Malignant triton tumor of the retroperitoneum: a case report and review of the literature
<p>Abstract</p> <p>Background</p> <p>Malignant triton tumors are relatively rare and highly aggressive tumors in which malignant schwannoma cells coexist with rhabdomyoblasts. Their occurrence in the retroperitoneum is uncommon and has been rarely reported.</p> &l...
| Main Authors: | , , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
BMC
2012-05-01
|
| Series: | World Journal of Surgical Oncology |
| Subjects: | |
| Online Access: | http://www.wjso.com/content/10/1/96 |
| _version_ | 1818107795783811072 |
|---|---|
| author | Li Zhiwei Xiang Jie Yan Sheng Gao Feng Zheng Shusen |
| author_facet | Li Zhiwei Xiang Jie Yan Sheng Gao Feng Zheng Shusen |
| author_sort | Li Zhiwei |
| collection | DOAJ |
| description | <p>Abstract</p> <p>Background</p> <p>Malignant triton tumors are relatively rare and highly aggressive tumors in which malignant schwannoma cells coexist with rhabdomyoblasts. Their occurrence in the retroperitoneum is uncommon and has been rarely reported.</p> <p>Case presentation</p> <p>We present the case of a patient with a retroperitoneal malignant triton tumor. A 32-year-old male was referred with epigastric pain and an abdominal mass. Computed tomography revealed a huge soft tissue retroperitoneal mass that involved adjacent organs and vessels. Complete resection was undertaken. Pathological examination confirmed the presence of a malignant triton tumor. The patient died two and a half months after surgery, as a result of local recurrence.</p> <p>Conclusion</p> <p>Malignant triton tumors are uncommon sarcomas that are associated with a high incidence of developing local recurrence and distant metastases. Immunohistochemical staining showing nerve sheath differentiation with rhabdomyoblastic cells confirms the diagnosis. Complete excision of the tumor is the most effective treatment strategy for these retroperitoneal tumors.</p> |
| first_indexed | 2024-12-11T02:05:09Z |
| format | Article |
| id | doaj.art-2b4aecd5c64b48b3b454cfc1375a6bcf |
| institution | Directory Open Access Journal |
| issn | 1477-7819 |
| language | English |
| last_indexed | 2024-12-11T02:05:09Z |
| publishDate | 2012-05-01 |
| publisher | BMC |
| record_format | Article |
| series | World Journal of Surgical Oncology |
| spelling | doaj.art-2b4aecd5c64b48b3b454cfc1375a6bcf2022-12-22T01:24:24ZengBMCWorld Journal of Surgical Oncology1477-78192012-05-011019610.1186/1477-7819-10-96Malignant triton tumor of the retroperitoneum: a case report and review of the literatureLi ZhiweiXiang JieYan ShengGao FengZheng Shusen<p>Abstract</p> <p>Background</p> <p>Malignant triton tumors are relatively rare and highly aggressive tumors in which malignant schwannoma cells coexist with rhabdomyoblasts. Their occurrence in the retroperitoneum is uncommon and has been rarely reported.</p> <p>Case presentation</p> <p>We present the case of a patient with a retroperitoneal malignant triton tumor. A 32-year-old male was referred with epigastric pain and an abdominal mass. Computed tomography revealed a huge soft tissue retroperitoneal mass that involved adjacent organs and vessels. Complete resection was undertaken. Pathological examination confirmed the presence of a malignant triton tumor. The patient died two and a half months after surgery, as a result of local recurrence.</p> <p>Conclusion</p> <p>Malignant triton tumors are uncommon sarcomas that are associated with a high incidence of developing local recurrence and distant metastases. Immunohistochemical staining showing nerve sheath differentiation with rhabdomyoblastic cells confirms the diagnosis. Complete excision of the tumor is the most effective treatment strategy for these retroperitoneal tumors.</p>http://www.wjso.com/content/10/1/96Malignant triton tumorRetroperitoneumSurgeryPrognosis |
| spellingShingle | Li Zhiwei Xiang Jie Yan Sheng Gao Feng Zheng Shusen Malignant triton tumor of the retroperitoneum: a case report and review of the literature World Journal of Surgical Oncology Malignant triton tumor Retroperitoneum Surgery Prognosis |
| title | Malignant triton tumor of the retroperitoneum: a case report and review of the literature |
| title_full | Malignant triton tumor of the retroperitoneum: a case report and review of the literature |
| title_fullStr | Malignant triton tumor of the retroperitoneum: a case report and review of the literature |
| title_full_unstemmed | Malignant triton tumor of the retroperitoneum: a case report and review of the literature |
| title_short | Malignant triton tumor of the retroperitoneum: a case report and review of the literature |
| title_sort | malignant triton tumor of the retroperitoneum a case report and review of the literature |
| topic | Malignant triton tumor Retroperitoneum Surgery Prognosis |
| url | http://www.wjso.com/content/10/1/96 |
| work_keys_str_mv | AT lizhiwei malignanttritontumoroftheretroperitoneumacasereportandreviewoftheliterature AT xiangjie malignanttritontumoroftheretroperitoneumacasereportandreviewoftheliterature AT yansheng malignanttritontumoroftheretroperitoneumacasereportandreviewoftheliterature AT gaofeng malignanttritontumoroftheretroperitoneumacasereportandreviewoftheliterature AT zhengshusen malignanttritontumoroftheretroperitoneumacasereportandreviewoftheliterature |