Airway management in Escobar syndrome: A formidable challenge
Escobar syndrome is a rare autosomal recessive disorder characterized by flexion joint and digit contractures, skin webbing, cleft palate, deformity of spine and cervical spine fusion. Associated difficult airway is mainly due to micrognathia, retrognathia, webbing of neck and limitation of the mout...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2013-01-01
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| Series: | Indian Journal of Anaesthesia |
| Subjects: | |
| Online Access: | http://www.ijaweb.org/article.asp?issn=0019-5049;year=2013;volume=57;issue=6;spage=603;epage=605;aulast=Mathew |
| _version_ | 1828238398814420992 |
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| author | Shaji Mathew Souvik Chaudhuri H D Arun Kumar Tim Thomas Joseph |
| author_facet | Shaji Mathew Souvik Chaudhuri H D Arun Kumar Tim Thomas Joseph |
| author_sort | Shaji Mathew |
| collection | DOAJ |
| description | Escobar syndrome is a rare autosomal recessive disorder characterized by flexion joint and digit contractures, skin webbing, cleft palate, deformity of spine and cervical spine fusion. Associated difficult airway is mainly due to micrognathia, retrognathia, webbing of neck and limitation of the mouth opening and neck extension. We report a case of a 1 year old child with Escobar syndrome posted for bilateral hamstrings to quadriceps transfer. The child had adequate mouth opening with no evidence of cervical spine fusion, yet we faced difficulty in intubation which was ultimately overcome by securing a proseal laryngeal mask airway (PLMA) and then by intubating with an endotracheal tube railroaded over a paediatric fibreoptic bronchoscope passed through the lumen of a PLMA. |
| first_indexed | 2024-04-12T21:04:27Z |
| format | Article |
| id | doaj.art-1ae1e450402647ac9c251ea4b9a8f078 |
| institution | Directory Open Access Journal |
| issn | 0019-5049 |
| language | English |
| last_indexed | 2024-04-12T21:04:27Z |
| publishDate | 2013-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Indian Journal of Anaesthesia |
| spelling | doaj.art-1ae1e450402647ac9c251ea4b9a8f0782022-12-22T03:16:45ZengWolters Kluwer Medknow PublicationsIndian Journal of Anaesthesia0019-50492013-01-0157660360510.4103/0019-5049.123336Airway management in Escobar syndrome: A formidable challengeShaji MathewSouvik ChaudhuriH D Arun KumarTim Thomas JosephEscobar syndrome is a rare autosomal recessive disorder characterized by flexion joint and digit contractures, skin webbing, cleft palate, deformity of spine and cervical spine fusion. Associated difficult airway is mainly due to micrognathia, retrognathia, webbing of neck and limitation of the mouth opening and neck extension. We report a case of a 1 year old child with Escobar syndrome posted for bilateral hamstrings to quadriceps transfer. The child had adequate mouth opening with no evidence of cervical spine fusion, yet we faced difficulty in intubation which was ultimately overcome by securing a proseal laryngeal mask airway (PLMA) and then by intubating with an endotracheal tube railroaded over a paediatric fibreoptic bronchoscope passed through the lumen of a PLMA.http://www.ijaweb.org/article.asp?issn=0019-5049;year=2013;volume=57;issue=6;spage=603;epage=605;aulast=MathewDifficult airwayEscobar syndromeproseal laryngeal mask airway |
| spellingShingle | Shaji Mathew Souvik Chaudhuri H D Arun Kumar Tim Thomas Joseph Airway management in Escobar syndrome: A formidable challenge Indian Journal of Anaesthesia Difficult airway Escobar syndrome proseal laryngeal mask airway |
| title | Airway management in Escobar syndrome: A formidable challenge |
| title_full | Airway management in Escobar syndrome: A formidable challenge |
| title_fullStr | Airway management in Escobar syndrome: A formidable challenge |
| title_full_unstemmed | Airway management in Escobar syndrome: A formidable challenge |
| title_short | Airway management in Escobar syndrome: A formidable challenge |
| title_sort | airway management in escobar syndrome a formidable challenge |
| topic | Difficult airway Escobar syndrome proseal laryngeal mask airway |
| url | http://www.ijaweb.org/article.asp?issn=0019-5049;year=2013;volume=57;issue=6;spage=603;epage=605;aulast=Mathew |
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