Temporal bone rhabdomyosarcoma mimicking otitis media complicated by facial nerve palsy

Abstract Background Rhabdomyosarcoma is common in childhood, especially, the head and neck region, yet involvement of the temporal bone is rare. Case presentation We reported a case of an embryonal rhabdomyosarcoma in a 4.5-year-old boy presenting with external auditory canal polyp and purulent otor...

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Bibliographic Details
Main Authors: Ahmed Galal, Omneya Ahmed, Azza M. Rizk, Hanan Yehia Tayel, Rania G. Aly
Format: Article
Language:English
Published: SpringerOpen 2021-07-01
Series:The Egyptian Journal of Otolaryngology
Subjects:
Online Access:https://doi.org/10.1186/s43163-021-00126-5
Description
Summary:Abstract Background Rhabdomyosarcoma is common in childhood, especially, the head and neck region, yet involvement of the temporal bone is rare. Case presentation We reported a case of an embryonal rhabdomyosarcoma in a 4.5-year-old boy presenting with external auditory canal polyp and purulent otorrhea that later developed grade 6 facial palsy. Imaging showed soft tissue mass involving the middle ear, mastoid cavity, parotid gland, and parapharyngeal space. Subtotal petrosectomy with blind closure of the external auditory canal was performed with facial nerve decompression and debulking biopsy followed by combined chemoradiation. Conclusion Middle ear rhabdomyosarcoma is a rare pathology, usually present in childhood by symptoms similar to suppurative otitis media not responding to medical treatment leading to delayed diagnosis and development of complications.
ISSN:1012-5574
2090-8539