Delayed diagnosis and management of a congenital intranasal meningoencephalocele in a 24-year-old male

Background: Intranasal meningoencephalocele is a rare congenital malformation. It is defined by protrusion of cerebral tissue and meninges through a defect in the skull base. Serious complications usually occur in early childhood, however, symptoms occasionally can wait until adulthood. Case Pres...

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Main Authors: Ahtesham Khizar, Adeel Niaz, Syed Muhammad Azeem, Imran Ali, Khalid Mahmood
Format: Article
Language:English
Published: London Academic Publishing 2023-09-01
Series:Romanian Neurosurgery
Subjects:
Online Access:http://journals.lapub.co.uk/index.php/roneurosurgery/article/view/2313
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author Ahtesham Khizar
Adeel Niaz
Syed Muhammad Azeem
Imran Ali
Khalid Mahmood
author_facet Ahtesham Khizar
Adeel Niaz
Syed Muhammad Azeem
Imran Ali
Khalid Mahmood
author_sort Ahtesham Khizar
collection DOAJ
description Background: Intranasal meningoencephalocele is a rare congenital malformation. It is defined by protrusion of cerebral tissue and meninges through a defect in the skull base. Serious complications usually occur in early childhood, however, symptoms occasionally can wait until adulthood. Case Presentation: We report a case of a 24-year-old male who had a congenital intranasal meningoencephalocele with recurrent episodes of bacterial meningitis. After a delayed diagnosis, he eventually underwent Endoscopic Endonasal Repair of Meningoencephalocele via 'Bath-plug' technique. Conclusions: To prevent improper management, it is crucial that ENT colleagues, to whom these cases are primarily present, are well informed about this unusual condition. For the purpose of preventing further neurological problems, thorough neuroimaging evaluations and successful surgical repair are important. The 'Bath-plug' technique for anterior skull base cerebrospinal fluid leak repair is effective for a wide range of situations.
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spelling doaj.art-248e8923fa714809bce1c1e81624f4352023-09-29T02:22:37ZengLondon Academic PublishingRomanian Neurosurgery1220-88412344-49592023-09-01373Delayed diagnosis and management of a congenital intranasal meningoencephalocele in a 24-year-old maleAhtesham KhizarAdeel NiazSyed Muhammad Azeem Imran AliKhalid Mahmood Background: Intranasal meningoencephalocele is a rare congenital malformation. It is defined by protrusion of cerebral tissue and meninges through a defect in the skull base. Serious complications usually occur in early childhood, however, symptoms occasionally can wait until adulthood. Case Presentation: We report a case of a 24-year-old male who had a congenital intranasal meningoencephalocele with recurrent episodes of bacterial meningitis. After a delayed diagnosis, he eventually underwent Endoscopic Endonasal Repair of Meningoencephalocele via 'Bath-plug' technique. Conclusions: To prevent improper management, it is crucial that ENT colleagues, to whom these cases are primarily present, are well informed about this unusual condition. For the purpose of preventing further neurological problems, thorough neuroimaging evaluations and successful surgical repair are important. The 'Bath-plug' technique for anterior skull base cerebrospinal fluid leak repair is effective for a wide range of situations. http://journals.lapub.co.uk/index.php/roneurosurgery/article/view/2313congenitalintranasalmeningoencephaloceleCSF rhinorrhoeaendoscopy
spellingShingle Ahtesham Khizar
Adeel Niaz
Syed Muhammad Azeem
Imran Ali
Khalid Mahmood
Delayed diagnosis and management of a congenital intranasal meningoencephalocele in a 24-year-old male
Romanian Neurosurgery
congenital
intranasal
meningoencephalocele
CSF rhinorrhoea
endoscopy
title Delayed diagnosis and management of a congenital intranasal meningoencephalocele in a 24-year-old male
title_full Delayed diagnosis and management of a congenital intranasal meningoencephalocele in a 24-year-old male
title_fullStr Delayed diagnosis and management of a congenital intranasal meningoencephalocele in a 24-year-old male
title_full_unstemmed Delayed diagnosis and management of a congenital intranasal meningoencephalocele in a 24-year-old male
title_short Delayed diagnosis and management of a congenital intranasal meningoencephalocele in a 24-year-old male
title_sort delayed diagnosis and management of a congenital intranasal meningoencephalocele in a 24 year old male
topic congenital
intranasal
meningoencephalocele
CSF rhinorrhoea
endoscopy
url http://journals.lapub.co.uk/index.php/roneurosurgery/article/view/2313
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