Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent

The hemodynamics of anomalous origin of the pulmonary artery (PA) from the aorta is challenging. Different sources of blood supply to the lungs lead to a unique state of differential flow, pressure, and pulmonary vascular resistance in each lung. The decision for surgical reimplantation of the anoma...

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Main Authors: Saurabh Kumar Gupta, Mrigank Choubey, Sanjeev Kumar, Chetan Patel, Balram Airan
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2023-01-01
Series:Annals of Pediatric Cardiology
Subjects:
Online Access:http://www.annalspc.com/article.asp?issn=0974-2069;year=2023;volume=16;issue=1;spage=65;epage=70;aulast=Gupta
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author Saurabh Kumar Gupta
Mrigank Choubey
Sanjeev Kumar
Chetan Patel
Balram Airan
author_facet Saurabh Kumar Gupta
Mrigank Choubey
Sanjeev Kumar
Chetan Patel
Balram Airan
author_sort Saurabh Kumar Gupta
collection DOAJ
description The hemodynamics of anomalous origin of the pulmonary artery (PA) from the aorta is challenging. Different sources of blood supply to the lungs lead to a unique state of differential flow, pressure, and pulmonary vascular resistance in each lung. The decision for surgical reimplantation of the anomalous PA during infancy is easy. The assessment of operability beyond infancy, however, is perplexing. In this report, we describe stepwise multimodal hemodynamic evaluation and successful surgical management in a 15-year-old boy with an isolated anomalous origin of the right PA from the aorta. We also report 5-year hemodynamic data confirming sustained benefit over the long term, thus providing much-needed clinical validation of often cited Poiseuille's and Ohm's laws.
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spelling doaj.art-27f1a39baf39402095c23769c6a123dc2023-05-18T04:58:41ZengWolters Kluwer Medknow PublicationsAnnals of Pediatric Cardiology0974-20692023-01-01161657010.4103/apc.apc_98_22Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescentSaurabh Kumar GuptaMrigank ChoubeySanjeev KumarChetan PatelBalram AiranThe hemodynamics of anomalous origin of the pulmonary artery (PA) from the aorta is challenging. Different sources of blood supply to the lungs lead to a unique state of differential flow, pressure, and pulmonary vascular resistance in each lung. The decision for surgical reimplantation of the anomalous PA during infancy is easy. The assessment of operability beyond infancy, however, is perplexing. In this report, we describe stepwise multimodal hemodynamic evaluation and successful surgical management in a 15-year-old boy with an isolated anomalous origin of the right PA from the aorta. We also report 5-year hemodynamic data confirming sustained benefit over the long term, thus providing much-needed clinical validation of often cited Poiseuille's and Ohm's laws.http://www.annalspc.com/article.asp?issn=0974-2069;year=2023;volume=16;issue=1;spage=65;epage=70;aulast=Guptaanomalous origin of pulmonary arterycardiac catheterizationcardiac hemodynamicslung perfusionmagnetic resonance imaging
spellingShingle Saurabh Kumar Gupta
Mrigank Choubey
Sanjeev Kumar
Chetan Patel
Balram Airan
Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent
Annals of Pediatric Cardiology
anomalous origin of pulmonary artery
cardiac catheterization
cardiac hemodynamics
lung perfusion
magnetic resonance imaging
title Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent
title_full Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent
title_fullStr Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent
title_full_unstemmed Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent
title_short Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent
title_sort multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent
topic anomalous origin of pulmonary artery
cardiac catheterization
cardiac hemodynamics
lung perfusion
magnetic resonance imaging
url http://www.annalspc.com/article.asp?issn=0974-2069;year=2023;volume=16;issue=1;spage=65;epage=70;aulast=Gupta
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