A rare variant of intracardiac total anomalous pulmonary venous connection
Total anomalous pulmonary venous connection (TAPVC) with direct connection of the pulmonary veins to the morphologically right atrium is exceedingly rare other than in the setting of isomerism of the right atrial appendages. We present an interesting case of TAPVC in a patient with situs solitus tha...
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Elsevier
2017-11-01
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Series: | Revista Portuguesa de Cardiologia |
Online Access: | http://www.sciencedirect.com/science/article/pii/S0870255117307825 |
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author | Arun Gopalakrishnan Venkateshwaran Subramanian Bijulal Sasidharan Deepa Sasikumar Kavassery Mahadevan Krishnamoorthy Baiju S. Dharan Ajitkumar Valaparambil |
author_facet | Arun Gopalakrishnan Venkateshwaran Subramanian Bijulal Sasidharan Deepa Sasikumar Kavassery Mahadevan Krishnamoorthy Baiju S. Dharan Ajitkumar Valaparambil |
author_sort | Arun Gopalakrishnan |
collection | DOAJ |
description | Total anomalous pulmonary venous connection (TAPVC) with direct connection of the pulmonary veins to the morphologically right atrium is exceedingly rare other than in the setting of isomerism of the right atrial appendages. We present an interesting case of TAPVC in a patient with situs solitus that connected to the right atrium via a broad-mouthed common chamber. Resumo: As variantes de retorno venoso pulmonar anómalo total (RVPAT) que resultam de conexão e de drenagem direta das veias pulmonares à aurícula morfologicamente direita são extremamente raras, exceto no caso de presença de isomerismo direito. Apresentamos um caso de RVPAT, com drenagem à aurícula direita através de um coletor comum, num doente com situs solitus. Keywords: Total anomalous pulmonary venous connection, Cardiac total anomalous pulmonary venous connection, Supracardiac total anomalous pulmonary venous connection, Palavras-chave: Conexão anómala total das veias pulmonares, Conexão anómala total de veias pulmonares cardíaca, Conexão anómala total de veias pulmonares supracardíaca |
first_indexed | 2024-12-13T02:46:18Z |
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id | doaj.art-17cbbc014f2f4e4b962697e6b2036596 |
institution | Directory Open Access Journal |
issn | 0870-2551 |
language | English |
last_indexed | 2024-12-13T02:46:18Z |
publishDate | 2017-11-01 |
publisher | Elsevier |
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series | Revista Portuguesa de Cardiologia |
spelling | doaj.art-17cbbc014f2f4e4b962697e6b20365962022-12-22T00:02:11ZengElsevierRevista Portuguesa de Cardiologia0870-25512017-11-013611869.e1869.e4A rare variant of intracardiac total anomalous pulmonary venous connectionArun Gopalakrishnan0Venkateshwaran Subramanian1Bijulal Sasidharan2Deepa Sasikumar3Kavassery Mahadevan Krishnamoorthy4Baiju S. Dharan5Ajitkumar Valaparambil6Sree Chitra Tirunal Institute for Medical Sciences and Technology, Department of Cardiology, Thiruvananthapuram, India; Corresponding author.Sree Chitra Tirunal Institute for Medical Sciences and Technology, Department of Cardiology, Thiruvananthapuram, IndiaSree Chitra Tirunal Institute for Medical Sciences and Technology, Department of Cardiology, Thiruvananthapuram, IndiaSree Chitra Tirunal Institute for Medical Sciences and Technology, Department of Cardiology, Thiruvananthapuram, IndiaSree Chitra Tirunal Institute for Medical Sciences and Technology, Department of Cardiology, Thiruvananthapuram, IndiaSree Chitra Tirunal Institute for Medical Sciences and Technology, Department of Cardiovascular and Thoracic Surgery, Division of Congenital Heart Surgery, Thiruvananthapuram, IndiaSree Chitra Tirunal Institute for Medical Sciences and Technology, Department of Cardiology, Thiruvananthapuram, IndiaTotal anomalous pulmonary venous connection (TAPVC) with direct connection of the pulmonary veins to the morphologically right atrium is exceedingly rare other than in the setting of isomerism of the right atrial appendages. We present an interesting case of TAPVC in a patient with situs solitus that connected to the right atrium via a broad-mouthed common chamber. Resumo: As variantes de retorno venoso pulmonar anómalo total (RVPAT) que resultam de conexão e de drenagem direta das veias pulmonares à aurícula morfologicamente direita são extremamente raras, exceto no caso de presença de isomerismo direito. Apresentamos um caso de RVPAT, com drenagem à aurícula direita através de um coletor comum, num doente com situs solitus. Keywords: Total anomalous pulmonary venous connection, Cardiac total anomalous pulmonary venous connection, Supracardiac total anomalous pulmonary venous connection, Palavras-chave: Conexão anómala total das veias pulmonares, Conexão anómala total de veias pulmonares cardíaca, Conexão anómala total de veias pulmonares supracardíacahttp://www.sciencedirect.com/science/article/pii/S0870255117307825 |
spellingShingle | Arun Gopalakrishnan Venkateshwaran Subramanian Bijulal Sasidharan Deepa Sasikumar Kavassery Mahadevan Krishnamoorthy Baiju S. Dharan Ajitkumar Valaparambil A rare variant of intracardiac total anomalous pulmonary venous connection Revista Portuguesa de Cardiologia |
title | A rare variant of intracardiac total anomalous pulmonary venous connection |
title_full | A rare variant of intracardiac total anomalous pulmonary venous connection |
title_fullStr | A rare variant of intracardiac total anomalous pulmonary venous connection |
title_full_unstemmed | A rare variant of intracardiac total anomalous pulmonary venous connection |
title_short | A rare variant of intracardiac total anomalous pulmonary venous connection |
title_sort | rare variant of intracardiac total anomalous pulmonary venous connection |
url | http://www.sciencedirect.com/science/article/pii/S0870255117307825 |
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