Acral pseudolymphomatous angiokeratoma: case report and literature review
The authors describe a case of a female patient with Acral Pseudolymphomatous Angiokeratoma of Children, known as APACHE. It is a rare benign cutaneous disease, of unknown etiology, characterized by multiple, asymptomatic erythematous-violaceous papules and nodules, usually located unilaterally with...
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Format: | Article |
Language: | English |
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Sociedade Brasileira de Dermatologia
2013-12-01
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Series: | Anais Brasileiros de Dermatologia |
Subjects: | |
Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000800039&tlng=en |
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author | Priscila Pacheco Lessa Juliana Chaib Ferreira Jorge Flávia Regina Ferreira Marcia Lanzoni de Alvarenga Lira Samuel Henrique Mandelbaum |
author_facet | Priscila Pacheco Lessa Juliana Chaib Ferreira Jorge Flávia Regina Ferreira Marcia Lanzoni de Alvarenga Lira Samuel Henrique Mandelbaum |
author_sort | Priscila Pacheco Lessa |
collection | DOAJ |
description | The authors describe a case of a female patient with Acral Pseudolymphomatous Angiokeratoma of Children, known as APACHE. It is a rare benign cutaneous disease, of unknown etiology, characterized by multiple, asymptomatic erythematous-violaceous papules and nodules, usually located unilaterally with acral distribution. Today, this denomination is questionable, since there are published reports of this disease in adults and in different locations. Clinically, it is similar to an angiokeratoma, whereas hystologically, it corresponds to a distinct type of pseudolymphoma. The immunohistochemical study is required to distinguish APACHE from cutaneous lymphoma. |
first_indexed | 2024-12-17T20:06:05Z |
format | Article |
id | doaj.art-2d13c6b78db44ea19e43f80a7c16a797 |
institution | Directory Open Access Journal |
issn | 0365-0596 |
language | English |
last_indexed | 2024-12-17T20:06:05Z |
publishDate | 2013-12-01 |
publisher | Sociedade Brasileira de Dermatologia |
record_format | Article |
series | Anais Brasileiros de Dermatologia |
spelling | doaj.art-2d13c6b78db44ea19e43f80a7c16a7972022-12-21T21:34:19ZengSociedade Brasileira de DermatologiaAnais Brasileiros de Dermatologia0365-05962013-12-01886 suppl 1394310.1590/abd1806-4841.20132413Acral pseudolymphomatous angiokeratoma: case report and literature reviewPriscila Pacheco LessaJuliana Chaib Ferreira JorgeFlávia Regina FerreiraMarcia Lanzoni de Alvarenga LiraSamuel Henrique MandelbaumThe authors describe a case of a female patient with Acral Pseudolymphomatous Angiokeratoma of Children, known as APACHE. It is a rare benign cutaneous disease, of unknown etiology, characterized by multiple, asymptomatic erythematous-violaceous papules and nodules, usually located unilaterally with acral distribution. Today, this denomination is questionable, since there are published reports of this disease in adults and in different locations. Clinically, it is similar to an angiokeratoma, whereas hystologically, it corresponds to a distinct type of pseudolymphoma. The immunohistochemical study is required to distinguish APACHE from cutaneous lymphoma.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000800039&tlng=enChildExtremitiesHemangiomaPseudolymphoma |
spellingShingle | Priscila Pacheco Lessa Juliana Chaib Ferreira Jorge Flávia Regina Ferreira Marcia Lanzoni de Alvarenga Lira Samuel Henrique Mandelbaum Acral pseudolymphomatous angiokeratoma: case report and literature review Anais Brasileiros de Dermatologia Child Extremities Hemangioma Pseudolymphoma |
title | Acral pseudolymphomatous angiokeratoma: case report and literature review |
title_full | Acral pseudolymphomatous angiokeratoma: case report and literature review |
title_fullStr | Acral pseudolymphomatous angiokeratoma: case report and literature review |
title_full_unstemmed | Acral pseudolymphomatous angiokeratoma: case report and literature review |
title_short | Acral pseudolymphomatous angiokeratoma: case report and literature review |
title_sort | acral pseudolymphomatous angiokeratoma case report and literature review |
topic | Child Extremities Hemangioma Pseudolymphoma |
url | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000800039&tlng=en |
work_keys_str_mv | AT priscilapachecolessa acralpseudolymphomatousangiokeratomacasereportandliteraturereview AT julianachaibferreirajorge acralpseudolymphomatousangiokeratomacasereportandliteraturereview AT flaviareginaferreira acralpseudolymphomatousangiokeratomacasereportandliteraturereview AT marcialanzonidealvarengalira acralpseudolymphomatousangiokeratomacasereportandliteraturereview AT samuelhenriquemandelbaum acralpseudolymphomatousangiokeratomacasereportandliteraturereview |