Displasia renal: revisão clínico-patológica.
Histology records from 63 nephrectomies were reviewed; 22 patients had unilateral totally dysplastic kidneys and 5 had polar or segmental dysplasia. A clinicopathological study of these cases was undertaken. In the first group, there was a slight male preponderance and 75% of the patients presented...
| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
| Published: |
Ordem dos Médicos
1992-05-01
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| Series: | Acta Médica Portuguesa |
| Online Access: | https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/3237 |
| _version_ | 1811242489658474496 |
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| author | A S Cunha J F de Sousa C Garcia |
| author_facet | A S Cunha J F de Sousa C Garcia |
| author_sort | A S Cunha |
| collection | DOAJ |
| description | Histology records from 63 nephrectomies were reviewed; 22 patients had unilateral totally dysplastic kidneys and 5 had polar or segmental dysplasia. A clinicopathological study of these cases was undertaken. In the first group, there was a slight male preponderance and 75% of the patients presented were under two years of age. Urinary tract infection was the most common complaint. 4 patients were diagnosed in utero by ultrasound and 5 infants presented an abdominal mass. Hypertension was documented in a newborn baby. Ipsilateral lower urinary tract anomalies were found in 12 patients and those of the contralateral kidney in 2 children. There were 3 cases of extrarenal anomalies. Histological examination revealed 13 cases of multicystic dysplasia and 9 of solid dysplasia. Metaplastic cartilage was found in 1 case. In the group of segmental dysplasia, age ranging from 27 weeks' gestation to 8 years, at the time of the diagnosis. They all had duplex kidneys and 4 had ureterocele. Histological study in these cases was similar to the one found in the previous series, although superimposed inflammatory changes were more pronounced. Some of the theories regarding the pathogenesis of this disorder are reviewed and the importance of its diagnosis is emphasised. |
| first_indexed | 2024-04-12T13:51:54Z |
| format | Article |
| id | doaj.art-2fa933f04956427eafe85833815769e0 |
| institution | Directory Open Access Journal |
| issn | 0870-399X 1646-0758 |
| language | English |
| last_indexed | 2024-04-12T13:51:54Z |
| publishDate | 1992-05-01 |
| publisher | Ordem dos Médicos |
| record_format | Article |
| series | Acta Médica Portuguesa |
| spelling | doaj.art-2fa933f04956427eafe85833815769e02022-12-22T03:30:29ZengOrdem dos MédicosActa Médica Portuguesa0870-399X1646-07581992-05-015510.20344/amp.3237Displasia renal: revisão clínico-patológica.A S Cunha0J F de SousaC GarciaLaboratório de Anatomia Patológica, Escola Superior de Medicina Dentária de Lisboa, Hospital de D. Estefânia.Histology records from 63 nephrectomies were reviewed; 22 patients had unilateral totally dysplastic kidneys and 5 had polar or segmental dysplasia. A clinicopathological study of these cases was undertaken. In the first group, there was a slight male preponderance and 75% of the patients presented were under two years of age. Urinary tract infection was the most common complaint. 4 patients were diagnosed in utero by ultrasound and 5 infants presented an abdominal mass. Hypertension was documented in a newborn baby. Ipsilateral lower urinary tract anomalies were found in 12 patients and those of the contralateral kidney in 2 children. There were 3 cases of extrarenal anomalies. Histological examination revealed 13 cases of multicystic dysplasia and 9 of solid dysplasia. Metaplastic cartilage was found in 1 case. In the group of segmental dysplasia, age ranging from 27 weeks' gestation to 8 years, at the time of the diagnosis. They all had duplex kidneys and 4 had ureterocele. Histological study in these cases was similar to the one found in the previous series, although superimposed inflammatory changes were more pronounced. Some of the theories regarding the pathogenesis of this disorder are reviewed and the importance of its diagnosis is emphasised.https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/3237 |
| spellingShingle | A S Cunha J F de Sousa C Garcia Displasia renal: revisão clínico-patológica. Acta Médica Portuguesa |
| title | Displasia renal: revisão clínico-patológica. |
| title_full | Displasia renal: revisão clínico-patológica. |
| title_fullStr | Displasia renal: revisão clínico-patológica. |
| title_full_unstemmed | Displasia renal: revisão clínico-patológica. |
| title_short | Displasia renal: revisão clínico-patológica. |
| title_sort | displasia renal revisao clinico patologica |
| url | https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/3237 |
| work_keys_str_mv | AT ascunha displasiarenalrevisaoclinicopatologica AT jfdesousa displasiarenalrevisaoclinicopatologica AT cgarcia displasiarenalrevisaoclinicopatologica |