Hirayama Disease: An Important Cause of Focal Hand Weakness in Young Adults

Patients with progressive hand weakness may be seen in ambulatory medical clinics or in emergency rooms due to direct effects on activities of daily living or inadvertent injury associated with overuse or attempts to maintain normal function. It is important to recognize potential cause(s) and perfo...

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Main Authors: Nan Jiang MD, PhD, Eroboghene E. Ubogu MD
Format: Article
Language:English
Published: SAGE Publishing 2021-03-01
Series:Journal of Investigative Medicine High Impact Case Reports
Online Access:https://doi.org/10.1177/23247096211001646
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author Nan Jiang MD, PhD
Eroboghene E. Ubogu MD
author_facet Nan Jiang MD, PhD
Eroboghene E. Ubogu MD
author_sort Nan Jiang MD, PhD
collection DOAJ
description Patients with progressive hand weakness may be seen in ambulatory medical clinics or in emergency rooms due to direct effects on activities of daily living or inadvertent injury associated with overuse or attempts to maintain normal function. It is important to recognize potential cause(s) and perform appropriate diagnostic tests and referrals that aid guide appropriate treatment that may lead to good outcomes. Hirayama disease is an underrecognized disorder in young adults due to an asymmetric growth-associated cervical spinal cord compression injury. Awareness of this disorder by internists, emergency room physicians, and radiologists would prevent unnecessary tests and interventions that may contribute to disease progression by delaying appropriate treatments or treating inappropriately, with consequential effects on outcomes. In this article, we describe 3 Hirayama disease cases from a single tertiary care institution and demonstrate how delayed diagnosis affected outcomes in 2 patients and early recognition facilitated improved outcomes in a patient.
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spelling doaj.art-1cee11a757d04f369211e59c1694046d2022-12-21T20:01:03ZengSAGE PublishingJournal of Investigative Medicine High Impact Case Reports2324-70962021-03-01910.1177/23247096211001646Hirayama Disease: An Important Cause of Focal Hand Weakness in Young AdultsNan Jiang MD, PhD0Eroboghene E. Ubogu MD1University of Alabama at Birmingham, AL, USAUniversity of Alabama at Birmingham, AL, USAPatients with progressive hand weakness may be seen in ambulatory medical clinics or in emergency rooms due to direct effects on activities of daily living or inadvertent injury associated with overuse or attempts to maintain normal function. It is important to recognize potential cause(s) and perform appropriate diagnostic tests and referrals that aid guide appropriate treatment that may lead to good outcomes. Hirayama disease is an underrecognized disorder in young adults due to an asymmetric growth-associated cervical spinal cord compression injury. Awareness of this disorder by internists, emergency room physicians, and radiologists would prevent unnecessary tests and interventions that may contribute to disease progression by delaying appropriate treatments or treating inappropriately, with consequential effects on outcomes. In this article, we describe 3 Hirayama disease cases from a single tertiary care institution and demonstrate how delayed diagnosis affected outcomes in 2 patients and early recognition facilitated improved outcomes in a patient.https://doi.org/10.1177/23247096211001646
spellingShingle Nan Jiang MD, PhD
Eroboghene E. Ubogu MD
Hirayama Disease: An Important Cause of Focal Hand Weakness in Young Adults
Journal of Investigative Medicine High Impact Case Reports
title Hirayama Disease: An Important Cause of Focal Hand Weakness in Young Adults
title_full Hirayama Disease: An Important Cause of Focal Hand Weakness in Young Adults
title_fullStr Hirayama Disease: An Important Cause of Focal Hand Weakness in Young Adults
title_full_unstemmed Hirayama Disease: An Important Cause of Focal Hand Weakness in Young Adults
title_short Hirayama Disease: An Important Cause of Focal Hand Weakness in Young Adults
title_sort hirayama disease an important cause of focal hand weakness in young adults
url https://doi.org/10.1177/23247096211001646
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