Surgical management of recurrent desmoid tumor in a young male

Desmoid tumors are rare, aggressive fibroblastic soft tissue tumors. We report a case of a 20-year-old male with recurrence of desmoid tumor of the left shoulder after initial complete resection 3 years prior. Pathology revealed fibromatosis desmoid type. After complete resection of tumor at 17-year...

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Main Authors: Omar A. Santiago Báez, Atenas A. Martínez Bernal, Pedro E. Ruiz Medina, Jaime A. Aponte Ortiz, Victor N. Ortiz Justiniano
Format: Article
Language:English
Published: Elsevier 2022-07-01
Series:Journal of Pediatric Surgery Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2213576622001294
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author Omar A. Santiago Báez
Atenas A. Martínez Bernal
Pedro E. Ruiz Medina
Jaime A. Aponte Ortiz
Victor N. Ortiz Justiniano
author_facet Omar A. Santiago Báez
Atenas A. Martínez Bernal
Pedro E. Ruiz Medina
Jaime A. Aponte Ortiz
Victor N. Ortiz Justiniano
author_sort Omar A. Santiago Báez
collection DOAJ
description Desmoid tumors are rare, aggressive fibroblastic soft tissue tumors. We report a case of a 20-year-old male with recurrence of desmoid tumor of the left shoulder after initial complete resection 3 years prior. Pathology revealed fibromatosis desmoid type. After complete resection of tumor at 17-year-old, no symptoms were reported after 3 years of first resection, when he developed numbness and weakness of the left upper extremity. Magnetic resonance imaging demonstrated an enlarging arteriovenous malformation at the left shoulder with possible recurrence. Excision was performed, and after tissue examination evidence of recurrent fibromatosis desmoid type was found without arteriovenous malformation. Recurrence after complete resection could be as high as 70%. Early recurrence recognition is essential as tumor growth before the infiltration of the aggressive tumor makes the resection more difficult and increases surgical risk of complications.
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spelling doaj.art-203151088e9c414fbc26975f232ac9e02022-12-22T00:23:18ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662022-07-0182102302Surgical management of recurrent desmoid tumor in a young maleOmar A. Santiago Báez0Atenas A. Martínez Bernal1Pedro E. Ruiz Medina2Jaime A. Aponte Ortiz3Victor N. Ortiz Justiniano4Department of Pediatrics at Puerto Rico Women and Children's Hospital, Bayamón, Puerto Rico; Corresponding author.Department of Pediatric Surgery at Puerto Rico Women and Children's Hospital, Bayamón, Puerto RicoDepartment of General Surgery at University of Puerto Rico Medical Sciences Campus, San Juan, Puerto RicoDepartment of General Surgery at University of Puerto Rico Medical Sciences Campus, San Juan, Puerto RicoDepartment of Pediatric Surgery at Puerto Rico Women and Children's Hospital, Bayamón, Puerto Rico; Department of General Surgery at University of Puerto Rico Medical Sciences Campus, San Juan, Puerto RicoDesmoid tumors are rare, aggressive fibroblastic soft tissue tumors. We report a case of a 20-year-old male with recurrence of desmoid tumor of the left shoulder after initial complete resection 3 years prior. Pathology revealed fibromatosis desmoid type. After complete resection of tumor at 17-year-old, no symptoms were reported after 3 years of first resection, when he developed numbness and weakness of the left upper extremity. Magnetic resonance imaging demonstrated an enlarging arteriovenous malformation at the left shoulder with possible recurrence. Excision was performed, and after tissue examination evidence of recurrent fibromatosis desmoid type was found without arteriovenous malformation. Recurrence after complete resection could be as high as 70%. Early recurrence recognition is essential as tumor growth before the infiltration of the aggressive tumor makes the resection more difficult and increases surgical risk of complications.http://www.sciencedirect.com/science/article/pii/S2213576622001294Desmoid tumorDesmoid fibromatosisDesmoid recurrenceRadical dissection
spellingShingle Omar A. Santiago Báez
Atenas A. Martínez Bernal
Pedro E. Ruiz Medina
Jaime A. Aponte Ortiz
Victor N. Ortiz Justiniano
Surgical management of recurrent desmoid tumor in a young male
Journal of Pediatric Surgery Case Reports
Desmoid tumor
Desmoid fibromatosis
Desmoid recurrence
Radical dissection
title Surgical management of recurrent desmoid tumor in a young male
title_full Surgical management of recurrent desmoid tumor in a young male
title_fullStr Surgical management of recurrent desmoid tumor in a young male
title_full_unstemmed Surgical management of recurrent desmoid tumor in a young male
title_short Surgical management of recurrent desmoid tumor in a young male
title_sort surgical management of recurrent desmoid tumor in a young male
topic Desmoid tumor
Desmoid fibromatosis
Desmoid recurrence
Radical dissection
url http://www.sciencedirect.com/science/article/pii/S2213576622001294
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