Cored in the act: the use of models to understand core myopathies
The core myopathies are a group of congenital myopathies with variable clinical expression – ranging from early-onset skeletal-muscle weakness to later-onset disease of variable severity – that are identified by characteristic ‘core-like’ lesions in myofibers and the presence of hypothonia and slowl...
Main Authors: | Aurora Fusto, Louise A. Moyle, Penney M. Gilbert, Elena Pegoraro |
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Format: | Article |
Language: | English |
Published: |
The Company of Biologists
2019-12-01
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Series: | Disease Models & Mechanisms |
Subjects: | |
Online Access: | http://dmm.biologists.org/content/12/12/dmm041368 |
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