A rare case of hemophagocytic lymphohistiocytosis associated with sarcoidosis

Sarcoidosis is a chronic granulomatous disorder often misdiagnosed as tuberculosis. Hemophagocytic lymphohistiocytosis (HLH) is a potentially fatal complication linked to extensive hemophagocytosis and hyperinflammatory response. Cases of sarcoidosis developing HLH are rarely documented and difficul...

Full description

Bibliographic Details
Main Authors: Vikas Marwah, Nikhil Kumar, Robin Choudhary, Deepti Mutreja, Anmol Sharma
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2023-01-01
Series:Journal of Advanced Lung Health
Subjects:
Online Access:http://www.jalh.org/article.asp?issn=2772-7165;year=2023;volume=3;issue=3;spage=125;epage=127;aulast=Marwah
_version_ 1797738645466120192
author Vikas Marwah
Nikhil Kumar
Robin Choudhary
Deepti Mutreja
Anmol Sharma
author_facet Vikas Marwah
Nikhil Kumar
Robin Choudhary
Deepti Mutreja
Anmol Sharma
author_sort Vikas Marwah
collection DOAJ
description Sarcoidosis is a chronic granulomatous disorder often misdiagnosed as tuberculosis. Hemophagocytic lymphohistiocytosis (HLH) is a potentially fatal complication linked to extensive hemophagocytosis and hyperinflammatory response. Cases of sarcoidosis developing HLH are rarely documented and difficult to diagnose. We present the case of a 63-year-old female with sarcoidosis complicated with HLH, successfully managed at our center.
first_indexed 2024-03-12T13:46:50Z
format Article
id doaj.art-2d45f71b25324caf9590e28ba56eba11
institution Directory Open Access Journal
issn 2772-7165
2772-7173
language English
last_indexed 2024-03-12T13:46:50Z
publishDate 2023-01-01
publisher Wolters Kluwer Medknow Publications
record_format Article
series Journal of Advanced Lung Health
spelling doaj.art-2d45f71b25324caf9590e28ba56eba112023-08-23T08:56:11ZengWolters Kluwer Medknow PublicationsJournal of Advanced Lung Health2772-71652772-71732023-01-013312512710.4103/jalh.jalh_8_23A rare case of hemophagocytic lymphohistiocytosis associated with sarcoidosisVikas MarwahNikhil KumarRobin ChoudharyDeepti MutrejaAnmol SharmaSarcoidosis is a chronic granulomatous disorder often misdiagnosed as tuberculosis. Hemophagocytic lymphohistiocytosis (HLH) is a potentially fatal complication linked to extensive hemophagocytosis and hyperinflammatory response. Cases of sarcoidosis developing HLH are rarely documented and difficult to diagnose. We present the case of a 63-year-old female with sarcoidosis complicated with HLH, successfully managed at our center.http://www.jalh.org/article.asp?issn=2772-7165;year=2023;volume=3;issue=3;spage=125;epage=127;aulast=Marwahcorticosteroidshemophagocytic lymphohistiocytosismacrophage activation syndromesarcoidosis
spellingShingle Vikas Marwah
Nikhil Kumar
Robin Choudhary
Deepti Mutreja
Anmol Sharma
A rare case of hemophagocytic lymphohistiocytosis associated with sarcoidosis
Journal of Advanced Lung Health
corticosteroids
hemophagocytic lymphohistiocytosis
macrophage activation syndrome
sarcoidosis
title A rare case of hemophagocytic lymphohistiocytosis associated with sarcoidosis
title_full A rare case of hemophagocytic lymphohistiocytosis associated with sarcoidosis
title_fullStr A rare case of hemophagocytic lymphohistiocytosis associated with sarcoidosis
title_full_unstemmed A rare case of hemophagocytic lymphohistiocytosis associated with sarcoidosis
title_short A rare case of hemophagocytic lymphohistiocytosis associated with sarcoidosis
title_sort rare case of hemophagocytic lymphohistiocytosis associated with sarcoidosis
topic corticosteroids
hemophagocytic lymphohistiocytosis
macrophage activation syndrome
sarcoidosis
url http://www.jalh.org/article.asp?issn=2772-7165;year=2023;volume=3;issue=3;spage=125;epage=127;aulast=Marwah
work_keys_str_mv AT vikasmarwah ararecaseofhemophagocyticlymphohistiocytosisassociatedwithsarcoidosis
AT nikhilkumar ararecaseofhemophagocyticlymphohistiocytosisassociatedwithsarcoidosis
AT robinchoudhary ararecaseofhemophagocyticlymphohistiocytosisassociatedwithsarcoidosis
AT deeptimutreja ararecaseofhemophagocyticlymphohistiocytosisassociatedwithsarcoidosis
AT anmolsharma ararecaseofhemophagocyticlymphohistiocytosisassociatedwithsarcoidosis
AT vikasmarwah rarecaseofhemophagocyticlymphohistiocytosisassociatedwithsarcoidosis
AT nikhilkumar rarecaseofhemophagocyticlymphohistiocytosisassociatedwithsarcoidosis
AT robinchoudhary rarecaseofhemophagocyticlymphohistiocytosisassociatedwithsarcoidosis
AT deeptimutreja rarecaseofhemophagocyticlymphohistiocytosisassociatedwithsarcoidosis
AT anmolsharma rarecaseofhemophagocyticlymphohistiocytosisassociatedwithsarcoidosis