Gorlin syndrome: A case report

Gorlin syndrome is a rare autosomal dominant disorder which characterize by multi-organ abnormities such as odontogenic keratocysts in the jaw, skeletal abnormities and multiple basal cell carcinoma etc. We report a case of this syndrome in a young man with palmar pits, multiple facial BCC, clacific...

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Main Authors: Abbas Darjani, Hojat Eftekhari, Nahid Nickhah
Format: Article
Language:English
Published: Our Dermatology Online 2016-01-01
Series:Nasza Dermatologia Online
Subjects:
Online Access:http://www.odermatol.com/issue-in-html/2016-1-18/
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author Abbas Darjani
Hojat Eftekhari
Nahid Nickhah
author_facet Abbas Darjani
Hojat Eftekhari
Nahid Nickhah
author_sort Abbas Darjani
collection DOAJ
description Gorlin syndrome is a rare autosomal dominant disorder which characterize by multi-organ abnormities such as odontogenic keratocysts in the jaw, skeletal abnormities and multiple basal cell carcinoma etc. We report a case of this syndrome in a young man with palmar pits, multiple facial BCC, clacifications of the falx cerebri and bifid rib.
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spelling doaj.art-28a686e726404a12af16fb55dff0b9dd2022-12-21T17:45:31ZengOur Dermatology OnlineNasza Dermatologia Online2081-93902081-93902016-01-0171727410.7241/ourd.20161.18Gorlin syndrome: A case reportAbbas Darjani0 Hojat Eftekhari1Nahid Nickhah2Department of Dermatology, Razi Medical Center, Guilan University of Medical Sciences, Rasht, IranDepartment of Dermatology, Razi Medical Center, Guilan University of Medical Sciences, Rasht, IranDepartment of Dermatology, Razi Medical Center, Guilan University of Medical Sciences, Rasht, IranGorlin syndrome is a rare autosomal dominant disorder which characterize by multi-organ abnormities such as odontogenic keratocysts in the jaw, skeletal abnormities and multiple basal cell carcinoma etc. We report a case of this syndrome in a young man with palmar pits, multiple facial BCC, clacifications of the falx cerebri and bifid rib.http://www.odermatol.com/issue-in-html/2016-1-18/Gorlin- Golts syndrome; Nevoid basal cell carcinoma syndrome; Odontogenic keratocysts; Bifid rib
spellingShingle Abbas Darjani
Hojat Eftekhari
Nahid Nickhah
Gorlin syndrome: A case report
Nasza Dermatologia Online
Gorlin- Golts syndrome; Nevoid basal cell carcinoma syndrome; Odontogenic keratocysts; Bifid rib
title Gorlin syndrome: A case report
title_full Gorlin syndrome: A case report
title_fullStr Gorlin syndrome: A case report
title_full_unstemmed Gorlin syndrome: A case report
title_short Gorlin syndrome: A case report
title_sort gorlin syndrome a case report
topic Gorlin- Golts syndrome; Nevoid basal cell carcinoma syndrome; Odontogenic keratocysts; Bifid rib
url http://www.odermatol.com/issue-in-html/2016-1-18/
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AT hojateftekhari gorlinsyndromeacasereport
AT nahidnickhah gorlinsyndromeacasereport