Optimising the management of pulmonary arterial hypertension patients: emergency treatments
Pulmonary arterial hypertension (PAH) is a rare and potentially fatal disease whose management is usually restricted to a few specialised centres. As patients do not necessarily live in the neighbourhood of these centres, daily care and emergencies have to be delegated to first and second lines. Tre...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
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European Respiratory Society
2010-09-01
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| Series: | European Respiratory Review |
| Subjects: | |
| Online Access: | http://err.ersjournals.com/content/19/117/204.full.pdf+html |
| _version_ | 1811282374001950720 |
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| author | R. Naeije M. Delcroix |
| author_facet | R. Naeije M. Delcroix |
| author_sort | R. Naeije |
| collection | DOAJ |
| description | Pulmonary arterial hypertension (PAH) is a rare and potentially fatal disease whose management is usually restricted to a few specialised centres. As patients do not necessarily live in the neighbourhood of these centres, daily care and emergencies have to be delegated to first and second lines. Treatment guidelines do not usually provide recommendations for acute emergency situations as evidence is scarce. This short review provides a description of our therapeutic protocols based on available data. A model of transmural organisation of care for PAH patients, currently applied in Belgium, is described. Thereafter, based on an analysis of the reasons of death in the PAH population, a review of the main emergencies is provided. Cardiac arrest and resuscitation, decompensated right heart failure, respiratory failure, arrhythmia, pericardial effusion, haemoptysis, surgery and drug-related adverse events will be discussed successively. Case reports showing the precariousness of PAH patients will enforce our thesis of the need for optimal patient management organisation. |
| first_indexed | 2024-04-13T01:51:26Z |
| format | Article |
| id | doaj.art-2207b4661c774408bb281aab75641804 |
| institution | Directory Open Access Journal |
| issn | 0905-9180 1600-0617 |
| language | English |
| last_indexed | 2024-04-13T01:51:26Z |
| publishDate | 2010-09-01 |
| publisher | European Respiratory Society |
| record_format | Article |
| series | European Respiratory Review |
| spelling | doaj.art-2207b4661c774408bb281aab756418042022-12-22T03:07:52ZengEuropean Respiratory SocietyEuropean Respiratory Review0905-91801600-06172010-09-0119117204211Optimising the management of pulmonary arterial hypertension patients: emergency treatmentsR. NaeijeM. DelcroixPulmonary arterial hypertension (PAH) is a rare and potentially fatal disease whose management is usually restricted to a few specialised centres. As patients do not necessarily live in the neighbourhood of these centres, daily care and emergencies have to be delegated to first and second lines. Treatment guidelines do not usually provide recommendations for acute emergency situations as evidence is scarce. This short review provides a description of our therapeutic protocols based on available data. A model of transmural organisation of care for PAH patients, currently applied in Belgium, is described. Thereafter, based on an analysis of the reasons of death in the PAH population, a review of the main emergencies is provided. Cardiac arrest and resuscitation, decompensated right heart failure, respiratory failure, arrhythmia, pericardial effusion, haemoptysis, surgery and drug-related adverse events will be discussed successively. Case reports showing the precariousness of PAH patients will enforce our thesis of the need for optimal patient management organisation.http://err.ersjournals.com/content/19/117/204.full.pdf+htmlEmergenciesorganisation of carepulmonary arterial hypertension |
| spellingShingle | R. Naeije M. Delcroix Optimising the management of pulmonary arterial hypertension patients: emergency treatments European Respiratory Review Emergencies organisation of care pulmonary arterial hypertension |
| title | Optimising the management of pulmonary arterial hypertension patients: emergency treatments |
| title_full | Optimising the management of pulmonary arterial hypertension patients: emergency treatments |
| title_fullStr | Optimising the management of pulmonary arterial hypertension patients: emergency treatments |
| title_full_unstemmed | Optimising the management of pulmonary arterial hypertension patients: emergency treatments |
| title_short | Optimising the management of pulmonary arterial hypertension patients: emergency treatments |
| title_sort | optimising the management of pulmonary arterial hypertension patients emergency treatments |
| topic | Emergencies organisation of care pulmonary arterial hypertension |
| url | http://err.ersjournals.com/content/19/117/204.full.pdf+html |
| work_keys_str_mv | AT rnaeije optimisingthemanagementofpulmonaryarterialhypertensionpatientsemergencytreatments AT mdelcroix optimisingthemanagementofpulmonaryarterialhypertensionpatientsemergencytreatments |