A rare cause of cyanosis in childhood: Pulmonary arteriovenous malformation
Pulmonary arteriovenous malformation, which is defined as the presence of an ab-normal connection between the pulmonary artery and pulmonary vein, is rarely seen. Although it generally presents as a congenital condition, it may be accompanied by hereditary hemorrhagic telangiectasia. Clinical signs...
| Main Authors: | , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
KARE Publishing
2017-09-01
|
| Series: | Türk Kardiyoloji Derneği Arşivi |
| Subjects: | |
| Online Access: | https://jag.journalagent.com/z4/download_fulltext.asp?pdir=tkd&un=TKDA-57262 |
| _version_ | 1797920345194233856 |
|---|---|
| author | Osman Güvenç Murat Saygı İbrahim Halil Demir Ender Ödemiş |
| author_facet | Osman Güvenç Murat Saygı İbrahim Halil Demir Ender Ödemiş |
| author_sort | Osman Güvenç |
| collection | DOAJ |
| description | Pulmonary arteriovenous malformation, which is defined as the presence of an ab-normal connection between the pulmonary artery and pulmonary vein, is rarely seen. Although it generally presents as a congenital condition, it may be accompanied by hereditary hemorrhagic telangiectasia. Clinical signs vary according to the amount of shunt in proportion to the number and size of the fistulae. Patients may present with cyanosis and respiratory trouble. If the disease remains untreated, it may result in cardiac failure and ineffective endocarditis, thereby leading to the rupture of the an-eurysmal fistula. Transcatheter embolization of abnormal vascular connection is the current treatment method in this disease. This article describes the case of an 8½-year-old child. He was presented with the symptom of getting tired quickly. Transcutaneous oxygen saturation of 75%, and pulmonary arteriovenous malfor-mation was detected in his examination. Successful transcatheter fistula embolization was performed. |
| first_indexed | 2024-04-10T13:59:38Z |
| format | Article |
| id | doaj.art-18108820e24f456597c71e668ebe6ee9 |
| institution | Directory Open Access Journal |
| issn | 1016-5169 |
| language | English |
| last_indexed | 2024-04-10T13:59:38Z |
| publishDate | 2017-09-01 |
| publisher | KARE Publishing |
| record_format | Article |
| series | Türk Kardiyoloji Derneği Arşivi |
| spelling | doaj.art-18108820e24f456597c71e668ebe6ee92023-02-15T16:10:19ZengKARE PublishingTürk Kardiyoloji Derneği Arşivi1016-51692017-09-0145653854010.5543/tkda.2016.57262TKDA-57262A rare cause of cyanosis in childhood: Pulmonary arteriovenous malformationOsman Güvenç0Murat Saygı1İbrahim Halil Demir2Ender Ödemiş3Department of Pediatric Cardiology, Gynecologic and Pediatric Hospital, Batman, TurkeyDepartment of Pediatric Cardiology, Gaziosmanpaşa Taksim Training and Research Hospital, İstanbul, TurkeyDepartment of Pediatric Cardiology, Acıbadem University Faculty of Medicine, Istanbul, TurkeyDepartment of Pediatric Cardiology, Acıbadem University Faculty of Medicine, Istanbul, TurkeyPulmonary arteriovenous malformation, which is defined as the presence of an ab-normal connection between the pulmonary artery and pulmonary vein, is rarely seen. Although it generally presents as a congenital condition, it may be accompanied by hereditary hemorrhagic telangiectasia. Clinical signs vary according to the amount of shunt in proportion to the number and size of the fistulae. Patients may present with cyanosis and respiratory trouble. If the disease remains untreated, it may result in cardiac failure and ineffective endocarditis, thereby leading to the rupture of the an-eurysmal fistula. Transcatheter embolization of abnormal vascular connection is the current treatment method in this disease. This article describes the case of an 8½-year-old child. He was presented with the symptom of getting tired quickly. Transcutaneous oxygen saturation of 75%, and pulmonary arteriovenous malfor-mation was detected in his examination. Successful transcatheter fistula embolization was performed.https://jag.journalagent.com/z4/download_fulltext.asp?pdir=tkd&un=TKDA-57262childfistula embolizationpulmonary arteriovenous malformationcyanosis. |
| spellingShingle | Osman Güvenç Murat Saygı İbrahim Halil Demir Ender Ödemiş A rare cause of cyanosis in childhood: Pulmonary arteriovenous malformation Türk Kardiyoloji Derneği Arşivi child fistula embolization pulmonary arteriovenous malformation cyanosis. |
| title | A rare cause of cyanosis in childhood: Pulmonary arteriovenous malformation |
| title_full | A rare cause of cyanosis in childhood: Pulmonary arteriovenous malformation |
| title_fullStr | A rare cause of cyanosis in childhood: Pulmonary arteriovenous malformation |
| title_full_unstemmed | A rare cause of cyanosis in childhood: Pulmonary arteriovenous malformation |
| title_short | A rare cause of cyanosis in childhood: Pulmonary arteriovenous malformation |
| title_sort | rare cause of cyanosis in childhood pulmonary arteriovenous malformation |
| topic | child fistula embolization pulmonary arteriovenous malformation cyanosis. |
| url | https://jag.journalagent.com/z4/download_fulltext.asp?pdir=tkd&un=TKDA-57262 |
| work_keys_str_mv | AT osmanguvenc ararecauseofcyanosisinchildhoodpulmonaryarteriovenousmalformation AT muratsaygı ararecauseofcyanosisinchildhoodpulmonaryarteriovenousmalformation AT ibrahimhalildemir ararecauseofcyanosisinchildhoodpulmonaryarteriovenousmalformation AT enderodemis ararecauseofcyanosisinchildhoodpulmonaryarteriovenousmalformation AT osmanguvenc rarecauseofcyanosisinchildhoodpulmonaryarteriovenousmalformation AT muratsaygı rarecauseofcyanosisinchildhoodpulmonaryarteriovenousmalformation AT ibrahimhalildemir rarecauseofcyanosisinchildhoodpulmonaryarteriovenousmalformation AT enderodemis rarecauseofcyanosisinchildhoodpulmonaryarteriovenousmalformation |