Malignant fibrous histiocytoma of the scalp: A rare differential with a dramatic clinical presentation
Malignant fibrous histiocytoma (MFH) a pleomorphic sarcoma of uncertain origin was first described by O′Brien and Stout in 1964. It is the most common primary soft tissue sarcoma of late adult life; its occurrence is rare in the pediatric population. MFHs are commonly known to arise in the extremiti...
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Format: | Article |
Language: | English |
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Wolters Kluwer Medknow Publications
2014-01-01
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Series: | Journal of Indian Association of Pediatric Surgeons |
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Online Access: | http://www.jiaps.com/article.asp?issn=0971-9261;year=2014;volume=19;issue=4;spage=227;epage=229;aulast=Krishnamurthy |
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author | Arvind Krishnamurthy |
author_facet | Arvind Krishnamurthy |
author_sort | Arvind Krishnamurthy |
collection | DOAJ |
description | Malignant fibrous histiocytoma (MFH) a pleomorphic sarcoma of uncertain origin was first described by O′Brien and Stout in 1964. It is the most common primary soft tissue sarcoma of late adult life; its occurrence is rare in the pediatric population. MFHs are commonly known to arise in the extremities and the trunk although it can occur almost anywhere in the body. MFH of the scalp is extremely rare; moreover, there is paucity of literature with regards to prevalence of scalp and skull neoplasms. We present an unusual case of a primary MFH involving the scalp of a 5-year-old child and discuss its unusual clinical presentation, histology with immunohistochemistry correlation and its management. Reviewing the literature of primary MFH of the scalp, our patient to the best of our knowledge, is probably the youngest case reported so far. |
first_indexed | 2024-04-12T11:41:35Z |
format | Article |
id | doaj.art-1f09f1c6f5fb40d38f71fde895593ac0 |
institution | Directory Open Access Journal |
issn | 0971-9261 1998-3891 |
language | English |
last_indexed | 2024-04-12T11:41:35Z |
publishDate | 2014-01-01 |
publisher | Wolters Kluwer Medknow Publications |
record_format | Article |
series | Journal of Indian Association of Pediatric Surgeons |
spelling | doaj.art-1f09f1c6f5fb40d38f71fde895593ac02022-12-22T03:34:37ZengWolters Kluwer Medknow PublicationsJournal of Indian Association of Pediatric Surgeons0971-92611998-38912014-01-0119422722910.4103/0971-9261.142015Malignant fibrous histiocytoma of the scalp: A rare differential with a dramatic clinical presentationArvind KrishnamurthyMalignant fibrous histiocytoma (MFH) a pleomorphic sarcoma of uncertain origin was first described by O′Brien and Stout in 1964. It is the most common primary soft tissue sarcoma of late adult life; its occurrence is rare in the pediatric population. MFHs are commonly known to arise in the extremities and the trunk although it can occur almost anywhere in the body. MFH of the scalp is extremely rare; moreover, there is paucity of literature with regards to prevalence of scalp and skull neoplasms. We present an unusual case of a primary MFH involving the scalp of a 5-year-old child and discuss its unusual clinical presentation, histology with immunohistochemistry correlation and its management. Reviewing the literature of primary MFH of the scalp, our patient to the best of our knowledge, is probably the youngest case reported so far.http://www.jiaps.com/article.asp?issn=0971-9261;year=2014;volume=19;issue=4;spage=227;epage=229;aulast=KrishnamurthyChildrenmalignant fibrous histiocytomascalp tumors |
spellingShingle | Arvind Krishnamurthy Malignant fibrous histiocytoma of the scalp: A rare differential with a dramatic clinical presentation Journal of Indian Association of Pediatric Surgeons Children malignant fibrous histiocytoma scalp tumors |
title | Malignant fibrous histiocytoma of the scalp: A rare differential with a dramatic clinical presentation |
title_full | Malignant fibrous histiocytoma of the scalp: A rare differential with a dramatic clinical presentation |
title_fullStr | Malignant fibrous histiocytoma of the scalp: A rare differential with a dramatic clinical presentation |
title_full_unstemmed | Malignant fibrous histiocytoma of the scalp: A rare differential with a dramatic clinical presentation |
title_short | Malignant fibrous histiocytoma of the scalp: A rare differential with a dramatic clinical presentation |
title_sort | malignant fibrous histiocytoma of the scalp a rare differential with a dramatic clinical presentation |
topic | Children malignant fibrous histiocytoma scalp tumors |
url | http://www.jiaps.com/article.asp?issn=0971-9261;year=2014;volume=19;issue=4;spage=227;epage=229;aulast=Krishnamurthy |
work_keys_str_mv | AT arvindkrishnamurthy malignantfibroushistiocytomaofthescalpararedifferentialwithadramaticclinicalpresentation |