A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease

IgG4-related lung disease (IgG4-RLD) is a rare and chronic progressive autoimmune disease. We report a case of IgG4-related inflammatory pseudo-tumor of the lung that was seropositive for proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA). A 61-year-old male had a mass lesion in the right...

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Main Authors: Hirokazu Touge, Katsuyuki Tomita, Akira Yamasaki, Eiji Shimizu
Format: Article
Language:English
Published: Elsevier 2017-01-01
Series:Respiratory Medicine Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2213007116302192
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author Hirokazu Touge
Katsuyuki Tomita
Akira Yamasaki
Eiji Shimizu
author_facet Hirokazu Touge
Katsuyuki Tomita
Akira Yamasaki
Eiji Shimizu
author_sort Hirokazu Touge
collection DOAJ
description IgG4-related lung disease (IgG4-RLD) is a rare and chronic progressive autoimmune disease. We report a case of IgG4-related inflammatory pseudo-tumor of the lung that was seropositive for proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA). A 61-year-old male had a mass lesion in the right lower lung field in chest X-ray. Transbronchial lung biopsy resulted in a pathological diagnosis of IgG4-RLD. The condition was improved by hormonal therapy.
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spelling doaj.art-2ae5c80707a54094b4dc3add741faea92022-12-21T20:50:30ZengElsevierRespiratory Medicine Case Reports2213-00712017-01-0120C929410.1016/j.rmcr.2017.01.001A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung diseaseHirokazu Touge0Katsuyuki Tomita1Akira Yamasaki2Eiji Shimizu3Department of Respiratory Medicine, Yonago Medical Centre, Tottori, JapanDepartment of Respiratory Medicine, Yonago Medical Centre, Tottori, JapanDivision of Medical Oncology and Molecular Respirology, Tottori University Faculty of Medicine, Tottori, JapanDivision of Medical Oncology and Molecular Respirology, Tottori University Faculty of Medicine, Tottori, JapanIgG4-related lung disease (IgG4-RLD) is a rare and chronic progressive autoimmune disease. We report a case of IgG4-related inflammatory pseudo-tumor of the lung that was seropositive for proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA). A 61-year-old male had a mass lesion in the right lower lung field in chest X-ray. Transbronchial lung biopsy resulted in a pathological diagnosis of IgG4-RLD. The condition was improved by hormonal therapy.http://www.sciencedirect.com/science/article/pii/S2213007116302192IgG4LungPR3-ANCA
spellingShingle Hirokazu Touge
Katsuyuki Tomita
Akira Yamasaki
Eiji Shimizu
A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease
Respiratory Medicine Case Reports
IgG4
Lung
PR3-ANCA
title A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease
title_full A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease
title_fullStr A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease
title_full_unstemmed A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease
title_short A case of proteinase 3 anti-neutrophil cytoplasmic antibody (PR3-ANCA) positive/IgG4-related lung disease
title_sort case of proteinase 3 anti neutrophil cytoplasmic antibody pr3 anca positive igg4 related lung disease
topic IgG4
Lung
PR3-ANCA
url http://www.sciencedirect.com/science/article/pii/S2213007116302192
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