A Methionine-Portioning-Based Medical Nutrition Therapy with Relaxed Fruit and Vegetable Consumption in Patients with Pyridoxine-Nonresponsive Cystathionine-β-Synthase Deficiency

A Methionine-Portioning-Based Medical Nutrition Therapy with Relaxed Fruit and Vegetable Consumption in Patients with Pyridoxine-Nonresponsive Cystathionine-β-Synthase Deficiency

The main treatment for pyridoxine-nonresponsive cystathionine-β-synthase deficiency is a strict diet. Most centers prescribe low-protein diets based on gram–protein exchanges, and all protein sources are weighed. The purpose of this study is to investigate the effects of a more liberal methionine (M...

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Bibliographic Details
Main Authors: Esma Uygur, Cigdem Aktuglu-Zeybek, Mirsaid Aghalarov, Mehmet Serif Cansever, Ertugrul Kıykım, Tanyel Zubarioglu
Format: Article
Language:English
Published: MDPI AG 2023-07-01
Series:Nutrients
Subjects:
CBS deficiency
homocystinuria
homocysteine
simplified diet
methionine portioning
fruits
Online Access:https://www.mdpi.com/2072-6643/15/14/3105

Internet

https://www.mdpi.com/2072-6643/15/14/3105

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