A rare clinical case of pulmonary artery sarcoma

Pulmonary artery sarcoma (PAS) is a malignant and very rare tumor with frequent misdiagnosis. A rare clinical case with this pathology is presented. The patient had daily fever for 6 months, he was examined in various hospitals, but the cause of fever could not be determined. In our hospital, echoca...

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Main Authors: G. R. Bikbaeva, A. N. Kovalskaya, A. P. Rodin, G. V. Salamov, T. V. Pavlova, D. V. Duplyakov
Format: Article
Language:English
Published: Столичная издательская компания 2024-03-01
Series:Рациональная фармакотерапия в кардиологии
Subjects:
Online Access:https://www.rpcardio.online/jour/article/view/2984
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author G. R. Bikbaeva
A. N. Kovalskaya
A. P. Rodin
G. V. Salamov
T. V. Pavlova
D. V. Duplyakov
author_facet G. R. Bikbaeva
A. N. Kovalskaya
A. P. Rodin
G. V. Salamov
T. V. Pavlova
D. V. Duplyakov
author_sort G. R. Bikbaeva
collection DOAJ
description Pulmonary artery sarcoma (PAS) is a malignant and very rare tumor with frequent misdiagnosis. A rare clinical case with this pathology is presented. The patient had daily fever for 6 months, he was examined in various hospitals, but the cause of fever could not be determined. In our hospital, echocardiography revealed a mass in the left pulmonary artery (PA) with obstruction. CT-angiopulmonography showed a filling defect in the left PA, blocking the lumen of the artery by 90%. According to histopathology, the patient was diagnosed with pulmonary artery sarcoma. Subsequently, the following was performed: thrombendarterectomy from the pulmonary artery, combined pneumonectomy on the left side, suturing of the secondary atrial septal defect, followed by 3 courses of monochemotherapy with paclitaxel. After 1 year and 9 months, due to disease progression the patient died. The prognosis of PAS depends on early diagnosis, so doctors should be aware of this disease and use the best treatment options.
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spelling doaj.art-1ab17468979e43bbb80d06a753442af92024-12-04T11:48:22ZengСтоличная издательская компанияРациональная фармакотерапия в кардиологии1819-64462225-36532024-03-01201525610.20996/1819-6446-2024-29842182A rare clinical case of pulmonary artery sarcomaG. R. Bikbaeva0A. N. Kovalskaya1A. P. Rodin2G. V. Salamov3T. V. Pavlova4D. V. Duplyakov5V. P. Polyakov Samara Regional Clinical Cardiology Dispensary; Samara State Medical UniversitySamara State Medical UniversitySamara State Medical UniversityV. P. Polyakov Samara Regional Clinical Cardiology Dispensary; Samara State Medical UniversityV. P. Polyakov Samara Regional Clinical Cardiology Dispensary; Samara State Medical UniversityV. P. Polyakov Samara Regional Clinical Cardiology Dispensary; Samara State Medical UniversityPulmonary artery sarcoma (PAS) is a malignant and very rare tumor with frequent misdiagnosis. A rare clinical case with this pathology is presented. The patient had daily fever for 6 months, he was examined in various hospitals, but the cause of fever could not be determined. In our hospital, echocardiography revealed a mass in the left pulmonary artery (PA) with obstruction. CT-angiopulmonography showed a filling defect in the left PA, blocking the lumen of the artery by 90%. According to histopathology, the patient was diagnosed with pulmonary artery sarcoma. Subsequently, the following was performed: thrombendarterectomy from the pulmonary artery, combined pneumonectomy on the left side, suturing of the secondary atrial septal defect, followed by 3 courses of monochemotherapy with paclitaxel. After 1 year and 9 months, due to disease progression the patient died. The prognosis of PAS depends on early diagnosis, so doctors should be aware of this disease and use the best treatment options.https://www.rpcardio.online/jour/article/view/2984pulmonary artery sarcomapulmonary embolismcomputed tomography of the thoracic cavity
spellingShingle G. R. Bikbaeva
A. N. Kovalskaya
A. P. Rodin
G. V. Salamov
T. V. Pavlova
D. V. Duplyakov
A rare clinical case of pulmonary artery sarcoma
Рациональная фармакотерапия в кардиологии
pulmonary artery sarcoma
pulmonary embolism
computed tomography of the thoracic cavity
title A rare clinical case of pulmonary artery sarcoma
title_full A rare clinical case of pulmonary artery sarcoma
title_fullStr A rare clinical case of pulmonary artery sarcoma
title_full_unstemmed A rare clinical case of pulmonary artery sarcoma
title_short A rare clinical case of pulmonary artery sarcoma
title_sort rare clinical case of pulmonary artery sarcoma
topic pulmonary artery sarcoma
pulmonary embolism
computed tomography of the thoracic cavity
url https://www.rpcardio.online/jour/article/view/2984
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