Albright′s Hereditary Osteodystrophy: A Constellation of Clinical Features
Pseudohypoparathyroidism (PHP) is an inherited metabolic disorder characterized by end-organ resistance to the action of PTH (Parathyroid Hormone). There are four types of PHPs namely Ia, lb, Ic and II. PHP Ia is associated with a constellation of clinical features referred to as Albright′s Heredita...
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Format: | Article |
Language: | English |
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Wolters Kluwer Medknow Publications
2010-01-01
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Series: | Journal of Indian Academy of Oral Medicine and Radiology |
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Online Access: | http://www.jiaomr.in/article.asp?issn=0972-1363;year=2010;volume=22;issue=4;spage=215;epage=217;aulast=Ambika;type=0 |
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author | L Ambika Vaishali Keluskar |
author_facet | L Ambika Vaishali Keluskar |
author_sort | L Ambika |
collection | DOAJ |
description | Pseudohypoparathyroidism (PHP) is an inherited metabolic disorder characterized by end-organ resistance to the action of PTH (Parathyroid Hormone). There are four types of PHPs namely Ia, lb, Ic and II. PHP Ia is associated with a constellation of clinical features referred to as Albright′s Hereditary Osteodystroohy (AHO). The oral manifestation of AHO found in the literature includes aplasia and or enamel hypoplasia, late tooth eruption and enlarged radicular channels susceptible to caries. Here, we are reporting a rare case of a 14-year-old girl with Albrigt′s hereditary osteodystrophy with disintinctive oral manifesitations. |
first_indexed | 2024-12-14T20:25:46Z |
format | Article |
id | doaj.art-1c80ec4f447748b2935bcf320121e6dd |
institution | Directory Open Access Journal |
issn | 0972-1363 0975-1572 |
language | English |
last_indexed | 2024-12-14T20:25:46Z |
publishDate | 2010-01-01 |
publisher | Wolters Kluwer Medknow Publications |
record_format | Article |
series | Journal of Indian Academy of Oral Medicine and Radiology |
spelling | doaj.art-1c80ec4f447748b2935bcf320121e6dd2022-12-21T22:48:37ZengWolters Kluwer Medknow PublicationsJournal of Indian Academy of Oral Medicine and Radiology0972-13630975-15722010-01-01224215217Albright′s Hereditary Osteodystrophy: A Constellation of Clinical FeaturesL AmbikaVaishali KeluskarPseudohypoparathyroidism (PHP) is an inherited metabolic disorder characterized by end-organ resistance to the action of PTH (Parathyroid Hormone). There are four types of PHPs namely Ia, lb, Ic and II. PHP Ia is associated with a constellation of clinical features referred to as Albright′s Hereditary Osteodystroohy (AHO). The oral manifestation of AHO found in the literature includes aplasia and or enamel hypoplasia, late tooth eruption and enlarged radicular channels susceptible to caries. Here, we are reporting a rare case of a 14-year-old girl with Albrigt′s hereditary osteodystrophy with disintinctive oral manifesitations.http://www.jiaomr.in/article.asp?issn=0972-1363;year=2010;volume=22;issue=4;spage=215;epage=217;aulast=Ambika;type=0Albright′s hereditary osteodystrophyPseudohypoparathyroidismOral manifestation |
spellingShingle | L Ambika Vaishali Keluskar Albright′s Hereditary Osteodystrophy: A Constellation of Clinical Features Journal of Indian Academy of Oral Medicine and Radiology Albright′s hereditary osteodystrophy Pseudohypoparathyroidism Oral manifestation |
title | Albright′s Hereditary Osteodystrophy: A Constellation of Clinical Features |
title_full | Albright′s Hereditary Osteodystrophy: A Constellation of Clinical Features |
title_fullStr | Albright′s Hereditary Osteodystrophy: A Constellation of Clinical Features |
title_full_unstemmed | Albright′s Hereditary Osteodystrophy: A Constellation of Clinical Features |
title_short | Albright′s Hereditary Osteodystrophy: A Constellation of Clinical Features |
title_sort | albright s hereditary osteodystrophy a constellation of clinical features |
topic | Albright′s hereditary osteodystrophy Pseudohypoparathyroidism Oral manifestation |
url | http://www.jiaomr.in/article.asp?issn=0972-1363;year=2010;volume=22;issue=4;spage=215;epage=217;aulast=Ambika;type=0 |
work_keys_str_mv | AT lambika albrightshereditaryosteodystrophyaconstellationofclinicalfeatures AT vaishalikeluskar albrightshereditaryosteodystrophyaconstellationofclinicalfeatures |