A rare case of a peripheral Ewing sarcoma primitive neuroectodermal tumor of pelvic origin
Primitive neuroectodermal tumors (PNET) represent malignant neuroectodermal tumors composed of small round cells. They can be differentiated between originating from the peripheral nervous system or the central nervous system. Peripheral PNET (pPNET) can be further subclassified as one of the Ewing...
| Main Authors: | , , , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Elsevier
2023-04-01
|
| Series: | Radiology Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S1930043323000067 |
| _version_ | 1797894920019640320 |
|---|---|
| author | Erinie Mekheal, MD Brooke Kania, DO Unnati Vishwakarma, MD Derrick Joseph, MD Vinod Kumar, MD Michael Maroules, MD |
| author_facet | Erinie Mekheal, MD Brooke Kania, DO Unnati Vishwakarma, MD Derrick Joseph, MD Vinod Kumar, MD Michael Maroules, MD |
| author_sort | Erinie Mekheal, MD |
| collection | DOAJ |
| description | Primitive neuroectodermal tumors (PNET) represent malignant neuroectodermal tumors composed of small round cells. They can be differentiated between originating from the peripheral nervous system or the central nervous system. Peripheral PNET (pPNET) can be further subclassified as one of the Ewing family tumors (EFT). Although rare, EFT can originate in the female genital tract and pelvic region. Here, we present a case of a middle-aged female with PNET masses in her uterus, abdomen, and hepatic lobes. We discuss the diagnostic modalities, including immunohistochemistry, histopathology, and imaging findings associated with this rare malignancy. |
| first_indexed | 2024-04-10T07:17:01Z |
| format | Article |
| id | doaj.art-2110e0e812bf4cf4a0e2e4f1b89c08b4 |
| institution | Directory Open Access Journal |
| issn | 1930-0433 |
| language | English |
| last_indexed | 2024-04-10T07:17:01Z |
| publishDate | 2023-04-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj.art-2110e0e812bf4cf4a0e2e4f1b89c08b42023-02-25T04:09:38ZengElsevierRadiology Case Reports1930-04332023-04-0118414371441A rare case of a peripheral Ewing sarcoma primitive neuroectodermal tumor of pelvic originErinie Mekheal, MD0Brooke Kania, DO1Unnati Vishwakarma, MD2Derrick Joseph, MD3Vinod Kumar, MD4Michael Maroules, MD5Department(s) of Hematology/Oncology and Internal Medicine, St. Joseph's University Medical Center, 703 Main St., Paterson, NJ USA 07503Corresponding author.; Department(s) of Hematology/Oncology and Internal Medicine, St. Joseph's University Medical Center, 703 Main St., Paterson, NJ USA 07503Department(s) of Hematology/Oncology and Internal Medicine, St. Joseph's University Medical Center, 703 Main St., Paterson, NJ USA 07503Department(s) of Hematology/Oncology and Internal Medicine, St. Joseph's University Medical Center, 703 Main St., Paterson, NJ USA 07503Department(s) of Hematology/Oncology and Internal Medicine, St. Joseph's University Medical Center, 703 Main St., Paterson, NJ USA 07503Department(s) of Hematology/Oncology and Internal Medicine, St. Joseph's University Medical Center, 703 Main St., Paterson, NJ USA 07503Primitive neuroectodermal tumors (PNET) represent malignant neuroectodermal tumors composed of small round cells. They can be differentiated between originating from the peripheral nervous system or the central nervous system. Peripheral PNET (pPNET) can be further subclassified as one of the Ewing family tumors (EFT). Although rare, EFT can originate in the female genital tract and pelvic region. Here, we present a case of a middle-aged female with PNET masses in her uterus, abdomen, and hepatic lobes. We discuss the diagnostic modalities, including immunohistochemistry, histopathology, and imaging findings associated with this rare malignancy.http://www.sciencedirect.com/science/article/pii/S1930043323000067Primitive neuroectodermal tumorsEwing sarcomaOvaryOvarian malignancy |
| spellingShingle | Erinie Mekheal, MD Brooke Kania, DO Unnati Vishwakarma, MD Derrick Joseph, MD Vinod Kumar, MD Michael Maroules, MD A rare case of a peripheral Ewing sarcoma primitive neuroectodermal tumor of pelvic origin Radiology Case Reports Primitive neuroectodermal tumors Ewing sarcoma Ovary Ovarian malignancy |
| title | A rare case of a peripheral Ewing sarcoma primitive neuroectodermal tumor of pelvic origin |
| title_full | A rare case of a peripheral Ewing sarcoma primitive neuroectodermal tumor of pelvic origin |
| title_fullStr | A rare case of a peripheral Ewing sarcoma primitive neuroectodermal tumor of pelvic origin |
| title_full_unstemmed | A rare case of a peripheral Ewing sarcoma primitive neuroectodermal tumor of pelvic origin |
| title_short | A rare case of a peripheral Ewing sarcoma primitive neuroectodermal tumor of pelvic origin |
| title_sort | rare case of a peripheral ewing sarcoma primitive neuroectodermal tumor of pelvic origin |
| topic | Primitive neuroectodermal tumors Ewing sarcoma Ovary Ovarian malignancy |
| url | http://www.sciencedirect.com/science/article/pii/S1930043323000067 |
| work_keys_str_mv | AT eriniemekhealmd ararecaseofaperipheralewingsarcomaprimitiveneuroectodermaltumorofpelvicorigin AT brookekaniado ararecaseofaperipheralewingsarcomaprimitiveneuroectodermaltumorofpelvicorigin AT unnativishwakarmamd ararecaseofaperipheralewingsarcomaprimitiveneuroectodermaltumorofpelvicorigin AT derrickjosephmd ararecaseofaperipheralewingsarcomaprimitiveneuroectodermaltumorofpelvicorigin AT vinodkumarmd ararecaseofaperipheralewingsarcomaprimitiveneuroectodermaltumorofpelvicorigin AT michaelmaroulesmd ararecaseofaperipheralewingsarcomaprimitiveneuroectodermaltumorofpelvicorigin AT eriniemekhealmd rarecaseofaperipheralewingsarcomaprimitiveneuroectodermaltumorofpelvicorigin AT brookekaniado rarecaseofaperipheralewingsarcomaprimitiveneuroectodermaltumorofpelvicorigin AT unnativishwakarmamd rarecaseofaperipheralewingsarcomaprimitiveneuroectodermaltumorofpelvicorigin AT derrickjosephmd rarecaseofaperipheralewingsarcomaprimitiveneuroectodermaltumorofpelvicorigin AT vinodkumarmd rarecaseofaperipheralewingsarcomaprimitiveneuroectodermaltumorofpelvicorigin AT michaelmaroulesmd rarecaseofaperipheralewingsarcomaprimitiveneuroectodermaltumorofpelvicorigin |