Total Hip Arthroplasty in a Patient With Fascioscapulohumeral Dystrophy
Facioscapulohumeral dystrophy is an autosomal dominant disorder that results in progressive muscle weakness. Patients most commonly present with facial and periscapular muscle weakness, which progresses to involve their upper and lower extremities as well as truncal muscles. We present a patient wit...
| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
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Elsevier
2023-02-01
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| Series: | Arthroplasty Today |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2352344122001856 |
| _version_ | 1797924693198503936 |
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| author | Rachel A. Thomas, MD Dennis J. Warfield, Jr., MD Lucas E. Nikkel, MD |
| author_facet | Rachel A. Thomas, MD Dennis J. Warfield, Jr., MD Lucas E. Nikkel, MD |
| author_sort | Rachel A. Thomas, MD |
| collection | DOAJ |
| description | Facioscapulohumeral dystrophy is an autosomal dominant disorder that results in progressive muscle weakness. Patients most commonly present with facial and periscapular muscle weakness, which progresses to involve their upper and lower extremities as well as truncal muscles. We present a patient with facioscapulohumeral dystrophy who underwent staged bilateral total hip arthroplasties but developed late prosthetic joint infection. This case also reports the management of periprosthetic joint infection after total hip arthroplasties through explant and placement of an articulating spacer as well as both neuraxial and general anesthetic management for this uncommon neuromuscular disorder. |
| first_indexed | 2024-04-10T15:05:00Z |
| format | Article |
| id | doaj.art-1a3dc11346244d38b830de6cf28d1810 |
| institution | Directory Open Access Journal |
| issn | 2352-3441 |
| language | English |
| last_indexed | 2024-04-10T15:05:00Z |
| publishDate | 2023-02-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Arthroplasty Today |
| spelling | doaj.art-1a3dc11346244d38b830de6cf28d18102023-02-15T04:28:17ZengElsevierArthroplasty Today2352-34412023-02-0119101021Total Hip Arthroplasty in a Patient With Fascioscapulohumeral DystrophyRachel A. Thomas, MD0Dennis J. Warfield, Jr., MD1Lucas E. Nikkel, MD2Orthopaedic Surgery, Penn State Health Milton S. Hershey Medical Center, Hershey, PA, USA; Corresponding author. Orthopaedic Surgery, Penn State Health Milton S. Hershey Medical Center, 500 University Drive, Hershey, PA 17033, USA. Tel.: +1 262 389 6996.Anesthesiology and Perioperative Medicine, Penn State Health Milton S. Hershey Medical Center, Hershey, PA, USAOrthopaedic Surgery, Penn State Health Milton S. Hershey Medical Center, Hershey, PA, USAFacioscapulohumeral dystrophy is an autosomal dominant disorder that results in progressive muscle weakness. Patients most commonly present with facial and periscapular muscle weakness, which progresses to involve their upper and lower extremities as well as truncal muscles. We present a patient with facioscapulohumeral dystrophy who underwent staged bilateral total hip arthroplasties but developed late prosthetic joint infection. This case also reports the management of periprosthetic joint infection after total hip arthroplasties through explant and placement of an articulating spacer as well as both neuraxial and general anesthetic management for this uncommon neuromuscular disorder.http://www.sciencedirect.com/science/article/pii/S2352344122001856Fascioscapulohumeral dystrophyTotal hip arthroplastyPeriprosthetic joint infectionMuscular dystrophy anesthesia |
| spellingShingle | Rachel A. Thomas, MD Dennis J. Warfield, Jr., MD Lucas E. Nikkel, MD Total Hip Arthroplasty in a Patient With Fascioscapulohumeral Dystrophy Arthroplasty Today Fascioscapulohumeral dystrophy Total hip arthroplasty Periprosthetic joint infection Muscular dystrophy anesthesia |
| title | Total Hip Arthroplasty in a Patient With Fascioscapulohumeral Dystrophy |
| title_full | Total Hip Arthroplasty in a Patient With Fascioscapulohumeral Dystrophy |
| title_fullStr | Total Hip Arthroplasty in a Patient With Fascioscapulohumeral Dystrophy |
| title_full_unstemmed | Total Hip Arthroplasty in a Patient With Fascioscapulohumeral Dystrophy |
| title_short | Total Hip Arthroplasty in a Patient With Fascioscapulohumeral Dystrophy |
| title_sort | total hip arthroplasty in a patient with fascioscapulohumeral dystrophy |
| topic | Fascioscapulohumeral dystrophy Total hip arthroplasty Periprosthetic joint infection Muscular dystrophy anesthesia |
| url | http://www.sciencedirect.com/science/article/pii/S2352344122001856 |
| work_keys_str_mv | AT rachelathomasmd totalhiparthroplastyinapatientwithfascioscapulohumeraldystrophy AT dennisjwarfieldjrmd totalhiparthroplastyinapatientwithfascioscapulohumeraldystrophy AT lucasenikkelmd totalhiparthroplastyinapatientwithfascioscapulohumeraldystrophy |