Wunderlich Syndrome Managed with Angiomyolipoma Embolization – Renal Artery Anatomic Variant Augmenting Safe and Nephron-Sparing Intervention
Background: Wunderlich syndrome is an uncommon entity characterized by spontaneous, nontraumatic renal bleeding into the subcapsular and perirenal regions. The most frequent benign tumor, angiomyolipoma, is the most common cause of Wunderlich syndrome.Case presentation: We report a case of Wunderli...
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| Format: | Article |
| Language: | English |
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Vilnius University Press
2024-03-01
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| Series: | Acta Medica Lituanica |
| Subjects: | |
| Online Access: | https://www.journals.vu.lt/AML/article/view/32555 |
| _version_ | 1797194446039678976 |
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| author | Tara Prasad Tripathy Alamelu Alagappan Ranjan Kumar Patel Srikant Kumar Behera Sandip Kumar Panda Suprava Naik |
| author_facet | Tara Prasad Tripathy Alamelu Alagappan Ranjan Kumar Patel Srikant Kumar Behera Sandip Kumar Panda Suprava Naik |
| author_sort | Tara Prasad Tripathy |
| collection | DOAJ |
| description |
Background: Wunderlich syndrome is an uncommon entity characterized by spontaneous, nontraumatic renal bleeding into the subcapsular and perirenal regions. The most frequent benign tumor, angiomyolipoma, is the most common cause of Wunderlich syndrome.Case presentation: We report a case of Wunderlich syndrome in angiomyolipoma. Intratumoral pseudoaneurysm arising from feeders of an accessory renal artery supplying the lower pole of the kidney was selectively embolized. Rarely does a sporadic renal angiomyolipoma develop a giant pseudoaneurysm.Conclusion: Transarterial embolization is imperative to control the bleeding or as a preventative measure to reduce the risk of intralesional pseudoaneurysm rupture. When vascular interventional facilities are unavailable, surgery may be necessary.
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| first_indexed | 2024-03-07T15:41:22Z |
| format | Article |
| id | doaj.art-25450fb06ffb49f9851a3568b5c1ed4a |
| institution | Directory Open Access Journal |
| issn | 1392-0138 2029-4174 |
| language | English |
| last_indexed | 2024-04-24T05:56:24Z |
| publishDate | 2024-03-01 |
| publisher | Vilnius University Press |
| record_format | Article |
| series | Acta Medica Lituanica |
| spelling | doaj.art-25450fb06ffb49f9851a3568b5c1ed4a2024-04-23T08:58:36ZengVilnius University PressActa Medica Lituanica1392-01382029-41742024-03-0131110.15388/Amed.2024.31.1.3Wunderlich Syndrome Managed with Angiomyolipoma Embolization – Renal Artery Anatomic Variant Augmenting Safe and Nephron-Sparing InterventionTara Prasad Tripathy0https://orcid.org/0000-0003-3763-9089Alamelu Alagappan1https://orcid.org/0000-0003-3569-8771Ranjan Kumar Patel2Srikant Kumar Behera3Sandip Kumar Panda4Suprava Naik5MBBS, MD, PDCC, Department of Radiodiagnosis, AIIMS, Bhubaneswar, IndiaDepartment of Radiodiagnosis, AIIMS, Bhubaneswar, IndiaMBBS, MD, Radiodiagnosis, IndiaMBBS, MD, DM, Department of Medicine, AIIMS, Bhubaneswar, IndiaMBBS, MD, DM, Department of Nephrology, AIIMS, Bhubaneswar, IndiaMBBS, M.D., Department of Radiodiagnosis, AIIMS, Bhubaneswar, India Background: Wunderlich syndrome is an uncommon entity characterized by spontaneous, nontraumatic renal bleeding into the subcapsular and perirenal regions. The most frequent benign tumor, angiomyolipoma, is the most common cause of Wunderlich syndrome.Case presentation: We report a case of Wunderlich syndrome in angiomyolipoma. Intratumoral pseudoaneurysm arising from feeders of an accessory renal artery supplying the lower pole of the kidney was selectively embolized. Rarely does a sporadic renal angiomyolipoma develop a giant pseudoaneurysm.Conclusion: Transarterial embolization is imperative to control the bleeding or as a preventative measure to reduce the risk of intralesional pseudoaneurysm rupture. When vascular interventional facilities are unavailable, surgery may be necessary. https://www.journals.vu.lt/AML/article/view/32555Wunderlich syndromeembolizationangiomyolipoma |
| spellingShingle | Tara Prasad Tripathy Alamelu Alagappan Ranjan Kumar Patel Srikant Kumar Behera Sandip Kumar Panda Suprava Naik Wunderlich Syndrome Managed with Angiomyolipoma Embolization – Renal Artery Anatomic Variant Augmenting Safe and Nephron-Sparing Intervention Acta Medica Lituanica Wunderlich syndrome embolization angiomyolipoma |
| title | Wunderlich Syndrome Managed with Angiomyolipoma Embolization – Renal Artery Anatomic Variant Augmenting Safe and Nephron-Sparing Intervention |
| title_full | Wunderlich Syndrome Managed with Angiomyolipoma Embolization – Renal Artery Anatomic Variant Augmenting Safe and Nephron-Sparing Intervention |
| title_fullStr | Wunderlich Syndrome Managed with Angiomyolipoma Embolization – Renal Artery Anatomic Variant Augmenting Safe and Nephron-Sparing Intervention |
| title_full_unstemmed | Wunderlich Syndrome Managed with Angiomyolipoma Embolization – Renal Artery Anatomic Variant Augmenting Safe and Nephron-Sparing Intervention |
| title_short | Wunderlich Syndrome Managed with Angiomyolipoma Embolization – Renal Artery Anatomic Variant Augmenting Safe and Nephron-Sparing Intervention |
| title_sort | wunderlich syndrome managed with angiomyolipoma embolization renal artery anatomic variant augmenting safe and nephron sparing intervention |
| topic | Wunderlich syndrome embolization angiomyolipoma |
| url | https://www.journals.vu.lt/AML/article/view/32555 |
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