Moyamoya disease in the practice of a pediatric-infectiologist
Moyamoya disease is a rare chronic cerebrovascular disorder characterized by gradually progressive luminal stenosis of the intracranial segments of the internal carotid artery and the initial segments of the anterior and middle cerebral arteries, thus forming a network of minor vascular anastomoses....
| Main Authors: | , , , , , , , , , , , |
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| Format: | Article |
| Language: | Russian |
| Published: |
Ltd. “The National Academy of Pediatric Science and Innovation”
2017-05-01
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| Series: | Rossijskij Vestnik Perinatologii i Pediatrii |
| Subjects: | |
| Online Access: | https://www.ped-perinatology.ru/jour/article/view/477 |
| Summary: | Moyamoya disease is a rare chronic cerebrovascular disorder characterized by gradually progressive luminal stenosis of the intracranial segments of the internal carotid artery and the initial segments of the anterior and middle cerebral arteries, thus forming a network of minor vascular anastomoses. Impaired blood supply in the above vessels due to occlusion leads to the development of ischemic and hemorrhagic strokes in the respective beds, causing a variety of neurological and visual disorders.Activation of herpesvirus infection in a 2-year-old infant provoked the onset of moyamoya disease. An abnormal posterior right eye segment (bindweed syndrome) detected by an ophthalmic examination, which is commonly concurrent with various cerebrovascular disorders, allowed cliniciansto adequately interpret mild transient neurologicalsymptoms and to rapidly diagnose moyamoya disease, by applying radiodiagnostic methods.The treatment involved antibiotic and antiviral therapy, infusion of glucose-salt solutions and encephabol. The infant’s status improved; seizures were stopped; right muscle tone fully recovered; and right hand tone remained reduced. Revascularization of the middle and anterior cerebral arteries were further performed. |
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| ISSN: | 1027-4065 2500-2228 |