Extraglandular orbital adenoid cystic carcinoma

Adenoid Cystic Carcinoma (ACC) is an uncommon malignancy and it's orbital primary presentation with no glandular involvement is exceedingly rare. However, ACC must be considered in the diagnosis of an orbital tumor, since complications such as intracranial spread and recurrence are often descri...

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Main Authors: Sami Elhamid, Bahaa Razem, Faiçal Slimani
Format: Article
Language:English
Published: Elsevier 2022-10-01
Series:Advances in Oral and Maxillofacial Surgery
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2667147622000796
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author Sami Elhamid
Bahaa Razem
Faiçal Slimani
author_facet Sami Elhamid
Bahaa Razem
Faiçal Slimani
author_sort Sami Elhamid
collection DOAJ
description Adenoid Cystic Carcinoma (ACC) is an uncommon malignancy and it's orbital primary presentation with no glandular involvement is exceedingly rare. However, ACC must be considered in the diagnosis of an orbital tumor, since complications such as intracranial spread and recurrence are often described. We present a case of primary orbital ACC treated with surgical excision and the outcome of a long term follow-up in the light of a litterature review.
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spelling doaj.art-2e16b63558244d4c9df7ff37e924b0a62022-12-22T04:23:57ZengElsevierAdvances in Oral and Maxillofacial Surgery2667-14762022-10-018100329Extraglandular orbital adenoid cystic carcinomaSami Elhamid0Bahaa Razem1Faiçal Slimani2Oral and Maxillofacial Surgery Department, CHUN Ibn Rochd: Centre Hospitalier Universitaire Ibn Rochd, Casablanca, Morocco; Corresponding author.Oral and Maxillofacial Surgery Department, CHUN Ibn Rochd: Centre Hospitalier Universitaire Ibn Rochd, Casablanca, MoroccoOral and Maxillofacial Surgery Department, CHUN Ibn Rochd: Centre Hospitalier Universitaire Ibn Rochd, Casablanca, Morocco; Hassan II University of Casablanca, Casablanca, MoroccoAdenoid Cystic Carcinoma (ACC) is an uncommon malignancy and it's orbital primary presentation with no glandular involvement is exceedingly rare. However, ACC must be considered in the diagnosis of an orbital tumor, since complications such as intracranial spread and recurrence are often described. We present a case of primary orbital ACC treated with surgical excision and the outcome of a long term follow-up in the light of a litterature review.http://www.sciencedirect.com/science/article/pii/S2667147622000796OrbitalAdenoid cystic carcinomaFollow-upPrimary
spellingShingle Sami Elhamid
Bahaa Razem
Faiçal Slimani
Extraglandular orbital adenoid cystic carcinoma
Advances in Oral and Maxillofacial Surgery
Orbital
Adenoid cystic carcinoma
Follow-up
Primary
title Extraglandular orbital adenoid cystic carcinoma
title_full Extraglandular orbital adenoid cystic carcinoma
title_fullStr Extraglandular orbital adenoid cystic carcinoma
title_full_unstemmed Extraglandular orbital adenoid cystic carcinoma
title_short Extraglandular orbital adenoid cystic carcinoma
title_sort extraglandular orbital adenoid cystic carcinoma
topic Orbital
Adenoid cystic carcinoma
Follow-up
Primary
url http://www.sciencedirect.com/science/article/pii/S2667147622000796
work_keys_str_mv AT samielhamid extraglandularorbitaladenoidcysticcarcinoma
AT bahaarazem extraglandularorbitaladenoidcysticcarcinoma
AT faicalslimani extraglandularorbitaladenoidcysticcarcinoma