nerve sheath tumor in a child |
| title_full | Malignant peripheral nerve sheath tumor in a child |
| title_fullStr | Malignant peripheral nerve sheath tumor in a child |
| title_full_unstemmed | Malignant peripheral nerve sheath tumor in a child |
| title_short | Malignant peripheral nerve sheath tumor in a child |
| title_sort | malignant peripheral nerve sheath tumor in a child |
| topic | Malignant peripheral nerve sheath tumor Nerve sheath neoplasms Peripheral nerve Child Neurofibroma Schwannoma |
| url | http://www.sciencedirect.com/science/article/pii/S1930043320305471 |
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