Multilocular cystic renal cell carcinoma in a 23 year old female

Multilocular cystic renal cell carcinoma (MCRCC) has been identified as a separate subtype of renal cell carcinoma (RCC) in the 2004 World Health Organization classification of adult renal tumors. MCRCC represents a rare variant of clear cell RCC. The common age group for this tumor is between 40 an...

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Main Authors: Shivakumarswamy Udasimath, J Niranjan, R Puruhotham, K R Nagesha
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2016-01-01
Series:Urology Annals
Subjects:
Online Access:http://www.urologyannals.com/article.asp?issn=0974-7796;year=2016;volume=8;issue=4;spage=506;epage=508;aulast=Udasimath
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author Shivakumarswamy Udasimath
J Niranjan
R Puruhotham
K R Nagesha
author_facet Shivakumarswamy Udasimath
J Niranjan
R Puruhotham
K R Nagesha
author_sort Shivakumarswamy Udasimath
collection DOAJ
description Multilocular cystic renal cell carcinoma (MCRCC) has been identified as a separate subtype of renal cell carcinoma (RCC) in the 2004 World Health Organization classification of adult renal tumors. MCRCC represents a rare variant of clear cell RCC. The common age group for this tumor is between 40 and 60 years. In our case, MCRCC occurred at the age of 23 years in a female patient. We report this case because of its rarity in this age group, sex, good prognosis, and also to avoid a misdiagnosis as conventional clear cell RCC. However, before making a diagnosis of MCRCC, it has to be differentiated from tubulocystic carcinoma, cystic nephroma, cystic clear cell carcinoma, and clear cell papillary RCC.
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spelling doaj.art-2d3a3a09c7694d06a45cb04a4bc18a842022-12-22T02:54:32ZengWolters Kluwer Medknow PublicationsUrology Annals0974-77960974-78342016-01-018450650810.4103/0974-7796.192095Multilocular cystic renal cell carcinoma in a 23 year old femaleShivakumarswamy UdasimathJ NiranjanR PuruhothamK R NageshaMultilocular cystic renal cell carcinoma (MCRCC) has been identified as a separate subtype of renal cell carcinoma (RCC) in the 2004 World Health Organization classification of adult renal tumors. MCRCC represents a rare variant of clear cell RCC. The common age group for this tumor is between 40 and 60 years. In our case, MCRCC occurred at the age of 23 years in a female patient. We report this case because of its rarity in this age group, sex, good prognosis, and also to avoid a misdiagnosis as conventional clear cell RCC. However, before making a diagnosis of MCRCC, it has to be differentiated from tubulocystic carcinoma, cystic nephroma, cystic clear cell carcinoma, and clear cell papillary RCC.http://www.urologyannals.com/article.asp?issn=0974-7796;year=2016;volume=8;issue=4;spage=506;epage=508;aulast=UdasimathClear cell renal cell carcinomakidneymultilocular cystic renal cell carcinoma
spellingShingle Shivakumarswamy Udasimath
J Niranjan
R Puruhotham
K R Nagesha
Multilocular cystic renal cell carcinoma in a 23 year old female
Urology Annals
Clear cell renal cell carcinoma
kidney
multilocular cystic renal cell carcinoma
title Multilocular cystic renal cell carcinoma in a 23 year old female
title_full Multilocular cystic renal cell carcinoma in a 23 year old female
title_fullStr Multilocular cystic renal cell carcinoma in a 23 year old female
title_full_unstemmed Multilocular cystic renal cell carcinoma in a 23 year old female
title_short Multilocular cystic renal cell carcinoma in a 23 year old female
title_sort multilocular cystic renal cell carcinoma in a 23 year old female
topic Clear cell renal cell carcinoma
kidney
multilocular cystic renal cell carcinoma
url http://www.urologyannals.com/article.asp?issn=0974-7796;year=2016;volume=8;issue=4;spage=506;epage=508;aulast=Udasimath
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AT jniranjan multilocularcysticrenalcellcarcinomaina23yearoldfemale
AT rpuruhotham multilocularcysticrenalcellcarcinomaina23yearoldfemale
AT krnagesha multilocularcysticrenalcellcarcinomaina23yearoldfemale