Idiopathic Retinal Vasculitis, Aneurysms and Neuroretinitis Syndrome Associated with Positive Perinuclear Antineutrophil Cytoplasmic Antibody

Purpose: To report a case of idiopathic retinal vasculitis, aneurysms and neuroretinitis (IRVAN) syndrome associated with positive perinuclear antineutrophil cytoplasmic antibody (P-ANCA). Case Report: A 51-year-old man presented with loss of vision in his right eye since many years ago and blurred...

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Main Authors: Ramin Nourinia, Talieh Montahai, Nasim Amoohashemi, Hossein Hassanpour, Masoud Soheilian
Format: Article
Language:English
Published: Knowledge E 2011-01-01
Series:Journal of Ophthalmic & Vision Research
Subjects:
Online Access:http://www.jovr.org/article.asp?issn=2008-322X;year=2011;volume=6;issue=4;spage=330;epage=333;aulast=Nourinia
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author Ramin Nourinia
Talieh Montahai
Nasim Amoohashemi
Hossein Hassanpour
Masoud Soheilian
author_facet Ramin Nourinia
Talieh Montahai
Nasim Amoohashemi
Hossein Hassanpour
Masoud Soheilian
author_sort Ramin Nourinia
collection DOAJ
description Purpose: To report a case of idiopathic retinal vasculitis, aneurysms and neuroretinitis (IRVAN) syndrome associated with positive perinuclear antineutrophil cytoplasmic antibody (P-ANCA). Case Report: A 51-year-old man presented with loss of vision in his right eye since many years ago and blurred vision in his left eye over the past year. Ophthalmologic examination revealed optic atrophy and old vascular sheathing in the right eye and blurred disc margin, macular exudation, flame shaped hemorrhages, retinal vascular sheathing and multiple aneurysms at arterial bifurcation sites in the left eye, findings compatible with IRVAN syndrome. On systemic workup, the only notable finding was P-ANCA positivity. Conclusion: IRVAN syndrome may be a retinal component of P-ANCA associated vasculitis.
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spelling doaj.art-29206b14f2214c84a056d309913fe1882022-12-22T03:56:17ZengKnowledge EJournal of Ophthalmic & Vision Research2008-322X2011-01-0164330333Idiopathic Retinal Vasculitis, Aneurysms and Neuroretinitis Syndrome Associated with Positive Perinuclear Antineutrophil Cytoplasmic AntibodyRamin NouriniaTalieh MontahaiNasim AmoohashemiHossein HassanpourMasoud SoheilianPurpose: To report a case of idiopathic retinal vasculitis, aneurysms and neuroretinitis (IRVAN) syndrome associated with positive perinuclear antineutrophil cytoplasmic antibody (P-ANCA). Case Report: A 51-year-old man presented with loss of vision in his right eye since many years ago and blurred vision in his left eye over the past year. Ophthalmologic examination revealed optic atrophy and old vascular sheathing in the right eye and blurred disc margin, macular exudation, flame shaped hemorrhages, retinal vascular sheathing and multiple aneurysms at arterial bifurcation sites in the left eye, findings compatible with IRVAN syndrome. On systemic workup, the only notable finding was P-ANCA positivity. Conclusion: IRVAN syndrome may be a retinal component of P-ANCA associated vasculitis.http://www.jovr.org/article.asp?issn=2008-322X;year=2011;volume=6;issue=4;spage=330;epage=333;aulast=NouriniaIRVAN Syndrome; P-ANCA
spellingShingle Ramin Nourinia
Talieh Montahai
Nasim Amoohashemi
Hossein Hassanpour
Masoud Soheilian
Idiopathic Retinal Vasculitis, Aneurysms and Neuroretinitis Syndrome Associated with Positive Perinuclear Antineutrophil Cytoplasmic Antibody
Journal of Ophthalmic & Vision Research
IRVAN Syndrome; P-ANCA
title Idiopathic Retinal Vasculitis, Aneurysms and Neuroretinitis Syndrome Associated with Positive Perinuclear Antineutrophil Cytoplasmic Antibody
title_full Idiopathic Retinal Vasculitis, Aneurysms and Neuroretinitis Syndrome Associated with Positive Perinuclear Antineutrophil Cytoplasmic Antibody
title_fullStr Idiopathic Retinal Vasculitis, Aneurysms and Neuroretinitis Syndrome Associated with Positive Perinuclear Antineutrophil Cytoplasmic Antibody
title_full_unstemmed Idiopathic Retinal Vasculitis, Aneurysms and Neuroretinitis Syndrome Associated with Positive Perinuclear Antineutrophil Cytoplasmic Antibody
title_short Idiopathic Retinal Vasculitis, Aneurysms and Neuroretinitis Syndrome Associated with Positive Perinuclear Antineutrophil Cytoplasmic Antibody
title_sort idiopathic retinal vasculitis aneurysms and neuroretinitis syndrome associated with positive perinuclear antineutrophil cytoplasmic antibody
topic IRVAN Syndrome; P-ANCA
url http://www.jovr.org/article.asp?issn=2008-322X;year=2011;volume=6;issue=4;spage=330;epage=333;aulast=Nourinia
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AT nasimamoohashemi idiopathicretinalvasculitisaneurysmsandneuroretinitissyndromeassociatedwithpositiveperinuclearantineutrophilcytoplasmicantibody
AT hosseinhassanpour idiopathicretinalvasculitisaneurysmsandneuroretinitissyndromeassociatedwithpositiveperinuclearantineutrophilcytoplasmicantibody
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