A Case of Rasmussen Encephalitis: The Differential Diagnoses and Role of Diagnostic Imaging

Rasmussen encephalitis is an extremely rare chronic inflammatory neurodegenerative disease affecting a single cerebral hemisphere, causing progressive neurological deterioration and intractable seizures. Imaging plays an important role in diagnosis by demonstrating focal or unihemispheric involvemen...

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Bibliographic Details
Main Authors: Binoj Varghese, MK Aneesh, Navdeep Singh, Percival Gilwaz
Format: Article
Language:English
Published: Oman Medical Specialty Board 2014-01-01
Series:Oman Medical Journal
Subjects:
Online Access:http://www.omjournal.org/fultext_PDF.aspx?DetailsID=482&type=fultext
Description
Summary:Rasmussen encephalitis is an extremely rare chronic inflammatory neurodegenerative disease affecting a single cerebral hemisphere, causing progressive neurological deterioration and intractable seizures. Imaging plays an important role in diagnosis by demonstrating focal or unihemispheric involvement and excluding other possible causes. Here, we report a case of Rasmussen encephalitis with an update on recent diagnostic criteria and emphasis on differential diagnoses which can be excluded on imaging.
ISSN:1999-768X
2070-5204