Vaginoplasty with Amnion Graft: Management of Mayer-Rokitansky-Kuster-Hauser Syndrome
Mayer-Rokitansky-Kuster-Hauser syndrome also known as mullerian agenesis is a rare congenital condition in which there is absence of uterus along with upper vagina. Patient usually presents with primary amenorrhea with or without cyclical lower abdominal pain but have normal secondary sexual charac...
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| Format: | Article |
| Language: | English |
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Nepal Health Research Council
2024-03-01
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| Series: | Journal of Nepal Health Research Council |
| Online Access: | http://103.69.126.137/index.php/jnhrc/article/view/4573 |
| _version_ | 1797248191577456640 |
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| author | Srijana Bhandari Ganesh Dangal Aruna Karki Hema Pradhan Ranjana Shrestha Kabin Bhattachan Kenusha Devi Tiwari Sonu Bharati Sunita Maharjan |
| author_facet | Srijana Bhandari Ganesh Dangal Aruna Karki Hema Pradhan Ranjana Shrestha Kabin Bhattachan Kenusha Devi Tiwari Sonu Bharati Sunita Maharjan |
| author_sort | Srijana Bhandari |
| collection | DOAJ |
| description |
Mayer-Rokitansky-Kuster-Hauser syndrome also known as mullerian agenesis is a rare congenital condition in which there is absence of uterus along with upper vagina. Patient usually presents with primary amenorrhea with or without cyclical lower abdominal pain but have normal secondary sexual characters. Modified McIndoe Vaginoplasty with amnion graft is the commonest surgery performed worldwide. A 23 year old girl with normal secondary sexual characters presented with primary amenorrhea with cyclical lower abdominal pain; on examination blind vagina was present. Vaginoplasty with amnion graft was done and vaginal mould was placed. Vaginal dilatation with Hegar’s dilator was done weekly until 6 weeks. She is under regular follow-up at present and advised for regular manual dilation at home. McIndoe Vaginoplasty with amnion graft is a simple yet rewarding procedure especially in low resource countries like ours, with good success rate and with minimal postoperative complications.
Keywords: Amnion graft; Mayer-Rokitansky-Kuster-Hauser Syndrome; Modified McIndoe Vaginoplasty; Primary amenorrhea; Secondary sexual characters.
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| first_indexed | 2024-04-24T20:10:40Z |
| format | Article |
| id | doaj.art-1f0203743d9d4c4290a2478cd4bfe126 |
| institution | Directory Open Access Journal |
| issn | 1727-5482 1999-6217 |
| language | English |
| last_indexed | 2024-04-24T20:10:40Z |
| publishDate | 2024-03-01 |
| publisher | Nepal Health Research Council |
| record_format | Article |
| series | Journal of Nepal Health Research Council |
| spelling | doaj.art-1f0203743d9d4c4290a2478cd4bfe1262024-03-23T09:08:46ZengNepal Health Research CouncilJournal of Nepal Health Research Council1727-54821999-62172024-03-0121310.33314/jnhrc.v21i3.4573Vaginoplasty with Amnion Graft: Management of Mayer-Rokitansky-Kuster-Hauser SyndromeSrijana Bhandari0Ganesh Dangal1Aruna Karki2Hema Pradhan3Ranjana Shrestha4Kabin Bhattachan5Kenusha Devi Tiwari6Sonu Bharati7Sunita Maharjan8Department of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, NepalDepartment of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, NepalDepartment of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, NepalDepartment of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, NepalDepartment of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, NepalDepartment of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, NepalDepartment of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, NepalDepartment of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, NepalDepartment of Obstetrics and Gynaecology, Kathmandu Model Hospital, Exhibition Road, Kathmandu, Nepal Mayer-Rokitansky-Kuster-Hauser syndrome also known as mullerian agenesis is a rare congenital condition in which there is absence of uterus along with upper vagina. Patient usually presents with primary amenorrhea with or without cyclical lower abdominal pain but have normal secondary sexual characters. Modified McIndoe Vaginoplasty with amnion graft is the commonest surgery performed worldwide. A 23 year old girl with normal secondary sexual characters presented with primary amenorrhea with cyclical lower abdominal pain; on examination blind vagina was present. Vaginoplasty with amnion graft was done and vaginal mould was placed. Vaginal dilatation with Hegar’s dilator was done weekly until 6 weeks. She is under regular follow-up at present and advised for regular manual dilation at home. McIndoe Vaginoplasty with amnion graft is a simple yet rewarding procedure especially in low resource countries like ours, with good success rate and with minimal postoperative complications. Keywords: Amnion graft; Mayer-Rokitansky-Kuster-Hauser Syndrome; Modified McIndoe Vaginoplasty; Primary amenorrhea; Secondary sexual characters. http://103.69.126.137/index.php/jnhrc/article/view/4573 |
| spellingShingle | Srijana Bhandari Ganesh Dangal Aruna Karki Hema Pradhan Ranjana Shrestha Kabin Bhattachan Kenusha Devi Tiwari Sonu Bharati Sunita Maharjan Vaginoplasty with Amnion Graft: Management of Mayer-Rokitansky-Kuster-Hauser Syndrome Journal of Nepal Health Research Council |
| title | Vaginoplasty with Amnion Graft: Management of Mayer-Rokitansky-Kuster-Hauser Syndrome |
| title_full | Vaginoplasty with Amnion Graft: Management of Mayer-Rokitansky-Kuster-Hauser Syndrome |
| title_fullStr | Vaginoplasty with Amnion Graft: Management of Mayer-Rokitansky-Kuster-Hauser Syndrome |
| title_full_unstemmed | Vaginoplasty with Amnion Graft: Management of Mayer-Rokitansky-Kuster-Hauser Syndrome |
| title_short | Vaginoplasty with Amnion Graft: Management of Mayer-Rokitansky-Kuster-Hauser Syndrome |
| title_sort | vaginoplasty with amnion graft management of mayer rokitansky kuster hauser syndrome |
| url | http://103.69.126.137/index.php/jnhrc/article/view/4573 |
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