Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma
We present the case of a young male patient with an initial diagnosis of a rhabdomyoma that was surgically treated at a different hospital when he was 17. After a 2-year disease-free period, the patient presented another intra-cardiac mass. He refused surgical treatment and died 5 years later. Post-...
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| Format: | Article |
| Language: | English |
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Frontiers Media S.A.
2021-10-01
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| Series: | Frontiers in Cardiovascular Medicine |
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| Online Access: | https://www.frontiersin.org/articles/10.3389/fcvm.2021.709328/full |
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| author | Jorge Cossío-Aranda Alberto Aranda-Frausto Joaquin Berarducci Nilda Espinola-Zavaleta Laila González-Melchor Clara Vázquez-Antona Gabriela Meléndez-Ramirez Javier Ivan Armenta-Moreno Candace Keirns |
| author_facet | Jorge Cossío-Aranda Alberto Aranda-Frausto Joaquin Berarducci Nilda Espinola-Zavaleta Laila González-Melchor Clara Vázquez-Antona Gabriela Meléndez-Ramirez Javier Ivan Armenta-Moreno Candace Keirns |
| author_sort | Jorge Cossío-Aranda |
| collection | DOAJ |
| description | We present the case of a young male patient with an initial diagnosis of a rhabdomyoma that was surgically treated at a different hospital when he was 17. After a 2-year disease-free period, the patient presented another intra-cardiac mass. He refused surgical treatment and died 5 years later. Post-mortem immunochemistry studies of both tumors led to the diagnosis of a primary malignant cardiac PEComa with histopathologic characteristics that resembled a rhabdomyoma with abundant “spider cells.” |
| first_indexed | 2024-12-21T05:38:36Z |
| format | Article |
| id | doaj.art-2c8ff36263d14bf19eef79632e57b70d |
| institution | Directory Open Access Journal |
| issn | 2297-055X |
| language | English |
| last_indexed | 2024-12-21T05:38:36Z |
| publishDate | 2021-10-01 |
| publisher | Frontiers Media S.A. |
| record_format | Article |
| series | Frontiers in Cardiovascular Medicine |
| spelling | doaj.art-2c8ff36263d14bf19eef79632e57b70d2022-12-21T19:14:20ZengFrontiers Media S.A.Frontiers in Cardiovascular Medicine2297-055X2021-10-01810.3389/fcvm.2021.709328709328Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac RhabdomyomaJorge Cossío-Aranda0Alberto Aranda-Frausto1Joaquin Berarducci2Nilda Espinola-Zavaleta3Laila González-Melchor4Clara Vázquez-Antona5Gabriela Meléndez-Ramirez6Javier Ivan Armenta-Moreno7Candace Keirns8Instituto Nacional de Cardiología Ignacio Chávez, Mexico City, MexicoInstituto Nacional de Cardiología Ignacio Chávez, Mexico City, MexicoInstituto Nacional de Cardiología Ignacio Chávez, Mexico City, MexicoInstituto Nacional de Cardiología Ignacio Chávez, Mexico City, MexicoInstituto Nacional de Cardiología Ignacio Chávez, Mexico City, MexicoInstituto Nacional de Cardiología Ignacio Chávez, Mexico City, MexicoInstituto Nacional de Cardiología Ignacio Chávez, Mexico City, MexicoInstituto Nacional de Cardiología Ignacio Chávez, Mexico City, MexicoInternational Medical Interpreters Association, Boston, MA, United StatesWe present the case of a young male patient with an initial diagnosis of a rhabdomyoma that was surgically treated at a different hospital when he was 17. After a 2-year disease-free period, the patient presented another intra-cardiac mass. He refused surgical treatment and died 5 years later. Post-mortem immunochemistry studies of both tumors led to the diagnosis of a primary malignant cardiac PEComa with histopathologic characteristics that resembled a rhabdomyoma with abundant “spider cells.”https://www.frontiersin.org/articles/10.3389/fcvm.2021.709328/fullcardiac tumorPEComaperivascular epithelioid cell neoplasmrhabdomyoma of heartarrhythmiacardiooncology |
| spellingShingle | Jorge Cossío-Aranda Alberto Aranda-Frausto Joaquin Berarducci Nilda Espinola-Zavaleta Laila González-Melchor Clara Vázquez-Antona Gabriela Meléndez-Ramirez Javier Ivan Armenta-Moreno Candace Keirns Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma Frontiers in Cardiovascular Medicine cardiac tumor PEComa perivascular epithelioid cell neoplasm rhabdomyoma of heart arrhythmia cardiooncology |
| title | Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma |
| title_full | Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma |
| title_fullStr | Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma |
| title_full_unstemmed | Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma |
| title_short | Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma |
| title_sort | case report a rare case of a ventricular perivascular epithelioid cell tumor with histologic characteristics that resembled a primary cardiac rhabdomyoma |
| topic | cardiac tumor PEComa perivascular epithelioid cell neoplasm rhabdomyoma of heart arrhythmia cardiooncology |
| url | https://www.frontiersin.org/articles/10.3389/fcvm.2021.709328/full |
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