Extremities Soft Tissue Sarcomas, more Common and as Dangerous as Bone Sarcomas
Abstract Musculoskeletal sarcomas are rare diseases that require attention. They often present high degree of malignancy at diagnosis and, if underestimated, they can evolve aggressively locally and systemically. They present as soft tissues arcoma and bone sarcomas, with soft tissue being four to f...
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| Format: | Article |
| Language: | English |
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Sociedade Brasileira de Ortopedia e Traumatologia
2020-09-01
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| Series: | Revista Brasileira de Ortopedia |
| Subjects: | |
| Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0102-36162021000400419&tlng=pt |
| _version_ | 1797335307876564992 |
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| author | Karen Voltan André Mathias Baptista Maurício Etchebehere |
| author_facet | Karen Voltan André Mathias Baptista Maurício Etchebehere |
| author_sort | Karen Voltan |
| collection | DOAJ |
| description | Abstract Musculoskeletal sarcomas are rare diseases that require attention. They often present high degree of malignancy at diagnosis and, if underestimated, they can evolve aggressively locally and systemically. They present as soft tissues arcoma and bone sarcomas, with soft tissue being four to five times more common. Most soft tissue sarcomas occur in the extremities. The most common subtypes in children and adolescents are rhabdomyosarcoma and synovial sarcoma; in adults, undifferentiated pleomorphic sarcoma, liposarcoma, leiomyosarcoma, myxofibrosarcoma and synovial sarcoma; all with a high degree of histological malignancy. Many soft tissue sarcomas are confused with benign soft tissue tumors, 100 times more common, so they are resected without the necessary planning, resulting in amputation of a limb that could have been preserved. As in all cancers, the most important prognostic factor is metastatic disease. When it is present, the overall survival rate falls around 20 to 30%. Survival rates are generally similar between bone and soft tissue sarcomas. So soft tissue sarcomas, in addition to being more prevalent, are as aggressive as bones arcomas, deserving a lot of attention from orthopedic surgeons, who are often the first line of care of carriers of these tumors. |
| first_indexed | 2024-03-08T08:36:10Z |
| format | Article |
| id | doaj.art-2f45dfe09628489cbc8dbfbf9821d39e |
| institution | Directory Open Access Journal |
| issn | 1982-4378 |
| language | English |
| last_indexed | 2024-03-08T08:36:10Z |
| publishDate | 2020-09-01 |
| publisher | Sociedade Brasileira de Ortopedia e Traumatologia |
| record_format | Article |
| series | Revista Brasileira de Ortopedia |
| spelling | doaj.art-2f45dfe09628489cbc8dbfbf9821d39e2024-02-02T01:16:59ZengSociedade Brasileira de Ortopedia e TraumatologiaRevista Brasileira de Ortopedia1982-43782020-09-0156441942410.1055/s-0040-1712136Extremities Soft Tissue Sarcomas, more Common and as Dangerous as Bone SarcomasKaren Voltanhttps://orcid.org/0000-0001-5025-0823André Mathias Baptistahttps://orcid.org/0000-0002-0830-4602Maurício Etchebeherehttps://orcid.org/0000-0002-5176-2369Abstract Musculoskeletal sarcomas are rare diseases that require attention. They often present high degree of malignancy at diagnosis and, if underestimated, they can evolve aggressively locally and systemically. They present as soft tissues arcoma and bone sarcomas, with soft tissue being four to five times more common. Most soft tissue sarcomas occur in the extremities. The most common subtypes in children and adolescents are rhabdomyosarcoma and synovial sarcoma; in adults, undifferentiated pleomorphic sarcoma, liposarcoma, leiomyosarcoma, myxofibrosarcoma and synovial sarcoma; all with a high degree of histological malignancy. Many soft tissue sarcomas are confused with benign soft tissue tumors, 100 times more common, so they are resected without the necessary planning, resulting in amputation of a limb that could have been preserved. As in all cancers, the most important prognostic factor is metastatic disease. When it is present, the overall survival rate falls around 20 to 30%. Survival rates are generally similar between bone and soft tissue sarcomas. So soft tissue sarcomas, in addition to being more prevalent, are as aggressive as bones arcomas, deserving a lot of attention from orthopedic surgeons, who are often the first line of care of carriers of these tumors.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0102-36162021000400419&tlng=ptepidemiologyearly detection of cancermetastasisneoplasmbone tissueprognostic factorssoft tissue sarcoma |
| spellingShingle | Karen Voltan André Mathias Baptista Maurício Etchebehere Extremities Soft Tissue Sarcomas, more Common and as Dangerous as Bone Sarcomas Revista Brasileira de Ortopedia epidemiology early detection of cancer metastasis neoplasm bone tissue prognostic factors soft tissue sarcoma |
| title | Extremities Soft Tissue Sarcomas, more Common and as Dangerous as Bone Sarcomas |
| title_full | Extremities Soft Tissue Sarcomas, more Common and as Dangerous as Bone Sarcomas |
| title_fullStr | Extremities Soft Tissue Sarcomas, more Common and as Dangerous as Bone Sarcomas |
| title_full_unstemmed | Extremities Soft Tissue Sarcomas, more Common and as Dangerous as Bone Sarcomas |
| title_short | Extremities Soft Tissue Sarcomas, more Common and as Dangerous as Bone Sarcomas |
| title_sort | extremities soft tissue sarcomas more common and as dangerous as bone sarcomas |
| topic | epidemiology early detection of cancer metastasis neoplasm bone tissue prognostic factors soft tissue sarcoma |
| url | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0102-36162021000400419&tlng=pt |
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