Hybrid treatment of fibroadipose vascular anomaly: A case report
First identified in 2014, fibroadipose vascular anomaly (FAVA) is a very rare type of venous and lymphatic malformation. Marked by tough fibrofatty tissue in the extremities overtaking portions of the muscles, it is associated with constant pain and contracture of the affected extremity. There is a...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
De Gruyter
2020-09-01
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| Series: | Open Medicine |
| Subjects: | |
| Online Access: | https://doi.org/10.1515/med-2020-0228 |
| _version_ | 1819118902346514432 |
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| author | Stillo Francesco Ruggiero Federica De Fiores Antonio Compagna Rita Amato Bruno |
| author_facet | Stillo Francesco Ruggiero Federica De Fiores Antonio Compagna Rita Amato Bruno |
| author_sort | Stillo Francesco |
| collection | DOAJ |
| description | First identified in 2014, fibroadipose vascular anomaly (FAVA) is a very rare type of venous and lymphatic malformation. Marked by tough fibrofatty tissue in the extremities overtaking portions of the muscles, it is associated with constant pain and contracture of the affected extremity. There is a paucity of literature, and no guidelines on treatment procedure are available. This case highlights the role of hybrid treatment with primary ethanol percutaneous ethanol embolization and additional surgery for radicality in excision of FAVA lesions. |
| first_indexed | 2024-12-22T05:56:15Z |
| format | Article |
| id | doaj.art-2c797e77499c440db9d862675ce54b3a |
| institution | Directory Open Access Journal |
| issn | 2391-5463 |
| language | English |
| last_indexed | 2024-12-22T05:56:15Z |
| publishDate | 2020-09-01 |
| publisher | De Gruyter |
| record_format | Article |
| series | Open Medicine |
| spelling | doaj.art-2c797e77499c440db9d862675ce54b3a2022-12-21T18:36:43ZengDe GruyterOpen Medicine2391-54632020-09-0115189089710.1515/med-2020-0228med-2020-0228Hybrid treatment of fibroadipose vascular anomaly: A case reportStillo Francesco0Ruggiero Federica1De Fiores Antonio2Compagna Rita3Amato Bruno4Vascular Malformation Unit, Department of Surgery, Istituto, Clinica Guarnieri, Via Tor de’ Schiavi, 139, 00172, Rome (RM), ItalyDepartment of Clinical and Molecular Medicine, Faculty of Medicine and Psychology, Vascular Surgery Unit, University of Rome La Sapienza, Via di Grottarossa 1035/1039, 00189Rome, ItalyVascular Malformation Unit, Department of Surgery, Istituto, Clinica Guarnieri, Via Tor de’ Schiavi, 139, 00172, Rome (RM), ItalyDepartment of Public Health, University of Naples “Federico II”, via Sergio Pansini, 5 – 80131, Naples, ItalyDepartment of Public Health, University of Naples “Federico II”, via Sergio Pansini, 5 – 80131, Naples, ItalyFirst identified in 2014, fibroadipose vascular anomaly (FAVA) is a very rare type of venous and lymphatic malformation. Marked by tough fibrofatty tissue in the extremities overtaking portions of the muscles, it is associated with constant pain and contracture of the affected extremity. There is a paucity of literature, and no guidelines on treatment procedure are available. This case highlights the role of hybrid treatment with primary ethanol percutaneous ethanol embolization and additional surgery for radicality in excision of FAVA lesions.https://doi.org/10.1515/med-2020-0228fibroadipose vascular anomalyethanol embolizationcase reportgrowth syndromespik3ca mutation |
| spellingShingle | Stillo Francesco Ruggiero Federica De Fiores Antonio Compagna Rita Amato Bruno Hybrid treatment of fibroadipose vascular anomaly: A case report Open Medicine fibroadipose vascular anomaly ethanol embolization case report growth syndromes pik3ca mutation |
| title | Hybrid treatment of fibroadipose vascular anomaly: A case report |
| title_full | Hybrid treatment of fibroadipose vascular anomaly: A case report |
| title_fullStr | Hybrid treatment of fibroadipose vascular anomaly: A case report |
| title_full_unstemmed | Hybrid treatment of fibroadipose vascular anomaly: A case report |
| title_short | Hybrid treatment of fibroadipose vascular anomaly: A case report |
| title_sort | hybrid treatment of fibroadipose vascular anomaly a case report |
| topic | fibroadipose vascular anomaly ethanol embolization case report growth syndromes pik3ca mutation |
| url | https://doi.org/10.1515/med-2020-0228 |
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