Co-Existence of Congenital Cystic Adenomatoid Malformation and Pulmonary Sequestration in a Newborn with Spontaneous Pneumothorax: A Case Report and Review of the Literature
Congenital bronchopulmonary malformations are uncommon anomalies of infants and children presenting as congenital lobar emphysema, bronchogenic cyst, congenital cystic adenomatoid malformation (CCAM), or pulmonary sequestration (PS). CCAM is the second most common congenital lung malformation in new...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Galenos Yayinevi
2019-06-01
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| Series: | Haseki Tıp Bülteni |
| Subjects: | |
| Online Access: |
http://www.hasekidergisi.com/archives/archive-detail/article-preview/co-existence-of-congenital-cystic-adenomatoid-malf/26219
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| Summary: | Congenital bronchopulmonary malformations are uncommon anomalies of infants and children presenting as congenital lobar emphysema, bronchogenic cyst, congenital cystic adenomatoid malformation (CCAM), or pulmonary sequestration (PS). CCAM is the second most common congenital lung malformation in newborns. There are five types of CCAM based on the embryologic and the histologic features. PS is defined as a mass of tissue developing in the lung but having no respiratory function. PS is classified into two types: extralobar and intralobar. Co-existence.of CCAM and PS is a rare occurrence. Hybrid lesions, especially type 2 CCAM and PS combination may have a more severe clinical progress. Herein, we report a male infant with type 2 CCAM in combination with PS who died despite both medical and surgical treatment. |
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| ISSN: | 1302-0072 2147-2688 |