Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent
The hemodynamics of anomalous origin of the pulmonary artery (PA) from the aorta is challenging. Different sources of blood supply to the lungs lead to a unique state of differential flow, pressure, and pulmonary vascular resistance in each lung. The decision for surgical reimplantation of the anoma...
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Format: | Article |
Language: | English |
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Wolters Kluwer Medknow Publications
2023-01-01
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Series: | Annals of Pediatric Cardiology |
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Online Access: | http://www.annalspc.com/article.asp?issn=0974-2069;year=2023;volume=16;issue=1;spage=65;epage=70;aulast=Gupta |
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author | Saurabh Kumar Gupta Mrigank Choubey Sanjeev Kumar Chetan Patel Balram Airan |
author_facet | Saurabh Kumar Gupta Mrigank Choubey Sanjeev Kumar Chetan Patel Balram Airan |
author_sort | Saurabh Kumar Gupta |
collection | DOAJ |
description | The hemodynamics of anomalous origin of the pulmonary artery (PA) from the aorta is challenging. Different sources of blood supply to the lungs lead to a unique state of differential flow, pressure, and pulmonary vascular resistance in each lung. The decision for surgical reimplantation of the anomalous PA during infancy is easy. The assessment of operability beyond infancy, however, is perplexing. In this report, we describe stepwise multimodal hemodynamic evaluation and successful surgical management in a 15-year-old boy with an isolated anomalous origin of the right PA from the aorta. We also report 5-year hemodynamic data confirming sustained benefit over the long term, thus providing much-needed clinical validation of often cited Poiseuille's and Ohm's laws. |
first_indexed | 2024-03-13T10:39:48Z |
format | Article |
id | doaj.art-27f1a39baf39402095c23769c6a123dc |
institution | Directory Open Access Journal |
issn | 0974-2069 |
language | English |
last_indexed | 2024-03-13T10:39:48Z |
publishDate | 2023-01-01 |
publisher | Wolters Kluwer Medknow Publications |
record_format | Article |
series | Annals of Pediatric Cardiology |
spelling | doaj.art-27f1a39baf39402095c23769c6a123dc2023-05-18T04:58:41ZengWolters Kluwer Medknow PublicationsAnnals of Pediatric Cardiology0974-20692023-01-01161657010.4103/apc.apc_98_22Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescentSaurabh Kumar GuptaMrigank ChoubeySanjeev KumarChetan PatelBalram AiranThe hemodynamics of anomalous origin of the pulmonary artery (PA) from the aorta is challenging. Different sources of blood supply to the lungs lead to a unique state of differential flow, pressure, and pulmonary vascular resistance in each lung. The decision for surgical reimplantation of the anomalous PA during infancy is easy. The assessment of operability beyond infancy, however, is perplexing. In this report, we describe stepwise multimodal hemodynamic evaluation and successful surgical management in a 15-year-old boy with an isolated anomalous origin of the right PA from the aorta. We also report 5-year hemodynamic data confirming sustained benefit over the long term, thus providing much-needed clinical validation of often cited Poiseuille's and Ohm's laws.http://www.annalspc.com/article.asp?issn=0974-2069;year=2023;volume=16;issue=1;spage=65;epage=70;aulast=Guptaanomalous origin of pulmonary arterycardiac catheterizationcardiac hemodynamicslung perfusionmagnetic resonance imaging |
spellingShingle | Saurabh Kumar Gupta Mrigank Choubey Sanjeev Kumar Chetan Patel Balram Airan Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent Annals of Pediatric Cardiology anomalous origin of pulmonary artery cardiac catheterization cardiac hemodynamics lung perfusion magnetic resonance imaging |
title | Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent |
title_full | Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent |
title_fullStr | Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent |
title_full_unstemmed | Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent |
title_short | Multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent |
title_sort | multimodality hemodynamic evaluation for optimizing management of anomalous origin of the right pulmonary artery from the aorta in an adolescent |
topic | anomalous origin of pulmonary artery cardiac catheterization cardiac hemodynamics lung perfusion magnetic resonance imaging |
url | http://www.annalspc.com/article.asp?issn=0974-2069;year=2023;volume=16;issue=1;spage=65;epage=70;aulast=Gupta |
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