Large para-testicular intra-scrotal malignant peripheral nerve sheath tumor managed with radical penectomy: A case report

Neurofibromatosis 1 is a relatively rare genetic disease characterized by widespread neurofibromas originating from the peripheral nervous system. Most growths are benign, but some carry a risk of transformation to malignant peripheral nerve sheath tumors. Although these growths can be found anywher...

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Bibliographic Details
Main Authors: Austin G. Kazarian, Jeremy M. West, James A. Brown, Bradley A. Erickson, Paul T. Gellhaus
Format: Article
Language:English
Published: Elsevier 2021-09-01
Series:Urology Case Reports
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Online Access:http://www.sciencedirect.com/science/article/pii/S2214442021001352
Description
Summary:Neurofibromatosis 1 is a relatively rare genetic disease characterized by widespread neurofibromas originating from the peripheral nervous system. Most growths are benign, but some carry a risk of transformation to malignant peripheral nerve sheath tumors. Although these growths can be found anywhere in the body, they are rarely found in the male external genitalia. This report discusses a case of a 25-year-old male patient with neurofibromatosis 1 presenting with a scrotal mass found to have a very large para-testicular intra-scrotal malignant peripheral nerve sheath tumor that required testicle-sparing radical penectomy.
ISSN:2214-4420