Crossed fused renal ectopia: Challenges in diagnosis and management
Aim: Crossed fused renal ectopia is a rare congenital malformation, which is reported to be usually asymptomatic but may have varied presentations. This survey was conducted to study the clinical profile and the challenges posed in the management of this entity. Materials and Methods: Retrospective...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2013-01-01
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| Series: | Journal of Indian Association of Pediatric Surgeons |
| Subjects: | |
| Online Access: | http://www.jiaps.com/article.asp?issn=0971-9261;year=2013;volume=18;issue=1;spage=7;epage=10;aulast=Solanki |
| _version_ | 1819052955859419136 |
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| author | Shailesh Solanki Veereshwar Bhatnagar Arun K Gupta Rakesh Kumar |
| author_facet | Shailesh Solanki Veereshwar Bhatnagar Arun K Gupta Rakesh Kumar |
| author_sort | Shailesh Solanki |
| collection | DOAJ |
| description | Aim: Crossed fused renal ectopia is a rare congenital malformation, which is reported to be usually asymptomatic but may have varied presentations. This survey was conducted to study the clinical profile and the challenges posed in the management of this entity. Materials and Methods: Retrospective analysis of 6 patients diagnosed to have crossed fused renal ectopia during 1997-2010. The diagnosis was confirmed during surgical exploration in one patient. In one patient it was detected on antenatal ultrasonography and in the other 4 patients it was detected during investigations for abdominal pain, abdominal mass, anorectal malformation and urinary tract infection. Results: The left moiety was crossed and fused with the right moiety in 4 cases. Ultrasonography was found to be a good screening investigation with useful diagnostic contributions from CT scans, radionuclide scintigraphy and magnetic resonance urography. Micturating cystourethrography revealed presence of VUR in 4 cases, 3 of whom have undergone ureteric reimplantation. Two patients required pyeloplasty for pelviureteric junction obstruction; in one of these patients the upper ureter was entrapped in the isthmus. In one patient, a non-functioning moiety resulted in nephrectomy. All children were asymptomatic at last follow-up with stable renal functions. Conclusions: Crossed fused renal ectopia was detected in most patients during investigation for other problems. It was found more commonly in boys. The left moiety was crossed to the right in the majority of cases. Associated urological problems were found in most cases and required the appropriate surgical management. |
| first_indexed | 2024-12-21T12:28:04Z |
| format | Article |
| id | doaj.art-209055b16ed44de79ff2b3636d834bc1 |
| institution | Directory Open Access Journal |
| issn | 0971-9261 1998-3891 |
| language | English |
| last_indexed | 2024-12-21T12:28:04Z |
| publishDate | 2013-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Journal of Indian Association of Pediatric Surgeons |
| spelling | doaj.art-209055b16ed44de79ff2b3636d834bc12022-12-21T19:04:06ZengWolters Kluwer Medknow PublicationsJournal of Indian Association of Pediatric Surgeons0971-92611998-38912013-01-0118171010.4103/0971-9261.107006Crossed fused renal ectopia: Challenges in diagnosis and managementShailesh SolankiVeereshwar BhatnagarArun K GuptaRakesh KumarAim: Crossed fused renal ectopia is a rare congenital malformation, which is reported to be usually asymptomatic but may have varied presentations. This survey was conducted to study the clinical profile and the challenges posed in the management of this entity. Materials and Methods: Retrospective analysis of 6 patients diagnosed to have crossed fused renal ectopia during 1997-2010. The diagnosis was confirmed during surgical exploration in one patient. In one patient it was detected on antenatal ultrasonography and in the other 4 patients it was detected during investigations for abdominal pain, abdominal mass, anorectal malformation and urinary tract infection. Results: The left moiety was crossed and fused with the right moiety in 4 cases. Ultrasonography was found to be a good screening investigation with useful diagnostic contributions from CT scans, radionuclide scintigraphy and magnetic resonance urography. Micturating cystourethrography revealed presence of VUR in 4 cases, 3 of whom have undergone ureteric reimplantation. Two patients required pyeloplasty for pelviureteric junction obstruction; in one of these patients the upper ureter was entrapped in the isthmus. In one patient, a non-functioning moiety resulted in nephrectomy. All children were asymptomatic at last follow-up with stable renal functions. Conclusions: Crossed fused renal ectopia was detected in most patients during investigation for other problems. It was found more commonly in boys. The left moiety was crossed to the right in the majority of cases. Associated urological problems were found in most cases and required the appropriate surgical management.http://www.jiaps.com/article.asp?issn=0971-9261;year=2013;volume=18;issue=1;spage=7;epage=10;aulast=SolankiCongenital anomalies of kidneycrossed fused renal ectopiafusion anomalies of kidney |
| spellingShingle | Shailesh Solanki Veereshwar Bhatnagar Arun K Gupta Rakesh Kumar Crossed fused renal ectopia: Challenges in diagnosis and management Journal of Indian Association of Pediatric Surgeons Congenital anomalies of kidney crossed fused renal ectopia fusion anomalies of kidney |
| title | Crossed fused renal ectopia: Challenges in diagnosis and management |
| title_full | Crossed fused renal ectopia: Challenges in diagnosis and management |
| title_fullStr | Crossed fused renal ectopia: Challenges in diagnosis and management |
| title_full_unstemmed | Crossed fused renal ectopia: Challenges in diagnosis and management |
| title_short | Crossed fused renal ectopia: Challenges in diagnosis and management |
| title_sort | crossed fused renal ectopia challenges in diagnosis and management |
| topic | Congenital anomalies of kidney crossed fused renal ectopia fusion anomalies of kidney |
| url | http://www.jiaps.com/article.asp?issn=0971-9261;year=2013;volume=18;issue=1;spage=7;epage=10;aulast=Solanki |
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