Gorlin syndrome: A case report
Gorlin syndrome is a rare autosomal dominant disorder which characterize by multi-organ abnormities such as odontogenic keratocysts in the jaw, skeletal abnormities and multiple basal cell carcinoma etc. We report a case of this syndrome in a young man with palmar pits, multiple facial BCC, clacific...
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Format: | Article |
Language: | English |
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Our Dermatology Online
2016-01-01
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Series: | Nasza Dermatologia Online |
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Online Access: | http://www.odermatol.com/issue-in-html/2016-1-18/ |
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author | Abbas Darjani Hojat Eftekhari Nahid Nickhah |
author_facet | Abbas Darjani Hojat Eftekhari Nahid Nickhah |
author_sort | Abbas Darjani |
collection | DOAJ |
description | Gorlin syndrome is a rare autosomal dominant disorder which characterize by multi-organ abnormities such as odontogenic keratocysts in the jaw, skeletal abnormities and multiple basal cell carcinoma etc. We report a case of this syndrome in a young man with palmar pits, multiple facial BCC, clacifications of the falx cerebri and bifid rib. |
first_indexed | 2024-12-23T13:18:41Z |
format | Article |
id | doaj.art-28a686e726404a12af16fb55dff0b9dd |
institution | Directory Open Access Journal |
issn | 2081-9390 2081-9390 |
language | English |
last_indexed | 2024-12-23T13:18:41Z |
publishDate | 2016-01-01 |
publisher | Our Dermatology Online |
record_format | Article |
series | Nasza Dermatologia Online |
spelling | doaj.art-28a686e726404a12af16fb55dff0b9dd2022-12-21T17:45:31ZengOur Dermatology OnlineNasza Dermatologia Online2081-93902081-93902016-01-0171727410.7241/ourd.20161.18Gorlin syndrome: A case reportAbbas Darjani0 Hojat Eftekhari1Nahid Nickhah2Department of Dermatology, Razi Medical Center, Guilan University of Medical Sciences, Rasht, IranDepartment of Dermatology, Razi Medical Center, Guilan University of Medical Sciences, Rasht, IranDepartment of Dermatology, Razi Medical Center, Guilan University of Medical Sciences, Rasht, IranGorlin syndrome is a rare autosomal dominant disorder which characterize by multi-organ abnormities such as odontogenic keratocysts in the jaw, skeletal abnormities and multiple basal cell carcinoma etc. We report a case of this syndrome in a young man with palmar pits, multiple facial BCC, clacifications of the falx cerebri and bifid rib.http://www.odermatol.com/issue-in-html/2016-1-18/Gorlin- Golts syndrome; Nevoid basal cell carcinoma syndrome; Odontogenic keratocysts; Bifid rib |
spellingShingle | Abbas Darjani Hojat Eftekhari Nahid Nickhah Gorlin syndrome: A case report Nasza Dermatologia Online Gorlin- Golts syndrome; Nevoid basal cell carcinoma syndrome; Odontogenic keratocysts; Bifid rib |
title | Gorlin syndrome: A case report |
title_full | Gorlin syndrome: A case report |
title_fullStr | Gorlin syndrome: A case report |
title_full_unstemmed | Gorlin syndrome: A case report |
title_short | Gorlin syndrome: A case report |
title_sort | gorlin syndrome a case report |
topic | Gorlin- Golts syndrome; Nevoid basal cell carcinoma syndrome; Odontogenic keratocysts; Bifid rib |
url | http://www.odermatol.com/issue-in-html/2016-1-18/ |
work_keys_str_mv | AT abbasdarjani gorlinsyndromeacasereport AT hojateftekhari gorlinsyndromeacasereport AT nahidnickhah gorlinsyndromeacasereport |