Albright′s Hereditary Osteodystrophy: A Constellation of Clinical Features

Pseudohypoparathyroidism (PHP) is an inherited metabolic disorder characterized by end-organ resistance to the action of PTH (Parathyroid Hormone). There are four types of PHPs namely Ia, lb, Ic and II. PHP Ia is associated with a constellation of clinical features referred to as Albright′s Heredita...

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Main Authors: L Ambika, Vaishali Keluskar
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2010-01-01
Series:Journal of Indian Academy of Oral Medicine and Radiology
Subjects:
Online Access:http://www.jiaomr.in/article.asp?issn=0972-1363;year=2010;volume=22;issue=4;spage=215;epage=217;aulast=Ambika;type=0
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author L Ambika
Vaishali Keluskar
author_facet L Ambika
Vaishali Keluskar
author_sort L Ambika
collection DOAJ
description Pseudohypoparathyroidism (PHP) is an inherited metabolic disorder characterized by end-organ resistance to the action of PTH (Parathyroid Hormone). There are four types of PHPs namely Ia, lb, Ic and II. PHP Ia is associated with a constellation of clinical features referred to as Albright′s Hereditary Osteodystroohy (AHO). The oral manifestation of AHO found in the literature includes aplasia and or enamel hypoplasia, late tooth eruption and enlarged radicular channels susceptible to caries. Here, we are reporting a rare case of a 14-year-old girl with Albrigt′s hereditary osteodystrophy with disintinctive oral manifesitations.
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spelling doaj.art-1c80ec4f447748b2935bcf320121e6dd2022-12-21T22:48:37ZengWolters Kluwer Medknow PublicationsJournal of Indian Academy of Oral Medicine and Radiology0972-13630975-15722010-01-01224215217Albright′s Hereditary Osteodystrophy: A Constellation of Clinical FeaturesL AmbikaVaishali KeluskarPseudohypoparathyroidism (PHP) is an inherited metabolic disorder characterized by end-organ resistance to the action of PTH (Parathyroid Hormone). There are four types of PHPs namely Ia, lb, Ic and II. PHP Ia is associated with a constellation of clinical features referred to as Albright′s Hereditary Osteodystroohy (AHO). The oral manifestation of AHO found in the literature includes aplasia and or enamel hypoplasia, late tooth eruption and enlarged radicular channels susceptible to caries. Here, we are reporting a rare case of a 14-year-old girl with Albrigt′s hereditary osteodystrophy with disintinctive oral manifesitations.http://www.jiaomr.in/article.asp?issn=0972-1363;year=2010;volume=22;issue=4;spage=215;epage=217;aulast=Ambika;type=0Albright′s hereditary osteodystrophyPseudohypoparathyroidismOral manifestation
spellingShingle L Ambika
Vaishali Keluskar
Albright′s Hereditary Osteodystrophy: A Constellation of Clinical Features
Journal of Indian Academy of Oral Medicine and Radiology
Albright′s hereditary osteodystrophy
Pseudohypoparathyroidism
Oral manifestation
title Albright′s Hereditary Osteodystrophy: A Constellation of Clinical Features
title_full Albright′s Hereditary Osteodystrophy: A Constellation of Clinical Features
title_fullStr Albright′s Hereditary Osteodystrophy: A Constellation of Clinical Features
title_full_unstemmed Albright′s Hereditary Osteodystrophy: A Constellation of Clinical Features
title_short Albright′s Hereditary Osteodystrophy: A Constellation of Clinical Features
title_sort albright s hereditary osteodystrophy a constellation of clinical features
topic Albright′s hereditary osteodystrophy
Pseudohypoparathyroidism
Oral manifestation
url http://www.jiaomr.in/article.asp?issn=0972-1363;year=2010;volume=22;issue=4;spage=215;epage=217;aulast=Ambika;type=0
work_keys_str_mv AT lambika albrightshereditaryosteodystrophyaconstellationofclinicalfeatures
AT vaishalikeluskar albrightshereditaryosteodystrophyaconstellationofclinicalfeatures