A rare variant of intracardiac total anomalous pulmonary venous connection

Total anomalous pulmonary venous connection (TAPVC) with direct connection of the pulmonary veins to the morphologically right atrium is exceedingly rare other than in the setting of isomerism of the right atrial appendages. We present an interesting case of TAPVC in a patient with situs solitus tha...

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Main Authors: Arun Gopalakrishnan, Venkateshwaran Subramanian, Bijulal Sasidharan, Deepa Sasikumar, Kavassery Mahadevan Krishnamoorthy, Baiju S. Dharan, Ajitkumar Valaparambil
Format: Article
Language:English
Published: Elsevier 2017-11-01
Series:Revista Portuguesa de Cardiologia
Online Access:http://www.sciencedirect.com/science/article/pii/S0870255117307825
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author Arun Gopalakrishnan
Venkateshwaran Subramanian
Bijulal Sasidharan
Deepa Sasikumar
Kavassery Mahadevan Krishnamoorthy
Baiju S. Dharan
Ajitkumar Valaparambil
author_facet Arun Gopalakrishnan
Venkateshwaran Subramanian
Bijulal Sasidharan
Deepa Sasikumar
Kavassery Mahadevan Krishnamoorthy
Baiju S. Dharan
Ajitkumar Valaparambil
author_sort Arun Gopalakrishnan
collection DOAJ
description Total anomalous pulmonary venous connection (TAPVC) with direct connection of the pulmonary veins to the morphologically right atrium is exceedingly rare other than in the setting of isomerism of the right atrial appendages. We present an interesting case of TAPVC in a patient with situs solitus that connected to the right atrium via a broad-mouthed common chamber. Resumo: As variantes de retorno venoso pulmonar anómalo total (RVPAT) que resultam de conexão e de drenagem direta das veias pulmonares à aurícula morfologicamente direita são extremamente raras, exceto no caso de presença de isomerismo direito. Apresentamos um caso de RVPAT, com drenagem à aurícula direita através de um coletor comum, num doente com situs solitus. Keywords: Total anomalous pulmonary venous connection, Cardiac total anomalous pulmonary venous connection, Supracardiac total anomalous pulmonary venous connection, Palavras-chave: Conexão anómala total das veias pulmonares, Conexão anómala total de veias pulmonares cardíaca, Conexão anómala total de veias pulmonares supracardíaca
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spelling doaj.art-17cbbc014f2f4e4b962697e6b20365962022-12-22T00:02:11ZengElsevierRevista Portuguesa de Cardiologia0870-25512017-11-013611869.e1869.e4A rare variant of intracardiac total anomalous pulmonary venous connectionArun Gopalakrishnan0Venkateshwaran Subramanian1Bijulal Sasidharan2Deepa Sasikumar3Kavassery Mahadevan Krishnamoorthy4Baiju S. Dharan5Ajitkumar Valaparambil6Sree Chitra Tirunal Institute for Medical Sciences and Technology, Department of Cardiology, Thiruvananthapuram, India; Corresponding author.Sree Chitra Tirunal Institute for Medical Sciences and Technology, Department of Cardiology, Thiruvananthapuram, IndiaSree Chitra Tirunal Institute for Medical Sciences and Technology, Department of Cardiology, Thiruvananthapuram, IndiaSree Chitra Tirunal Institute for Medical Sciences and Technology, Department of Cardiology, Thiruvananthapuram, IndiaSree Chitra Tirunal Institute for Medical Sciences and Technology, Department of Cardiology, Thiruvananthapuram, IndiaSree Chitra Tirunal Institute for Medical Sciences and Technology, Department of Cardiovascular and Thoracic Surgery, Division of Congenital Heart Surgery, Thiruvananthapuram, IndiaSree Chitra Tirunal Institute for Medical Sciences and Technology, Department of Cardiology, Thiruvananthapuram, IndiaTotal anomalous pulmonary venous connection (TAPVC) with direct connection of the pulmonary veins to the morphologically right atrium is exceedingly rare other than in the setting of isomerism of the right atrial appendages. We present an interesting case of TAPVC in a patient with situs solitus that connected to the right atrium via a broad-mouthed common chamber. Resumo: As variantes de retorno venoso pulmonar anómalo total (RVPAT) que resultam de conexão e de drenagem direta das veias pulmonares à aurícula morfologicamente direita são extremamente raras, exceto no caso de presença de isomerismo direito. Apresentamos um caso de RVPAT, com drenagem à aurícula direita através de um coletor comum, num doente com situs solitus. Keywords: Total anomalous pulmonary venous connection, Cardiac total anomalous pulmonary venous connection, Supracardiac total anomalous pulmonary venous connection, Palavras-chave: Conexão anómala total das veias pulmonares, Conexão anómala total de veias pulmonares cardíaca, Conexão anómala total de veias pulmonares supracardíacahttp://www.sciencedirect.com/science/article/pii/S0870255117307825
spellingShingle Arun Gopalakrishnan
Venkateshwaran Subramanian
Bijulal Sasidharan
Deepa Sasikumar
Kavassery Mahadevan Krishnamoorthy
Baiju S. Dharan
Ajitkumar Valaparambil
A rare variant of intracardiac total anomalous pulmonary venous connection
Revista Portuguesa de Cardiologia
title A rare variant of intracardiac total anomalous pulmonary venous connection
title_full A rare variant of intracardiac total anomalous pulmonary venous connection
title_fullStr A rare variant of intracardiac total anomalous pulmonary venous connection
title_full_unstemmed A rare variant of intracardiac total anomalous pulmonary venous connection
title_short A rare variant of intracardiac total anomalous pulmonary venous connection
title_sort rare variant of intracardiac total anomalous pulmonary venous connection
url http://www.sciencedirect.com/science/article/pii/S0870255117307825
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