Persistent mullerian duct syndrome: A single-center experience
Context: Persistent Mullerian duct syndrome (PMDS) is a rare disorder. It is a type of male pseudohermaphroditism, usually presenting as “Hernia Uteri Inguinalis”. Aims: This study aims to present our experience of PMDS, over a 7-year period. Settings and Design: Our center is a tertiary care facili...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Wolters Kluwer Medknow Publications
2018-01-01
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| Series: | Journal of Indian Association of Pediatric Surgeons |
| Subjects: | |
| Online Access: | http://www.jiaps.com/article.asp?issn=0971-9261;year=2018;volume=23;issue=4;spage=203;epage=205;aulast=Natarajan |
| _version_ | 1811218687166775296 |
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| author | Saravanan Natarajan Manikandhan Periasamy Saminathan Rangasamy Shankar Mohan Prabakaran Sundararajan |
| author_facet | Saravanan Natarajan Manikandhan Periasamy Saminathan Rangasamy Shankar Mohan Prabakaran Sundararajan |
| author_sort | Saravanan Natarajan |
| collection | DOAJ |
| description | Context: Persistent Mullerian duct syndrome (PMDS) is a rare disorder. It is a type of male pseudohermaphroditism, usually presenting as “Hernia Uteri Inguinalis”.
Aims: This study aims to present our experience of PMDS, over a 7-year period.
Settings and Design: Our center is a tertiary care facility, situated in Tamil Nadu, a southern state of India.
Subjects and Methods: This is a retrospective study. The study period was from 2007 to 2015. Seven cases presented during that period. The difficulties in diagnosis, treatment options discussed, along with a review of literature are presented.
Results: Seven cases of PMDS presented over 8 years. Only four were diagnosed preoperatively. Mullerian remnants were excised in five cases.
Conclusions: PMDS is rare. Orchiopexy should be the goal of treatment. |
| first_indexed | 2024-04-12T07:12:30Z |
| format | Article |
| id | doaj.art-25afe9fe9668460cab5fadd6f0a13aab |
| institution | Directory Open Access Journal |
| issn | 0971-9261 1998-3891 |
| language | English |
| last_indexed | 2024-04-12T07:12:30Z |
| publishDate | 2018-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Journal of Indian Association of Pediatric Surgeons |
| spelling | doaj.art-25afe9fe9668460cab5fadd6f0a13aab2022-12-22T03:42:34ZengWolters Kluwer Medknow PublicationsJournal of Indian Association of Pediatric Surgeons0971-92611998-38912018-01-0123420320510.4103/jiaps.JIAPS_61_17Persistent mullerian duct syndrome: A single-center experienceSaravanan NatarajanManikandhan PeriasamySaminathan RangasamyShankar MohanPrabakaran SundararajanContext: Persistent Mullerian duct syndrome (PMDS) is a rare disorder. It is a type of male pseudohermaphroditism, usually presenting as “Hernia Uteri Inguinalis”. Aims: This study aims to present our experience of PMDS, over a 7-year period. Settings and Design: Our center is a tertiary care facility, situated in Tamil Nadu, a southern state of India. Subjects and Methods: This is a retrospective study. The study period was from 2007 to 2015. Seven cases presented during that period. The difficulties in diagnosis, treatment options discussed, along with a review of literature are presented. Results: Seven cases of PMDS presented over 8 years. Only four were diagnosed preoperatively. Mullerian remnants were excised in five cases. Conclusions: PMDS is rare. Orchiopexy should be the goal of treatment.http://www.jiaps.com/article.asp?issn=0971-9261;year=2018;volume=23;issue=4;spage=203;epage=205;aulast=NatarajanMale pseudohermaphroditismOrchipexypersistent Mullerian duct syndrometransverse testicular ectopia |
| spellingShingle | Saravanan Natarajan Manikandhan Periasamy Saminathan Rangasamy Shankar Mohan Prabakaran Sundararajan Persistent mullerian duct syndrome: A single-center experience Journal of Indian Association of Pediatric Surgeons Male pseudohermaphroditism Orchipexy persistent Mullerian duct syndrome transverse testicular ectopia |
| title | Persistent mullerian duct syndrome: A single-center experience |
| title_full | Persistent mullerian duct syndrome: A single-center experience |
| title_fullStr | Persistent mullerian duct syndrome: A single-center experience |
| title_full_unstemmed | Persistent mullerian duct syndrome: A single-center experience |
| title_short | Persistent mullerian duct syndrome: A single-center experience |
| title_sort | persistent mullerian duct syndrome a single center experience |
| topic | Male pseudohermaphroditism Orchipexy persistent Mullerian duct syndrome transverse testicular ectopia |
| url | http://www.jiaps.com/article.asp?issn=0971-9261;year=2018;volume=23;issue=4;spage=203;epage=205;aulast=Natarajan |
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