Double trouble: Bilateral cerebral involvement in Sturge-Weber syndrome
Sturge-Weber syndrome, also known as encephalotrigeminal angiomatosis or meningofacial angiomatosis, is characterised in its classical form by a congenital, usually unilateral, ‘portwine stain’ (capillary naevus) on the face, convulsions, typical intracranial calcification and some degree of mental...
| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
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AOSIS
2015-08-01
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| Series: | South African Journal of Radiology |
| Online Access: | https://sajr.org.za/index.php/sajr/article/view/760 |
| _version_ | 1828836827955462144 |
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| author | Narosha Adroos Janet Smal Farhana E. Suleman |
| author_facet | Narosha Adroos Janet Smal Farhana E. Suleman |
| author_sort | Narosha Adroos |
| collection | DOAJ |
| description | Sturge-Weber syndrome, also known as encephalotrigeminal angiomatosis or meningofacial angiomatosis, is characterised in its classical form by a congenital, usually unilateral, ‘portwine stain’ (capillary naevus) on the face, convulsions, typical intracranial calcification and some degree of mental retardation and hemiparesis. The clinical correlation of intractable seizures with the presence of bilateral intracranial disease has management and prognostic implications, thus making the presence of bilateral disease an important factor to all those involved in the management of the child with Sturge-Weber syndrome. |
| first_indexed | 2024-12-12T18:30:14Z |
| format | Article |
| id | doaj.art-2dda11dc34f5453592028ddf6a7d4fa9 |
| institution | Directory Open Access Journal |
| issn | 1027-202X 2078-6778 |
| language | English |
| last_indexed | 2024-12-12T18:30:14Z |
| publishDate | 2015-08-01 |
| publisher | AOSIS |
| record_format | Article |
| series | South African Journal of Radiology |
| spelling | doaj.art-2dda11dc34f5453592028ddf6a7d4fa92022-12-22T00:15:57ZengAOSISSouth African Journal of Radiology1027-202X2078-67782015-08-01191e1e410.4102/sajr.v19i1.760632Double trouble: Bilateral cerebral involvement in Sturge-Weber syndromeNarosha Adroos0Janet Smal1Farhana E. Suleman2Department of Radiology, University of PretoriaDepartment of Radiology, University of PretoriaDepartment of Radiology, University of PretoriaSturge-Weber syndrome, also known as encephalotrigeminal angiomatosis or meningofacial angiomatosis, is characterised in its classical form by a congenital, usually unilateral, ‘portwine stain’ (capillary naevus) on the face, convulsions, typical intracranial calcification and some degree of mental retardation and hemiparesis. The clinical correlation of intractable seizures with the presence of bilateral intracranial disease has management and prognostic implications, thus making the presence of bilateral disease an important factor to all those involved in the management of the child with Sturge-Weber syndrome.https://sajr.org.za/index.php/sajr/article/view/760 |
| spellingShingle | Narosha Adroos Janet Smal Farhana E. Suleman Double trouble: Bilateral cerebral involvement in Sturge-Weber syndrome South African Journal of Radiology |
| title | Double trouble: Bilateral cerebral involvement in Sturge-Weber syndrome |
| title_full | Double trouble: Bilateral cerebral involvement in Sturge-Weber syndrome |
| title_fullStr | Double trouble: Bilateral cerebral involvement in Sturge-Weber syndrome |
| title_full_unstemmed | Double trouble: Bilateral cerebral involvement in Sturge-Weber syndrome |
| title_short | Double trouble: Bilateral cerebral involvement in Sturge-Weber syndrome |
| title_sort | double trouble bilateral cerebral involvement in sturge weber syndrome |
| url | https://sajr.org.za/index.php/sajr/article/view/760 |
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