Adult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical Outcome
Background: Spinal hamartoma is an extremely rare lesion for symptomatic spinal cord compression in adult population. Without any association of spinal dysraphism and neurofibromatosis, only 3 cases have been reported in the literature. Case description: A 40-year-old man presented with lumbago femo...
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| Format: | Article |
| Language: | English |
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Al-Azhar University, Faculty of Medicine (Damietta)
2021-07-01
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| Series: | International Journal of Medical Arts |
| Subjects: | |
| Online Access: | https://ijma.journals.ekb.eg/article_160652_7a0bbe9d7c5cd1a6ecf9cc5edd7e61b0.pdf |
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| author | Nazmin Ahmed Shahidul Khan KM Tarikul Islam Avijit Dey Vishal Chavda Ottavio Tomasi Gianluca Scalia Giuseppe E. Umana Bipin Chaurasia |
| author_facet | Nazmin Ahmed Shahidul Khan KM Tarikul Islam Avijit Dey Vishal Chavda Ottavio Tomasi Gianluca Scalia Giuseppe E. Umana Bipin Chaurasia |
| author_sort | Nazmin Ahmed |
| collection | DOAJ |
| description | Background: Spinal hamartoma is an extremely rare lesion for symptomatic spinal cord compression in adult population. Without any association of spinal dysraphism and neurofibromatosis, only 3 cases have been reported in the literature. Case description: A 40-year-old man presented with lumbago femorica for 6 months. Gradually the symptoms worsened and he developed features of Cauda equina syndrome. Magnetic Resonence Imagimg demonstrated a heterogeneously hyperintense intradural extramedullary mass in both T1 and T2WI, involving conus medullaris and cauda equina, opposite to L1. Patient underwent near total resection of lesion through posterior midline approach. Histopathological features were consistent with hamartoma. Patient neurologically improved and follow up MRI at 6 months showed static small nodular tumor residue. Conclusion: To the best of our knowledge, current report is the fourth case of spinal hamartoma in adult male, without any association of spinal dysraphism and neurofibromatosis .This may be the first reported case from Bangladesh. |
| first_indexed | 2024-12-19T02:35:59Z |
| format | Article |
| id | doaj.art-25dd1a45dcb34951b26a7ce65e14309d |
| institution | Directory Open Access Journal |
| issn | 2636-4174 2682-3780 |
| language | English |
| last_indexed | 2024-12-19T02:35:59Z |
| publishDate | 2021-07-01 |
| publisher | Al-Azhar University, Faculty of Medicine (Damietta) |
| record_format | Article |
| series | International Journal of Medical Arts |
| spelling | doaj.art-25dd1a45dcb34951b26a7ce65e14309d2022-12-21T20:39:24ZengAl-Azhar University, Faculty of Medicine (Damietta)International Journal of Medical Arts2636-41742682-37802021-07-01331556156110.21608/ijma.2021.66305.1279160652Adult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical OutcomeNazmin Ahmed0Shahidul Khan1KM Tarikul Islam2Avijit Dey3Vishal Chavda4Ottavio Tomasi5Gianluca Scalia6Giuseppe E. Umana7Bipin Chaurasia8Department of Neurosurgery, Ibn Sina Diagnostic and Consultation Center, Lalbag, Dhaka, BangladeshConsultant, Department of Orthopaedic surgery, Bangabandhu Sheikh Mujib Medical University, Dhaka, BangladeshDepartment of Neurosurgery, Bangabandhu Sheikh Mujib Medical University, Dhaka, BangladeshDepartment of Neurosurgery, Bangabandhu Sheikh Mujib Medical University, Dhaka, BangladeshDivision of Anesthesia,Sardar Womens Hospital, Bapunagar, Ahmedabad, IndiaDepartment of Neurological Surgery,Christian Doppler Medical Centre, Laboratory for Microsurgical Neuroanatomy,Paracelsus Medical University,Salzburg, AustriaNeurosurgery Unit,Highly specialised Hospital and National importence,Garibaldi,Catania,ItalyDepartment of Neurosurgery,Trauma and Gamma Knief Centre,Cannizzaro Hospital,Catania,ItalyDepartment of Neurosurgery, Bhawani Hospital, Birgunj, NepalBackground: Spinal hamartoma is an extremely rare lesion for symptomatic spinal cord compression in adult population. Without any association of spinal dysraphism and neurofibromatosis, only 3 cases have been reported in the literature. Case description: A 40-year-old man presented with lumbago femorica for 6 months. Gradually the symptoms worsened and he developed features of Cauda equina syndrome. Magnetic Resonence Imagimg demonstrated a heterogeneously hyperintense intradural extramedullary mass in both T1 and T2WI, involving conus medullaris and cauda equina, opposite to L1. Patient underwent near total resection of lesion through posterior midline approach. Histopathological features were consistent with hamartoma. Patient neurologically improved and follow up MRI at 6 months showed static small nodular tumor residue. Conclusion: To the best of our knowledge, current report is the fourth case of spinal hamartoma in adult male, without any association of spinal dysraphism and neurofibromatosis .This may be the first reported case from Bangladesh.https://ijma.journals.ekb.eg/article_160652_7a0bbe9d7c5cd1a6ecf9cc5edd7e61b0.pdfhamartomaneurofibromatosisspinal dysraphism |
| spellingShingle | Nazmin Ahmed Shahidul Khan KM Tarikul Islam Avijit Dey Vishal Chavda Ottavio Tomasi Gianluca Scalia Giuseppe E. Umana Bipin Chaurasia Adult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical Outcome International Journal of Medical Arts hamartoma neurofibromatosis spinal dysraphism |
| title | Adult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical Outcome |
| title_full | Adult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical Outcome |
| title_fullStr | Adult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical Outcome |
| title_full_unstemmed | Adult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical Outcome |
| title_short | Adult Spinal Hamartoma Involving Conus Medullaris: Brief Review About Associated Congenital Abnormalities and Surgical Outcome |
| title_sort | adult spinal hamartoma involving conus medullaris brief review about associated congenital abnormalities and surgical outcome |
| topic | hamartoma neurofibromatosis spinal dysraphism |
| url | https://ijma.journals.ekb.eg/article_160652_7a0bbe9d7c5cd1a6ecf9cc5edd7e61b0.pdf |
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