A rare clinical case of pulmonary artery sarcoma
Pulmonary artery sarcoma (PAS) is a malignant and very rare tumor with frequent misdiagnosis. A rare clinical case with this pathology is presented. The patient had daily fever for 6 months, he was examined in various hospitals, but the cause of fever could not be determined. In our hospital, echoca...
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Столичная издательская компания
2024-03-01
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Series: | Рациональная фармакотерапия в кардиологии |
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Online Access: | https://www.rpcardio.online/jour/article/view/2984 |
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author | G. R. Bikbaeva A. N. Kovalskaya A. P. Rodin G. V. Salamov T. V. Pavlova D. V. Duplyakov |
author_facet | G. R. Bikbaeva A. N. Kovalskaya A. P. Rodin G. V. Salamov T. V. Pavlova D. V. Duplyakov |
author_sort | G. R. Bikbaeva |
collection | DOAJ |
description | Pulmonary artery sarcoma (PAS) is a malignant and very rare tumor with frequent misdiagnosis. A rare clinical case with this pathology is presented. The patient had daily fever for 6 months, he was examined in various hospitals, but the cause of fever could not be determined. In our hospital, echocardiography revealed a mass in the left pulmonary artery (PA) with obstruction. CT-angiopulmonography showed a filling defect in the left PA, blocking the lumen of the artery by 90%. According to histopathology, the patient was diagnosed with pulmonary artery sarcoma. Subsequently, the following was performed: thrombendarterectomy from the pulmonary artery, combined pneumonectomy on the left side, suturing of the secondary atrial septal defect, followed by 3 courses of monochemotherapy with paclitaxel. After 1 year and 9 months, due to disease progression the patient died. The prognosis of PAS depends on early diagnosis, so doctors should be aware of this disease and use the best treatment options. |
first_indexed | 2024-04-24T15:53:19Z |
format | Article |
id | doaj.art-1ab17468979e43bbb80d06a753442af9 |
institution | Directory Open Access Journal |
issn | 1819-6446 2225-3653 |
language | English |
last_indexed | 2025-02-17T22:14:11Z |
publishDate | 2024-03-01 |
publisher | Столичная издательская компания |
record_format | Article |
series | Рациональная фармакотерапия в кардиологии |
spelling | doaj.art-1ab17468979e43bbb80d06a753442af92024-12-04T11:48:22ZengСтоличная издательская компанияРациональная фармакотерапия в кардиологии1819-64462225-36532024-03-01201525610.20996/1819-6446-2024-29842182A rare clinical case of pulmonary artery sarcomaG. R. Bikbaeva0A. N. Kovalskaya1A. P. Rodin2G. V. Salamov3T. V. Pavlova4D. V. Duplyakov5V. P. Polyakov Samara Regional Clinical Cardiology Dispensary; Samara State Medical UniversitySamara State Medical UniversitySamara State Medical UniversityV. P. Polyakov Samara Regional Clinical Cardiology Dispensary; Samara State Medical UniversityV. P. Polyakov Samara Regional Clinical Cardiology Dispensary; Samara State Medical UniversityV. P. Polyakov Samara Regional Clinical Cardiology Dispensary; Samara State Medical UniversityPulmonary artery sarcoma (PAS) is a malignant and very rare tumor with frequent misdiagnosis. A rare clinical case with this pathology is presented. The patient had daily fever for 6 months, he was examined in various hospitals, but the cause of fever could not be determined. In our hospital, echocardiography revealed a mass in the left pulmonary artery (PA) with obstruction. CT-angiopulmonography showed a filling defect in the left PA, blocking the lumen of the artery by 90%. According to histopathology, the patient was diagnosed with pulmonary artery sarcoma. Subsequently, the following was performed: thrombendarterectomy from the pulmonary artery, combined pneumonectomy on the left side, suturing of the secondary atrial septal defect, followed by 3 courses of monochemotherapy with paclitaxel. After 1 year and 9 months, due to disease progression the patient died. The prognosis of PAS depends on early diagnosis, so doctors should be aware of this disease and use the best treatment options.https://www.rpcardio.online/jour/article/view/2984pulmonary artery sarcomapulmonary embolismcomputed tomography of the thoracic cavity |
spellingShingle | G. R. Bikbaeva A. N. Kovalskaya A. P. Rodin G. V. Salamov T. V. Pavlova D. V. Duplyakov A rare clinical case of pulmonary artery sarcoma Рациональная фармакотерапия в кардиологии pulmonary artery sarcoma pulmonary embolism computed tomography of the thoracic cavity |
title | A rare clinical case of pulmonary artery sarcoma |
title_full | A rare clinical case of pulmonary artery sarcoma |
title_fullStr | A rare clinical case of pulmonary artery sarcoma |
title_full_unstemmed | A rare clinical case of pulmonary artery sarcoma |
title_short | A rare clinical case of pulmonary artery sarcoma |
title_sort | rare clinical case of pulmonary artery sarcoma |
topic | pulmonary artery sarcoma pulmonary embolism computed tomography of the thoracic cavity |
url | https://www.rpcardio.online/jour/article/view/2984 |
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