Kartagener's syndrome presented with nasal obstruction: A case report

The nasal polyposis is a chronic inflammatory process of the nasal mucosa. Although it is rare in children, there may be also association with cystic fibrosis and primary ciliary dyskinesia. About 50% of primary ciliary dyskinesia patients develop situs inversus and it is known as Kartagener's...

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Main Authors: Suna Asilsoy, Buket Kilicaslan, Cem Ozer
Format: Article
Language:English
Published: Cukurova University 2014-08-01
Series:Çukurova Üniversitesi Tıp Fakültesi Dergisi
Subjects:
Online Access:http://www.scopemed.org/fulltextpdf.php?mno=159361
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author Suna Asilsoy
Buket Kilicaslan
Cem Ozer
author_facet Suna Asilsoy
Buket Kilicaslan
Cem Ozer
author_sort Suna Asilsoy
collection DOAJ
description The nasal polyposis is a chronic inflammatory process of the nasal mucosa. Although it is rare in children, there may be also association with cystic fibrosis and primary ciliary dyskinesia. About 50% of primary ciliary dyskinesia patients develop situs inversus and it is known as Kartagener's syndrome. The Kartagener's sydrome is a rare autosomal recessive disorder characterized by sinusitis, bronchiectasis, situs inversus. Clinically, patients present to the otolaryngologist with nasal obstruction. We as pediatricians, should consider nasal polyposis as a rare cause of nasal obstruction in children. In the presence of recurrent upper and lower respiratory tract infections accompanying nasal polyposis, Kartagener's syndrome must be kept in mind as a rare reason. [Cukurova Med J 2014; 39(4.000): 942-945]
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spelling doaj.art-23af641460484fe897735e6c60b21bfb2023-02-15T16:22:01ZengCukurova UniversityÇukurova Üniversitesi Tıp Fakültesi Dergisi0250-51502014-08-01394942945159361Kartagener's syndrome presented with nasal obstruction: A case reportSuna Asilsoy0Buket Kilicaslan1Cem Ozer2Baskent Universitesi Adana Uygulama ve Arastirma Merkezi Cocuk Allerji Bilim Dali Baskent Universitesi Adana Uygulama ve Arastirma Merkezi Cocuk Sagligi ve Hastaliklari Anabilim Dali Baskent Universitesi Adana Uygulama ve Arastirma Merkezi Kulak Burun Bogaz Anabilim DaliThe nasal polyposis is a chronic inflammatory process of the nasal mucosa. Although it is rare in children, there may be also association with cystic fibrosis and primary ciliary dyskinesia. About 50% of primary ciliary dyskinesia patients develop situs inversus and it is known as Kartagener's syndrome. The Kartagener's sydrome is a rare autosomal recessive disorder characterized by sinusitis, bronchiectasis, situs inversus. Clinically, patients present to the otolaryngologist with nasal obstruction. We as pediatricians, should consider nasal polyposis as a rare cause of nasal obstruction in children. In the presence of recurrent upper and lower respiratory tract infections accompanying nasal polyposis, Kartagener's syndrome must be kept in mind as a rare reason. [Cukurova Med J 2014; 39(4.000): 942-945]http://www.scopemed.org/fulltextpdf.php?mno=159361Nasal polyposisKartagener's syndromeprimary ciliary dyskinesiachildren
spellingShingle Suna Asilsoy
Buket Kilicaslan
Cem Ozer
Kartagener's syndrome presented with nasal obstruction: A case report
Çukurova Üniversitesi Tıp Fakültesi Dergisi
Nasal polyposis
Kartagener's syndrome
primary ciliary dyskinesia
children
title Kartagener's syndrome presented with nasal obstruction: A case report
title_full Kartagener's syndrome presented with nasal obstruction: A case report
title_fullStr Kartagener's syndrome presented with nasal obstruction: A case report
title_full_unstemmed Kartagener's syndrome presented with nasal obstruction: A case report
title_short Kartagener's syndrome presented with nasal obstruction: A case report
title_sort kartagener s syndrome presented with nasal obstruction a case report
topic Nasal polyposis
Kartagener's syndrome
primary ciliary dyskinesia
children
url http://www.scopemed.org/fulltextpdf.php?mno=159361
work_keys_str_mv AT sunaasilsoy kartagenerssyndromepresentedwithnasalobstructionacasereport
AT buketkilicaslan kartagenerssyndromepresentedwithnasalobstructionacasereport
AT cemozer kartagenerssyndromepresentedwithnasalobstructionacasereport