Primary Ewing’s Sarcoma of the Spine: About a Case
Ewing’s sarcoma is a primary malignant bone tumor affecting individuals in the second decade of life. Primary sarcomas of the spine are rare and the occurrence of primary Ewing’s sarcoma in the spine is very rare. There are 2 types of Ewing’s sarcoma of the spine, Ewing’s sarcoma of the sacral spine...
| Main Authors: | , , , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
SAGE Publishing
2022-10-01
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| Series: | Global Pediatric Health |
| Online Access: | https://doi.org/10.1177/2333794X221123874 |
| _version_ | 1811224117475540992 |
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| author | Amine Cherraqi MD Abir Lemrabet MD Ibrahima Diallo Dokal MD Najlae Lrhorfi MD Hicham Belghiti MD Nazik Allali PhD Latifa Chat PhD |
| author_facet | Amine Cherraqi MD Abir Lemrabet MD Ibrahima Diallo Dokal MD Najlae Lrhorfi MD Hicham Belghiti MD Nazik Allali PhD Latifa Chat PhD |
| author_sort | Amine Cherraqi MD |
| collection | DOAJ |
| description | Ewing’s sarcoma is a primary malignant bone tumor affecting individuals in the second decade of life. Primary sarcomas of the spine are rare and the occurrence of primary Ewing’s sarcoma in the spine is very rare. There are 2 types of Ewing’s sarcoma of the spine, Ewing’s sarcoma of the sacral spine which is very aggressive with a poor prognosis and Ewing’s sarcoma of the non-sacral spine which is an extremely rare occurrence. The patient may have a neurological deficit when the tumor extends into the spinal canal, causing compression of the spinal cord. Magnetic resonance imaging (MRI) is very sensitive in diagnosing the tumor and Evaluation of the extent of the tumor. Here, we report the case of a 12-year-old boy who presented with low back pain, weakness of both lower limbs and bilateral spastic paraplegia progressively evolving since 1 month. The CT and MRI scans showed the presence of a tissue lesion process centered on the vertebral body of L1, heterogeneously enhanced after injection of Gadolinium respecting the posterior arch, without bulging of the posterior wall with epiduritis, endocanal extension and spinal cord compression. The patient underwent decompression with surgical biopsy and posterior stabilization of the spine. Histopathology and immunohistochemistry studies confirmed the diagnosis of Ewing’s sarcoma and the patient was referred to an oncopediatric center for combined chemotherapy and radiotherapy, but died at home a few days later before the start of treatment. |
| first_indexed | 2024-04-12T08:44:50Z |
| format | Article |
| id | doaj.art-2fc8606674874fc1884c5f8426663066 |
| institution | Directory Open Access Journal |
| issn | 2333-794X |
| language | English |
| last_indexed | 2024-04-12T08:44:50Z |
| publishDate | 2022-10-01 |
| publisher | SAGE Publishing |
| record_format | Article |
| series | Global Pediatric Health |
| spelling | doaj.art-2fc8606674874fc1884c5f84266630662022-12-22T03:39:45ZengSAGE PublishingGlobal Pediatric Health2333-794X2022-10-01910.1177/2333794X221123874Primary Ewing’s Sarcoma of the Spine: About a CaseAmine Cherraqi MD0Abir Lemrabet MD1Ibrahima Diallo Dokal MD2Najlae Lrhorfi MD3Hicham Belghiti MD4Nazik Allali PhD5Latifa Chat PhD6Radiology Department Mother and Child Hospital IBN SINA, Rabat, MoroccoRadiology Department Mother and Child Hospital IBN SINA, Rabat, MoroccoRadiology Department Mother and Child Hospital IBN SINA, Rabat, MoroccoRadiology Department Mother and Child Hospital IBN SINA, Rabat, MoroccoCHU IBN SINA, Rabat, MoroccoRadiology Department Mother and Child Hospital IBN SINA, Rabat, MoroccoRadiology Department Mother and Child Hospital IBN SINA, Rabat, MoroccoEwing’s sarcoma is a primary malignant bone tumor affecting individuals in the second decade of life. Primary sarcomas of the spine are rare and the occurrence of primary Ewing’s sarcoma in the spine is very rare. There are 2 types of Ewing’s sarcoma of the spine, Ewing’s sarcoma of the sacral spine which is very aggressive with a poor prognosis and Ewing’s sarcoma of the non-sacral spine which is an extremely rare occurrence. The patient may have a neurological deficit when the tumor extends into the spinal canal, causing compression of the spinal cord. Magnetic resonance imaging (MRI) is very sensitive in diagnosing the tumor and Evaluation of the extent of the tumor. Here, we report the case of a 12-year-old boy who presented with low back pain, weakness of both lower limbs and bilateral spastic paraplegia progressively evolving since 1 month. The CT and MRI scans showed the presence of a tissue lesion process centered on the vertebral body of L1, heterogeneously enhanced after injection of Gadolinium respecting the posterior arch, without bulging of the posterior wall with epiduritis, endocanal extension and spinal cord compression. The patient underwent decompression with surgical biopsy and posterior stabilization of the spine. Histopathology and immunohistochemistry studies confirmed the diagnosis of Ewing’s sarcoma and the patient was referred to an oncopediatric center for combined chemotherapy and radiotherapy, but died at home a few days later before the start of treatment.https://doi.org/10.1177/2333794X221123874 |
| spellingShingle | Amine Cherraqi MD Abir Lemrabet MD Ibrahima Diallo Dokal MD Najlae Lrhorfi MD Hicham Belghiti MD Nazik Allali PhD Latifa Chat PhD Primary Ewing’s Sarcoma of the Spine: About a Case Global Pediatric Health |
| title | Primary Ewing’s Sarcoma of the Spine: About a Case |
| title_full | Primary Ewing’s Sarcoma of the Spine: About a Case |
| title_fullStr | Primary Ewing’s Sarcoma of the Spine: About a Case |
| title_full_unstemmed | Primary Ewing’s Sarcoma of the Spine: About a Case |
| title_short | Primary Ewing’s Sarcoma of the Spine: About a Case |
| title_sort | primary ewing s sarcoma of the spine about a case |
| url | https://doi.org/10.1177/2333794X221123874 |
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