Posterior fossa giant adenoid cystic carcinoma with skull base invasion mimicking glomus jugulare: A case report and review of literature
The author describes a rare case of giant adenoid cystic carcinoma (ACC) mimicking large paraganglioma with lower cranial nerve palsy. A 60-year-old female presented with a progressive increase in postauricular swelling with unilateral hearing loss, facial deviation, difficulty in swallowing, and ho...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
| Published: |
SAGE Publishing
2023-01-01
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| Series: | Rare Tumors |
| Online Access: | https://doi.org/10.1177/20363613221150218 |
| _version_ | 1797959872378044416 |
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| author | Anand Kumar Das MCh Neurosurgery Saraj Kumar Singh MCh Neurosurgery Kranti Bhavana MS Otolaryngology Subhash Kumar MD Radiodiagnosis |
| author_facet | Anand Kumar Das MCh Neurosurgery Saraj Kumar Singh MCh Neurosurgery Kranti Bhavana MS Otolaryngology Subhash Kumar MD Radiodiagnosis |
| author_sort | Anand Kumar Das MCh Neurosurgery |
| collection | DOAJ |
| description | The author describes a rare case of giant adenoid cystic carcinoma (ACC) mimicking large paraganglioma with lower cranial nerve palsy. A 60-year-old female presented with a progressive increase in postauricular swelling with unilateral hearing loss, facial deviation, difficulty in swallowing, and hoarseness of voice. MRI brain showed highly vascular infiltrating and osteolytic mass suggestive of large glomus jugulare versus sarcoma. It was completely engulfing the jugular foramen and lower cranial nerves with bony erosion of the jugular foramen and occipital condyle. The whole mastoid was filled with the tumor. On digital subtraction angiography the majority of blood supply was from the occipital branch of the external carotid artery and vertebral artery. The patient underwent percutaneous embolization followed by external carotid ligation and resection of the mass. The postoperative course was uneventful. Histopathology was suggestive of mixed ACCs. The patient received radiotherapy. After 1 year of follow up no recurrence or distant metastasis was noted. |
| first_indexed | 2024-04-11T00:37:46Z |
| format | Article |
| id | doaj.art-1d235a4a428a42feae9061819c10b3a0 |
| institution | Directory Open Access Journal |
| issn | 2036-3613 |
| language | English |
| last_indexed | 2024-04-11T00:37:46Z |
| publishDate | 2023-01-01 |
| publisher | SAGE Publishing |
| record_format | Article |
| series | Rare Tumors |
| spelling | doaj.art-1d235a4a428a42feae9061819c10b3a02023-01-06T14:03:24ZengSAGE PublishingRare Tumors2036-36132023-01-011510.1177/20363613221150218Posterior fossa giant adenoid cystic carcinoma with skull base invasion mimicking glomus jugulare: A case report and review of literatureAnand Kumar Das MCh NeurosurgerySaraj Kumar Singh MCh NeurosurgeryKranti Bhavana MS OtolaryngologySubhash Kumar MD RadiodiagnosisThe author describes a rare case of giant adenoid cystic carcinoma (ACC) mimicking large paraganglioma with lower cranial nerve palsy. A 60-year-old female presented with a progressive increase in postauricular swelling with unilateral hearing loss, facial deviation, difficulty in swallowing, and hoarseness of voice. MRI brain showed highly vascular infiltrating and osteolytic mass suggestive of large glomus jugulare versus sarcoma. It was completely engulfing the jugular foramen and lower cranial nerves with bony erosion of the jugular foramen and occipital condyle. The whole mastoid was filled with the tumor. On digital subtraction angiography the majority of blood supply was from the occipital branch of the external carotid artery and vertebral artery. The patient underwent percutaneous embolization followed by external carotid ligation and resection of the mass. The postoperative course was uneventful. Histopathology was suggestive of mixed ACCs. The patient received radiotherapy. After 1 year of follow up no recurrence or distant metastasis was noted.https://doi.org/10.1177/20363613221150218 |
| spellingShingle | Anand Kumar Das MCh Neurosurgery Saraj Kumar Singh MCh Neurosurgery Kranti Bhavana MS Otolaryngology Subhash Kumar MD Radiodiagnosis Posterior fossa giant adenoid cystic carcinoma with skull base invasion mimicking glomus jugulare: A case report and review of literature Rare Tumors |
| title | Posterior fossa giant adenoid cystic carcinoma with skull base invasion mimicking glomus jugulare: A case report and review of literature |
| title_full | Posterior fossa giant adenoid cystic carcinoma with skull base invasion mimicking glomus jugulare: A case report and review of literature |
| title_fullStr | Posterior fossa giant adenoid cystic carcinoma with skull base invasion mimicking glomus jugulare: A case report and review of literature |
| title_full_unstemmed | Posterior fossa giant adenoid cystic carcinoma with skull base invasion mimicking glomus jugulare: A case report and review of literature |
| title_short | Posterior fossa giant adenoid cystic carcinoma with skull base invasion mimicking glomus jugulare: A case report and review of literature |
| title_sort | posterior fossa giant adenoid cystic carcinoma with skull base invasion mimicking glomus jugulare a case report and review of literature |
| url | https://doi.org/10.1177/20363613221150218 |
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