Cyclic vomiting syndrome in children: a nationwide survey of current practice on behalf of the Italian Society of Pediatric Gastroenterology, Hepatology and Nutrition (SIGENP) and Italian Society of Pediatric Neurology (SINP)

Abstract Background Cyclic Vomiting Syndrome (CVS) is a rare functional gastrointestinal disorder, which has a considerable burden on quality of life of both children and their family. Aim of the study was to evaluate the diagnostic modalities and therapeutic approach to CVS among Italian tertiary c...

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Main Authors: Sara Isoldi, Giovanni Di Nardo, Saverio Mallardo, Pasquale Parisi, Umberto Raucci, Renato Tambucci, Paolo Quitadamo, Silvia Salvatore, Enrico Felici, Fabio Cisarò, Licia Pensabene, Claudia Banzato, Caterina Strisciuglio, Claudio Romano, Patrizia Fusco, Francesca Rigotti, Naire Sansotta, Silvia Caimmi, Salvatore Savasta, Giovanna Zuin, Marina Di Stefano, Silvia Provera, Angelo Campanozzi, Paolo Rossi, Simona Gatti, Mara Corpino, Patrizia Alvisi, Stefano Martelossi, Agnese Suppiej, Paolo Gandullia, Alberto Verrotti, Gianluca Terrin, Caterina Pacenza, Fabiola Fornaroli, Donatella Comito, Stefano D’Arrigo, Pasquale Striano, Federico Raviglione, Marco Carotenuto, Alessandro Orsini, Vincenzo Belcastro, Giovanna Di Corcia, Vincenzo Raieli, Michela Ada Noris Ferilli, Claudia Ruscitto, Elisabetta Spadoni, Salvatore Grosso, Renato D’Alonzo, Amanda Papa, Piero Pavone, Mariaclaudia Meli, Mario Velardita, Martina Mainetti, Nicola Vanacore, Osvaldo Borrelli
Format: Article
Language:English
Published: BMC 2022-08-01
Series:Italian Journal of Pediatrics
Subjects:
Online Access:https://doi.org/10.1186/s13052-022-01346-y
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author Sara Isoldi
Giovanni Di Nardo
Saverio Mallardo
Pasquale Parisi
Umberto Raucci
Renato Tambucci
Paolo Quitadamo
Silvia Salvatore
Enrico Felici
Fabio Cisarò
Licia Pensabene
Claudia Banzato
Caterina Strisciuglio
Claudio Romano
Patrizia Fusco
Francesca Rigotti
Naire Sansotta
Silvia Caimmi
Salvatore Savasta
Giovanna Zuin
Marina Di Stefano
Silvia Provera
Angelo Campanozzi
Paolo Rossi
Simona Gatti
Mara Corpino
Patrizia Alvisi
Stefano Martelossi
Agnese Suppiej
Paolo Gandullia
Alberto Verrotti
Gianluca Terrin
Caterina Pacenza
Fabiola Fornaroli
Donatella Comito
Stefano D’Arrigo
Pasquale Striano
Federico Raviglione
Marco Carotenuto
Alessandro Orsini
Vincenzo Belcastro
Giovanna Di Corcia
Vincenzo Raieli
Michela Ada Noris Ferilli
Claudia Ruscitto
Elisabetta Spadoni
Salvatore Grosso
Renato D’Alonzo
Amanda Papa
Piero Pavone
Mariaclaudia Meli
Mario Velardita
Martina Mainetti
Nicola Vanacore
Osvaldo Borrelli
author_facet Sara Isoldi
Giovanni Di Nardo
Saverio Mallardo
Pasquale Parisi
Umberto Raucci
Renato Tambucci
Paolo Quitadamo
Silvia Salvatore
Enrico Felici
Fabio Cisarò
Licia Pensabene
Claudia Banzato
Caterina Strisciuglio
Claudio Romano
Patrizia Fusco
Francesca Rigotti
Naire Sansotta
Silvia Caimmi
Salvatore Savasta
Giovanna Zuin
Marina Di Stefano
Silvia Provera
Angelo Campanozzi
Paolo Rossi
Simona Gatti
Mara Corpino
Patrizia Alvisi
Stefano Martelossi
Agnese Suppiej
Paolo Gandullia
Alberto Verrotti
Gianluca Terrin
Caterina Pacenza
Fabiola Fornaroli
Donatella Comito
Stefano D’Arrigo
Pasquale Striano
Federico Raviglione
Marco Carotenuto
Alessandro Orsini
Vincenzo Belcastro
Giovanna Di Corcia
Vincenzo Raieli
Michela Ada Noris Ferilli
Claudia Ruscitto
Elisabetta Spadoni
Salvatore Grosso
Renato D’Alonzo
Amanda Papa
Piero Pavone
Mariaclaudia Meli
Mario Velardita
Martina Mainetti
Nicola Vanacore
Osvaldo Borrelli
author_sort Sara Isoldi
collection DOAJ
description Abstract Background Cyclic Vomiting Syndrome (CVS) is a rare functional gastrointestinal disorder, which has a considerable burden on quality of life of both children and their family. Aim of the study was to evaluate the diagnostic modalities and therapeutic approach to CVS among Italian tertiary care centers and the differences according to subspecialties, as well as to explore whether potential predictive factors associated with either a poor outcome or a response to a specific treatment. Methods Cross-sectional multicenter web-based survey involving members of the Italian Society of Pediatric Gastroenterology, Hepatology and Nutrition (SIGENP) and Italian Society of Pediatric Neurology (SINP). Results A total of 67 responses were received and analyzed. Most of the respondent units cared for less than 20 patients. More than half of the patients were referred after 3 to 5 episodes, and a quarter after 5 attacks. We report different diagnostic approaches among Italian clinicians, which was particularly evident when comparing gastroenterologists and neurologists. Moreover, our survey demonstrated a predilection of certain drugs during emetic phase according to specific clinic, which reflects the cultural background of physicians. Conclusion In conclusion, our survey highlights poor consensus amongst clinicians in our country in the diagnosis and the management of children with CVS, raising the need for a national consensus guideline in order to standardize the practice.
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spelling doaj.art-2aea540e6a29406da26f892dd9d53b662022-12-22T04:24:06ZengBMCItalian Journal of Pediatrics1824-72882022-08-014811910.1186/s13052-022-01346-yCyclic vomiting syndrome in children: a nationwide survey of current practice on behalf of the Italian Society of Pediatric Gastroenterology, Hepatology and Nutrition (SIGENP) and Italian Society of Pediatric Neurology (SINP)Sara Isoldi0Giovanni Di Nardo1Saverio Mallardo2Pasquale Parisi3Umberto Raucci4Renato Tambucci5Paolo Quitadamo6Silvia Salvatore7Enrico Felici8Fabio Cisarò9Licia Pensabene10Claudia Banzato11Caterina Strisciuglio12Claudio Romano13Patrizia Fusco14Francesca Rigotti15Naire Sansotta16Silvia Caimmi17Salvatore Savasta18Giovanna Zuin19Marina Di Stefano20Silvia Provera21Angelo Campanozzi22Paolo Rossi23Simona Gatti24Mara Corpino25Patrizia Alvisi26Stefano Martelossi27Agnese Suppiej28Paolo Gandullia29Alberto Verrotti30Gianluca Terrin31Caterina Pacenza32Fabiola Fornaroli33Donatella Comito34Stefano D’Arrigo35Pasquale Striano36Federico Raviglione37Marco Carotenuto38Alessandro Orsini39Vincenzo Belcastro40Giovanna Di Corcia41Vincenzo Raieli42Michela Ada Noris Ferilli43Claudia Ruscitto44Elisabetta Spadoni45Salvatore Grosso46Renato D’Alonzo47Amanda Papa48Piero Pavone49Mariaclaudia Meli50Mario Velardita51Martina Mainetti52Nicola Vanacore53Osvaldo Borrelli54Maternal and Child Health Department, Santa Maria Goretti Hospital, Sapienza-University of RomeDepartment of Neuroscience, Mental Health and Sense Organs (NESMOS), Faculty of Medicine & Psychology, Sant’Andrea Hospital, Sapienza University of RomeMaternal and Child Health Department, Santa Maria Goretti Hospital, Sapienza-University of RomeDepartment of Neuroscience, Mental Health and Sense Organs (NESMOS), Faculty of Medicine & Psychology, Sant’Andrea Hospital, Sapienza University of RomePediatric Emergency Department, Bambino Gesù Children’s Hospital, Institute for Research, Hospitalization and Health Care (IRCCS)Digestive Endoscopy and Surgery Unit, Bambino Gesù Children’s Hospital, Institute for Research, Hospitalization and Health Care (IRCCS)Department of Pediatrics, A.O.R.N. Santobono-PausiliponPediatric Department, Ospedale “F. Del Ponte”, University of InsubriaUnit of Pediatrics, The Children Hospital, Azienda Ospedaliera SS Antonio e Biagio e Cesare ArrigoPediatric Gastroenterology Unit, Regina Margherita Children’s Hospital, Azienda Ospedaliera-Universitaria, Città della Salute e della Scienza di TorinoPediatric Unit, Department of Medical and Surgical Sciences, University “Magna Graecia” of CatanzaroDepartment of Surgical Sciences, Dentistry, Gynecology and Pediatrics, Pediatric Division, University of VeronaDepartment of Woman, Child, General and Specialistic Surgery, University of Campania “Luigi Vanvitelli”Pediatric Gastroenterology Unit, Department of Human Pathology in Adulthood and Childhood “G. Barresi”, University of MessinaPediatric Unit, Montis Regalis HospitalDepartment of Pediatrics, Bolzano HospitalPaediatric Hepatology, Gastroenterology and Transplantation, Hospital Papa Giovanni XXIIIPediatric Clinic, Foundation IRCCS Policlinico San Matteo, University of PaviaPediatric Clinic, Foundation IRCCS Policlinico San Matteo, University of PaviaPediatric Department, University of Milano Bicocca, FMBBM, San Gerardo HospitalDepartment of Pediatrics, IRCCS San Raffaele Scientific InstituteDepartment of Pediatrics, IRCCS Sacro Cuore Don Calabria HospitalDepartment of Medical and Surgical Sciences, Pediatric Unit, University of FoggiaDepartment of Pediatrics, Pediatric Gastroenterology and Liver Unit, Sapienza University of RomeDepartment of Pediatrics, Università Politecnica delle MarcheGastroenterologia Pediatrica, Clinica Pediatrica e Malattie Rare, Ospedale Pediatrico Microcitemico A. Cao, ARNAS BrotzuDepartment of Paediatrics, Ospedale Maggiore, Azienda USLPediatric Unit, Ca’ Foncello’s HospitalPediatric Section, Department of Medical Sciences, University of FerraraUOC Gastroenterologia, IRCCS Istituto Giannina GasliniDepartment of Pediatrics, University of PerugiaDepartment of Maternal and Child Health, Policlinico Umberto I, Sapienza University of RomeDepartment of Pediatrics, San Giovanni di Dio HospitalGastroenterology and Endoscopy Unit, Department of Medicine and Surgery, University of ParmaOspedale Santa CroceDevelopmental Neurology Division, Fondazione IRCCS Istituto Neurologico Carlo BestaPediatric Neurology Unit, IRCCS Istituto Giannina GasliniHospital Neuropsychiatry Service, ASST RhodenseClinic of Child and Adolescent Neuropsychiatry, Department of Mental Health and Physical and Preventive Medicine, Università degli Studi della Campania “Luigi Vanvitelli”Paediatric Neurology Section, Paediatric Department, Pisa University Hospital, University of PisaNeurology Unit, Maggiore HospitalPediatric Department, “Augusto Murri” HospitalChild Neuropsychiatry Unit - ISMEP- ARNAS CIVICODepartment of Neuroscience, Paediatric Headache Center, Bambino Gesù Children Hospital, IRCCSChild Neurology and Psychiatry Unit, Systems Medicine Department, Tor Vergata University Hospital of RomePediatric Department, Azienda Ospedaliera Nord-Ovest of Tuscany, San Luca Hospital of LuccaMolecular Medicine and Development, University of SienaPediatric and Neonatological Unit, Maternal and Child Department, Nuovo Ospedale San Giovanni BattistaInfantile Neuropsychiatry Departement Maggiore della Carità University HospitalSection of Pediatrics and Child Neuropsychiatry, Department of Clinical and Experimental Medicine, University of CataniaAzienda Policlinico, “Rodolico-San Marco Hospital”, University of CataniaDepartment of Pediatrics, Hospital “Salvatore e Saverio Gravina”Department of Pediatrics, Santa Maria delle Croci HospitalNational Centre for Epidemiology, Surveillance and Health Promotion, National Institute of HealthDivision of Neurogastroenterology and Motility, Department of Pediatric Gastroenterology, University College London (UCL) Institute of Child Health and Great Ormond Street HospitalAbstract Background Cyclic Vomiting Syndrome (CVS) is a rare functional gastrointestinal disorder, which has a considerable burden on quality of life of both children and their family. Aim of the study was to evaluate the diagnostic modalities and therapeutic approach to CVS among Italian tertiary care centers and the differences according to subspecialties, as well as to explore whether potential predictive factors associated with either a poor outcome or a response to a specific treatment. Methods Cross-sectional multicenter web-based survey involving members of the Italian Society of Pediatric Gastroenterology, Hepatology and Nutrition (SIGENP) and Italian Society of Pediatric Neurology (SINP). Results A total of 67 responses were received and analyzed. Most of the respondent units cared for less than 20 patients. More than half of the patients were referred after 3 to 5 episodes, and a quarter after 5 attacks. We report different diagnostic approaches among Italian clinicians, which was particularly evident when comparing gastroenterologists and neurologists. Moreover, our survey demonstrated a predilection of certain drugs during emetic phase according to specific clinic, which reflects the cultural background of physicians. Conclusion In conclusion, our survey highlights poor consensus amongst clinicians in our country in the diagnosis and the management of children with CVS, raising the need for a national consensus guideline in order to standardize the practice.https://doi.org/10.1186/s13052-022-01346-yCyclic vomitingManagementOutcomesPediatric
spellingShingle Sara Isoldi
Giovanni Di Nardo
Saverio Mallardo
Pasquale Parisi
Umberto Raucci
Renato Tambucci
Paolo Quitadamo
Silvia Salvatore
Enrico Felici
Fabio Cisarò
Licia Pensabene
Claudia Banzato
Caterina Strisciuglio
Claudio Romano
Patrizia Fusco
Francesca Rigotti
Naire Sansotta
Silvia Caimmi
Salvatore Savasta
Giovanna Zuin
Marina Di Stefano
Silvia Provera
Angelo Campanozzi
Paolo Rossi
Simona Gatti
Mara Corpino
Patrizia Alvisi
Stefano Martelossi
Agnese Suppiej
Paolo Gandullia
Alberto Verrotti
Gianluca Terrin
Caterina Pacenza
Fabiola Fornaroli
Donatella Comito
Stefano D’Arrigo
Pasquale Striano
Federico Raviglione
Marco Carotenuto
Alessandro Orsini
Vincenzo Belcastro
Giovanna Di Corcia
Vincenzo Raieli
Michela Ada Noris Ferilli
Claudia Ruscitto
Elisabetta Spadoni
Salvatore Grosso
Renato D’Alonzo
Amanda Papa
Piero Pavone
Mariaclaudia Meli
Mario Velardita
Martina Mainetti
Nicola Vanacore
Osvaldo Borrelli
Cyclic vomiting syndrome in children: a nationwide survey of current practice on behalf of the Italian Society of Pediatric Gastroenterology, Hepatology and Nutrition (SIGENP) and Italian Society of Pediatric Neurology (SINP)
Italian Journal of Pediatrics
Cyclic vomiting
Management
Outcomes
Pediatric
title Cyclic vomiting syndrome in children: a nationwide survey of current practice on behalf of the Italian Society of Pediatric Gastroenterology, Hepatology and Nutrition (SIGENP) and Italian Society of Pediatric Neurology (SINP)
title_full Cyclic vomiting syndrome in children: a nationwide survey of current practice on behalf of the Italian Society of Pediatric Gastroenterology, Hepatology and Nutrition (SIGENP) and Italian Society of Pediatric Neurology (SINP)
title_fullStr Cyclic vomiting syndrome in children: a nationwide survey of current practice on behalf of the Italian Society of Pediatric Gastroenterology, Hepatology and Nutrition (SIGENP) and Italian Society of Pediatric Neurology (SINP)
title_full_unstemmed Cyclic vomiting syndrome in children: a nationwide survey of current practice on behalf of the Italian Society of Pediatric Gastroenterology, Hepatology and Nutrition (SIGENP) and Italian Society of Pediatric Neurology (SINP)
title_short Cyclic vomiting syndrome in children: a nationwide survey of current practice on behalf of the Italian Society of Pediatric Gastroenterology, Hepatology and Nutrition (SIGENP) and Italian Society of Pediatric Neurology (SINP)
title_sort cyclic vomiting syndrome in children a nationwide survey of current practice on behalf of the italian society of pediatric gastroenterology hepatology and nutrition sigenp and italian society of pediatric neurology sinp
topic Cyclic vomiting
Management
Outcomes
Pediatric
url https://doi.org/10.1186/s13052-022-01346-y
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