Paroxysmal nocturnal hemoglobinuria: A rare case of recurrent episodes of icterus
In this work we describe a rare case of a patient with paroxysmal nocturnal hemoglobinuria (PNH) developed on the background of specific medical history of morbus Gilbert with chronically elevated bilirubin and recurrent attacks of macroscopic haematuria. We focus on a differential diagnosis of the...
Main Authors: | , , , , , , |
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Format: | Article |
Language: | English |
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Sciendo
2022-12-01
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Series: | Acta Medica Martiniana |
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Online Access: | https://doi.org/10.2478/acm-2022-0014 |
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author | Jakub Hoferica Lenka Nosakova Peter Uhrik Diana Vazanova Matus Scur Juraj Chudej Peter Banovcin |
author_facet | Jakub Hoferica Lenka Nosakova Peter Uhrik Diana Vazanova Matus Scur Juraj Chudej Peter Banovcin |
author_sort | Jakub Hoferica |
collection | DOAJ |
description | In this work we describe a rare case of a patient with paroxysmal nocturnal hemoglobinuria (PNH) developed on the background of specific medical history of morbus Gilbert with chronically elevated bilirubin and recurrent attacks of macroscopic haematuria. We focus on a differential diagnosis of the disease, its obstacles, and treatment options. |
first_indexed | 2024-04-10T21:29:11Z |
format | Article |
id | doaj.art-1d597316b5a14d0582b018697c40845e |
institution | Directory Open Access Journal |
issn | 1338-4139 |
language | English |
last_indexed | 2024-04-10T21:29:11Z |
publishDate | 2022-12-01 |
publisher | Sciendo |
record_format | Article |
series | Acta Medica Martiniana |
spelling | doaj.art-1d597316b5a14d0582b018697c40845e2023-01-19T13:53:17ZengSciendoActa Medica Martiniana1338-41392022-12-0122312212810.2478/acm-2022-0014Paroxysmal nocturnal hemoglobinuria: A rare case of recurrent episodes of icterusJakub Hoferica0Lenka Nosakova1Peter Uhrik2Diana Vazanova3Matus Scur4Juraj Chudej5Peter Banovcin6Clinic of Gastroenterological Internal Medicine, University Hospital in Martin and Jessenius Faculty of Medicine in Martin, Comenius University in Bratislava, Martin, SlovakiaClinic of Gastroenterological Internal Medicine, University Hospital in Martin and Jessenius Faculty of Medicine in Martin, Comenius University in Bratislava, Martin, SlovakiaClinic of Gastroenterological Internal Medicine, University Hospital in Martin and Jessenius Faculty of Medicine in Martin, Comenius University in Bratislava, Martin, SlovakiaClinic of Gastroenterological Internal Medicine, University Hospital in Martin and Jessenius Faculty of Medicine in Martin, Comenius University in Bratislava, Martin, SlovakiaClinic of Gastroenterological Internal Medicine, University Hospital in Martin and Jessenius Faculty of Medicine in Martin, Comenius University in Bratislava, Martin, SlovakiaDepartment of Hematology and Transfusiology of University Hospital in Martin and Jessenius Faculty of Medicine in Martin, Comenius University in Bratislava, Martin, SlovakiaClinic of Gastroenterological Internal Medicine, University Hospital in Martin and Jessenius Faculty of Medicine in Martin, Comenius University in Bratislava, Martin, SlovakiaIn this work we describe a rare case of a patient with paroxysmal nocturnal hemoglobinuria (PNH) developed on the background of specific medical history of morbus Gilbert with chronically elevated bilirubin and recurrent attacks of macroscopic haematuria. We focus on a differential diagnosis of the disease, its obstacles, and treatment options.https://doi.org/10.2478/acm-2022-0014paroxysmal nocturnal hemoglobinuriahaemolytic anaemiaicterus |
spellingShingle | Jakub Hoferica Lenka Nosakova Peter Uhrik Diana Vazanova Matus Scur Juraj Chudej Peter Banovcin Paroxysmal nocturnal hemoglobinuria: A rare case of recurrent episodes of icterus Acta Medica Martiniana paroxysmal nocturnal hemoglobinuria haemolytic anaemia icterus |
title | Paroxysmal nocturnal hemoglobinuria: A rare case of recurrent episodes of icterus |
title_full | Paroxysmal nocturnal hemoglobinuria: A rare case of recurrent episodes of icterus |
title_fullStr | Paroxysmal nocturnal hemoglobinuria: A rare case of recurrent episodes of icterus |
title_full_unstemmed | Paroxysmal nocturnal hemoglobinuria: A rare case of recurrent episodes of icterus |
title_short | Paroxysmal nocturnal hemoglobinuria: A rare case of recurrent episodes of icterus |
title_sort | paroxysmal nocturnal hemoglobinuria a rare case of recurrent episodes of icterus |
topic | paroxysmal nocturnal hemoglobinuria haemolytic anaemia icterus |
url | https://doi.org/10.2478/acm-2022-0014 |
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