Glaucoma in Ectropion Uveae Syndrome: A Case Report and Literature Review

Purpose: To report a case of advanced childhood glaucoma secondary to congenital ectropion uveae (CEU). Case Report: The patient was a seven-year-old boy with unilateral glaucoma secondary to CEU and facial asymmetry, mild unilateral ptosis, and proptosis in the left eye. The intraocular press...

Full description

Bibliographic Details
Main Authors: Mohammadmehdi Hatami, Azadeh Doozandeh, Mohadeseh Feizi
Format: Article
Language:English
Published: Knowledge E 2019-07-01
Series:Journal of Ophthalmic & Vision Research
Online Access:https://doi.org/10.18502/jovr.v14i3.4793
_version_ 1811323620770709504
author Mohammadmehdi Hatami
Azadeh Doozandeh
Mohadeseh Feizi
author_facet Mohammadmehdi Hatami
Azadeh Doozandeh
Mohadeseh Feizi
author_sort Mohammadmehdi Hatami
collection DOAJ
description Purpose: To report a case of advanced childhood glaucoma secondary to congenital ectropion uveae (CEU). Case Report: The patient was a seven-year-old boy with unilateral glaucoma secondary to CEU and facial asymmetry, mild unilateral ptosis, and proptosis in the left eye. The intraocular pressure (IOP) was 28 mmHg and cup-to-disc ratio was 0.8 in the left eye. After starting glaucoma medication, IOP decreased to 21 mmHg. In view of the uncontrolled IOP with medication and high cup-to-disc ratio and increased axial length of the left eye, mitomycin-C (MMC)-augmented trabeculectomy was planned. Despite sub-tenon MMC injection and bleb needling, the bleb failed after six months, and we had to perform a shunt procedure to control the IOP. Conclusion: Although CEU is rare, ophthalmologists should be familiar with this syndrome because of the high frequency of glaucoma and its challenging management during childhood.
first_indexed 2024-04-13T13:58:28Z
format Article
id doaj.art-2acf5f5fd7744e5d9c4208f9bb032a07
institution Directory Open Access Journal
issn 2008-322X
language English
last_indexed 2024-04-13T13:58:28Z
publishDate 2019-07-01
publisher Knowledge E
record_format Article
series Journal of Ophthalmic & Vision Research
spelling doaj.art-2acf5f5fd7744e5d9c4208f9bb032a072022-12-22T02:44:06ZengKnowledge EJournal of Ophthalmic & Vision Research2008-322X2019-07-01141610.18502/jovr.v14i3.4793jovr.v14i3.4793Glaucoma in Ectropion Uveae Syndrome: A Case Report and Literature ReviewMohammadmehdi HatamiAzadeh DoozandehMohadeseh FeiziPurpose: To report a case of advanced childhood glaucoma secondary to congenital ectropion uveae (CEU). Case Report: The patient was a seven-year-old boy with unilateral glaucoma secondary to CEU and facial asymmetry, mild unilateral ptosis, and proptosis in the left eye. The intraocular pressure (IOP) was 28 mmHg and cup-to-disc ratio was 0.8 in the left eye. After starting glaucoma medication, IOP decreased to 21 mmHg. In view of the uncontrolled IOP with medication and high cup-to-disc ratio and increased axial length of the left eye, mitomycin-C (MMC)-augmented trabeculectomy was planned. Despite sub-tenon MMC injection and bleb needling, the bleb failed after six months, and we had to perform a shunt procedure to control the IOP. Conclusion: Although CEU is rare, ophthalmologists should be familiar with this syndrome because of the high frequency of glaucoma and its challenging management during childhood.https://doi.org/10.18502/jovr.v14i3.4793
spellingShingle Mohammadmehdi Hatami
Azadeh Doozandeh
Mohadeseh Feizi
Glaucoma in Ectropion Uveae Syndrome: A Case Report and Literature Review
Journal of Ophthalmic & Vision Research
title Glaucoma in Ectropion Uveae Syndrome: A Case Report and Literature Review
title_full Glaucoma in Ectropion Uveae Syndrome: A Case Report and Literature Review
title_fullStr Glaucoma in Ectropion Uveae Syndrome: A Case Report and Literature Review
title_full_unstemmed Glaucoma in Ectropion Uveae Syndrome: A Case Report and Literature Review
title_short Glaucoma in Ectropion Uveae Syndrome: A Case Report and Literature Review
title_sort glaucoma in ectropion uveae syndrome a case report and literature review
url https://doi.org/10.18502/jovr.v14i3.4793
work_keys_str_mv AT mohammadmehdihatami glaucomainectropionuveaesyndromeacasereportandliteraturereview
AT azadehdoozandeh glaucomainectropionuveaesyndromeacasereportandliteraturereview
AT mohadesehfeizi glaucomainectropionuveaesyndromeacasereportandliteraturereview