Langerhans cell histiocytosis of the rib
Langerhans cell histiocytosis (LCH) is a rare systemic disease characterized by the proliferation and accumulation of Langerhans cells derived from bone marrow myeloid progenitor cells. The disease can affect a single organ or multi-organ system. The main sites involved in LCH include bones, lungs,...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Elsevier
2021-01-01
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| Series: | Journal of Pediatric Surgery Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2213576620303328 |
| Summary: | Langerhans cell histiocytosis (LCH) is a rare systemic disease characterized by the proliferation and accumulation of Langerhans cells derived from bone marrow myeloid progenitor cells. The disease can affect a single organ or multi-organ system. The main sites involved in LCH include bones, lungs, central nervous system, liver, thymus, skin, and lymph nodes, causing focal or systemic effects. We report a rare case of LCH showing a single osteolytic lesion on the posterolateral side of the tenth rib of a 2-year-old boy who presented with upper back pain. |
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| ISSN: | 2213-5766 |