Cardiac MRI in a Patient with Coincident Left Ventricular Non-Compaction and Hypertrophic Cardiomyopathy
Left ventricular non-compaction cardiomyopathy is a rare congenital cardiomyopathy that affects both children and adults. Since the clinical manifestations are not sufficient to establish diagnosis, echocardiography is the diagnostic tool that makes it possible to document ventricular non-compaction...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Tehran University of Medical Sciences
2011-12-01
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| Series: | Journal of Tehran University Heart Center |
| Subjects: | |
| Online Access: | http://journals.tums.ac.ir/PdfMed.aspx?pdf_med=/upload_files/pdf/20053.pdf&manuscript_id=20053 |
| _version_ | 1818458206413783040 |
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| author | Zahra Alizadeh-Sani Shabnam Madadi Anita Sadeghpour Zahra Khajali Pedram Golnari Majid Kiavar |
| author_facet | Zahra Alizadeh-Sani Shabnam Madadi Anita Sadeghpour Zahra Khajali Pedram Golnari Majid Kiavar |
| author_sort | Zahra Alizadeh-Sani |
| collection | DOAJ |
| description | Left ventricular non-compaction cardiomyopathy is a rare congenital cardiomyopathy that affects both children and adults. Since the clinical manifestations are not sufficient to establish diagnosis, echocardiography is the diagnostic tool that makes it possible to document ventricular non-compaction and establish prognostic factors. We report a 47-year-old woman with a history of dilated cardiomyopathy with unknown etiology. Echocardiography showed mild left ventricular enlargement with severe systolic dysfunction (EF = 20-25%). According to cardiac magnetic resonance imaging findings non-compaction left ventricle with hypertrophic cardiomyopathy was considered, and right ventricular septal biopsy was recommended. Right ventricular endomyocardial biopsy showed moderate hypertrophy of cardiac myocytes with foci of myocytolysis and moderate interstitial fibrosis. No evidence of infiltrative deposition was seen. |
| first_indexed | 2024-12-14T22:54:46Z |
| format | Article |
| id | doaj.art-186110211ee24bf9a39e31ae0b28379a |
| institution | Directory Open Access Journal |
| issn | 1735-8620 |
| language | English |
| last_indexed | 2024-12-14T22:54:46Z |
| publishDate | 2011-12-01 |
| publisher | Tehran University of Medical Sciences |
| record_format | Article |
| series | Journal of Tehran University Heart Center |
| spelling | doaj.art-186110211ee24bf9a39e31ae0b28379a2022-12-21T22:44:37ZengTehran University of Medical SciencesJournal of Tehran University Heart Center1735-86202011-12-0164214216Cardiac MRI in a Patient with Coincident Left Ventricular Non-Compaction and Hypertrophic CardiomyopathyZahra Alizadeh-SaniShabnam MadadiAnita SadeghpourZahra KhajaliPedram GolnariMajid KiavarLeft ventricular non-compaction cardiomyopathy is a rare congenital cardiomyopathy that affects both children and adults. Since the clinical manifestations are not sufficient to establish diagnosis, echocardiography is the diagnostic tool that makes it possible to document ventricular non-compaction and establish prognostic factors. We report a 47-year-old woman with a history of dilated cardiomyopathy with unknown etiology. Echocardiography showed mild left ventricular enlargement with severe systolic dysfunction (EF = 20-25%). According to cardiac magnetic resonance imaging findings non-compaction left ventricle with hypertrophic cardiomyopathy was considered, and right ventricular septal biopsy was recommended. Right ventricular endomyocardial biopsy showed moderate hypertrophy of cardiac myocytes with foci of myocytolysis and moderate interstitial fibrosis. No evidence of infiltrative deposition was seen.http://journals.tums.ac.ir/PdfMed.aspx?pdf_med=/upload_files/pdf/20053.pdf&manuscript_id=20053Magnetic resonance imagingCardiomyopathiesHeart defect, congenital |
| spellingShingle | Zahra Alizadeh-Sani Shabnam Madadi Anita Sadeghpour Zahra Khajali Pedram Golnari Majid Kiavar Cardiac MRI in a Patient with Coincident Left Ventricular Non-Compaction and Hypertrophic Cardiomyopathy Journal of Tehran University Heart Center Magnetic resonance imaging Cardiomyopathies Heart defect, congenital |
| title | Cardiac MRI in a Patient with Coincident Left Ventricular Non-Compaction and Hypertrophic Cardiomyopathy |
| title_full | Cardiac MRI in a Patient with Coincident Left Ventricular Non-Compaction and Hypertrophic Cardiomyopathy |
| title_fullStr | Cardiac MRI in a Patient with Coincident Left Ventricular Non-Compaction and Hypertrophic Cardiomyopathy |
| title_full_unstemmed | Cardiac MRI in a Patient with Coincident Left Ventricular Non-Compaction and Hypertrophic Cardiomyopathy |
| title_short | Cardiac MRI in a Patient with Coincident Left Ventricular Non-Compaction and Hypertrophic Cardiomyopathy |
| title_sort | cardiac mri in a patient with coincident left ventricular non compaction and hypertrophic cardiomyopathy |
| topic | Magnetic resonance imaging Cardiomyopathies Heart defect, congenital |
| url | http://journals.tums.ac.ir/PdfMed.aspx?pdf_med=/upload_files/pdf/20053.pdf&manuscript_id=20053 |
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