Moyamoya disease in a 3-year-old boy presenting with a focal motor seizure provoked by hyperventilation

A previously healthy, 3-year-old boy presented to the emergency department with an afebrile focal motor seizure. He was found crying and having a seizure 30 minutes earlier. During this seizure, he was jerking his head and right extremities. Subsequent magnetic resonance imaging showed acute infarct...

Full description

Bibliographic Details
Main Authors: Soojin Hwang, Jung Heon Kim, Hee Mang Yoon, Mi-Sun Yum
Format: Article
Language:English
Published: Korean Society of Pediatric Emergency Medicine 2018-06-01
Series:Pediatric Emergency Medicine Journal
Subjects:
Online Access:http://pemj.org/upload/pdf/pemj-2018-00199.pdf
Description
Summary:A previously healthy, 3-year-old boy presented to the emergency department with an afebrile focal motor seizure. He was found crying and having a seizure 30 minutes earlier. During this seizure, he was jerking his head and right extremities. Subsequent magnetic resonance imaging showed acute infarction in the bilateral frontal lobes, chiefly in the left. After hospitalization, conventional angiography demonstrated bilateral stenosis of the distal internal carotid arteries with development of lenticulostriate collaterals, which confirmed the diagnosis of moyamoya disease. It is vital to recognize focal motor seizures and situations related to hyperventilation in children with a seizure, which imply a structural lesion and a provoked cerebral ischemia in preexisting moyamoya disease, respectively.
ISSN:2383-4897
2508-5506