THE BASIC POINTS OF SAFE MANAGEMENT OF PREGNANCY AND DELIVERY IN PATIENTS WITH MARFAN SYNDROME
Marfan syndrome is dominantly inherited connective tissue diseases, associated with microfibrillar fiber connective tissue deficiency in vascular walls, heart valves, joints, dural membrane, bones, and other organs. Diagnosis may be confirmed by clinical criteria and molecular tests. Pregnancy bea...
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| Format: | Article |
| Language: | Russian |
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IRBIS LLC
2017-12-01
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| Series: | Акушерство, гинекология и репродукция |
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| Online Access: | https://www.gynecology.su/jour/article/view/429 |
| _version_ | 1797884113548476416 |
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| author | L. S. Radetskaya A. D. Makatsariya V. O. Bitsadze N. M. Khamani D. V. Mitryuk N. A. Makatsariya |
| author_facet | L. S. Radetskaya A. D. Makatsariya V. O. Bitsadze N. M. Khamani D. V. Mitryuk N. A. Makatsariya |
| author_sort | L. S. Radetskaya |
| collection | DOAJ |
| description | Marfan syndrome is dominantly inherited connective tissue diseases, associated with microfibrillar fiber connective tissue deficiency in vascular walls, heart valves, joints, dural membrane, bones, and other organs. Diagnosis may be confirmed by clinical criteria and molecular tests. Pregnancy bears a risk of fatal complications, including aortic dissection, aortic root dilation, mitral valve insufficiency. Women must be followed and managed in a high risk pregnancy unit by a team from obstetricians, cardiologists, anesthetists, pediatricians, neonatologists and cardiac surgeons who are skilled in high risk pregnancies. This approach allows to avoid the serious maternal and fetal complications. Caesarean section should be offered for such patients, because it minimizes the hemodynamic changes, associated with vaginal delivery. Some authors recommend to perform post-cesarean hysterectomy, because of the high incidence of massive hemorrhage in postpartum. |
| first_indexed | 2024-04-10T04:01:18Z |
| format | Article |
| id | doaj.art-1c09cbb0a3434b13831cd2049d4717c3 |
| institution | Directory Open Access Journal |
| issn | 2313-7347 2500-3194 |
| language | Russian |
| last_indexed | 2024-04-10T04:01:18Z |
| publishDate | 2017-12-01 |
| publisher | IRBIS LLC |
| record_format | Article |
| series | Акушерство, гинекология и репродукция |
| spelling | doaj.art-1c09cbb0a3434b13831cd2049d4717c32023-03-13T07:09:49ZrusIRBIS LLCАкушерство, гинекология и репродукция2313-73472500-31942017-12-01113828710.17749/2313-7347.2017.11.3.082-087405THE BASIC POINTS OF SAFE MANAGEMENT OF PREGNANCY AND DELIVERY IN PATIENTS WITH MARFAN SYNDROMEL. S. Radetskaya0A. D. Makatsariya1V. O. Bitsadze2N. M. Khamani3D. V. Mitryuk4N. A. Makatsariya5I.M. Sechenov First Moscow State Medical University, Health Ministry of Russian FederationI.M. Sechenov First Moscow State Medical University, Health Ministry of Russian FederationI.M. Sechenov First Moscow State Medical University, Health Ministry of Russian FederationI.M. Sechenov First Moscow State Medical University, Health Ministry of Russian FederationState Medical and Pharmaceutical University «Nicolae Testemitanu»I.M. Sechenov First Moscow State Medical University, Health Ministry of Russian FederationMarfan syndrome is dominantly inherited connective tissue diseases, associated with microfibrillar fiber connective tissue deficiency in vascular walls, heart valves, joints, dural membrane, bones, and other organs. Diagnosis may be confirmed by clinical criteria and molecular tests. Pregnancy bears a risk of fatal complications, including aortic dissection, aortic root dilation, mitral valve insufficiency. Women must be followed and managed in a high risk pregnancy unit by a team from obstetricians, cardiologists, anesthetists, pediatricians, neonatologists and cardiac surgeons who are skilled in high risk pregnancies. This approach allows to avoid the serious maternal and fetal complications. Caesarean section should be offered for such patients, because it minimizes the hemodynamic changes, associated with vaginal delivery. Some authors recommend to perform post-cesarean hysterectomy, because of the high incidence of massive hemorrhage in postpartum.https://www.gynecology.su/jour/article/view/429mesenchimal displasiasinherited connective tissue disordersmarfan syndromeehlers-danlos syndromeosler-weberrendu diseasepregnancyaortic dissection in pregnancycesarean sectionbleedinghemorrhage |
| spellingShingle | L. S. Radetskaya A. D. Makatsariya V. O. Bitsadze N. M. Khamani D. V. Mitryuk N. A. Makatsariya THE BASIC POINTS OF SAFE MANAGEMENT OF PREGNANCY AND DELIVERY IN PATIENTS WITH MARFAN SYNDROME Акушерство, гинекология и репродукция mesenchimal displasias inherited connective tissue disorders marfan syndrome ehlers-danlos syndrome osler-weberrendu disease pregnancy aortic dissection in pregnancy cesarean section bleeding hemorrhage |
| title | THE BASIC POINTS OF SAFE MANAGEMENT OF PREGNANCY AND DELIVERY IN PATIENTS WITH MARFAN SYNDROME |
| title_full | THE BASIC POINTS OF SAFE MANAGEMENT OF PREGNANCY AND DELIVERY IN PATIENTS WITH MARFAN SYNDROME |
| title_fullStr | THE BASIC POINTS OF SAFE MANAGEMENT OF PREGNANCY AND DELIVERY IN PATIENTS WITH MARFAN SYNDROME |
| title_full_unstemmed | THE BASIC POINTS OF SAFE MANAGEMENT OF PREGNANCY AND DELIVERY IN PATIENTS WITH MARFAN SYNDROME |
| title_short | THE BASIC POINTS OF SAFE MANAGEMENT OF PREGNANCY AND DELIVERY IN PATIENTS WITH MARFAN SYNDROME |
| title_sort | basic points of safe management of pregnancy and delivery in patients with marfan syndrome |
| topic | mesenchimal displasias inherited connective tissue disorders marfan syndrome ehlers-danlos syndrome osler-weberrendu disease pregnancy aortic dissection in pregnancy cesarean section bleeding hemorrhage |
| url | https://www.gynecology.su/jour/article/view/429 |
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